日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Calpain 3 and CaMKIIβ signaling are required to induce HSP70 necessary for adaptive muscle growth after atrophy

钙蛋白酶3和CaMKIIβ信号通路是诱导HSP70所必需的,而HSP70对于肌肉萎缩后的适应性生长至关重要。

Kramerova, Irina; Torres, Jorge A; Eskin, Ascia; Nelson, Stanley F; Spencer, Melissa J

Attenuated Ca(2+) release in a mouse model of limb girdle muscular dystrophy 2A

肢带型肌营养不良症2A小鼠模型中Ca(2+)释放减弱

DiFranco, Marino; Kramerova, Irina; Vergara, Julio L; Spencer, Melissa Jan

Failure to up-regulate transcription of genes necessary for muscle adaptation underlies limb girdle muscular dystrophy 2A (calpainopathy)

肢体带型肌营养不良症 2A(钙蛋白酶病)的根本原因是肌肉适应所需基因的转录上调失败。

Kramerova, Irina; Ermolova, Natalia; Eskin, Ascia; Hevener, Andrea; Quehenberger, Oswald; Armando, Aaron M; Haller, Ronald; Romain, Nadine; Nelson, Stanley F; Spencer, Melissa J

Pathogenity of some limb girdle muscular dystrophy mutations can result from reduced anchorage to myofibrils and altered stability of calpain 3.

某些肢带型肌营养不良症突变的致病性可能是由于肌原纤维锚定减少和钙蛋白酶 3 稳定性改变所致

Ermolova Natalia, Kudryashova Elena, DiFranco Marino, Vergara Julio, Kramerova Irina, Spencer Melissa J

Osteopontin promotes fibrosis in dystrophic mouse muscle by modulating immune cell subsets and intramuscular TGF-beta

骨桥蛋白通过调节免疫细胞亚群和肌内TGF-β促进营养不良小鼠肌肉的纤维化。

Vetrone, Sylvia A; Montecino-Rodriguez, Encarnacion; Kudryashova, Elena; Kramerova, Irina; Hoffman, Eric P; Liu, Scot D; Miceli, M Carrie; Spencer, Melissa J

Mitochondrial abnormalities, energy deficit and oxidative stress are features of calpain 3 deficiency in skeletal muscle

骨骼肌中钙蛋白酶3缺乏的特征包括线粒体异常、能量不足和氧化应激。

Kramerova, Irina; Kudryashova, Elena; Wu, Benjamin; Germain, Sean; Vandenborne, Krista; Romain, Nadine; Haller, Ronald G; Verity, M Anthony; Spencer, Melissa J

Calcium-dependent plasma membrane repair requires m- or mu-calpain, but not calpain-3, the proteasome, or caspases

钙依赖性质膜修复需要m-或mu-钙蛋白酶,但不需要钙蛋白酶-3、蛋白酶体或半胱天冬酶。

Mellgren, Ronald L; Miyake, Katsuya; Kramerova, Irina; Spencer, Melissa J; Bourg, Nathalie; Bartoli, Marc; Richard, Isabelle; Greer, Peter A; McNeil, Paul L

Novel role of calpain-3 in the triad-associated protein complex regulating calcium release in skeletal muscle

钙蛋白酶-3在调节骨骼肌钙释放的三联体相关蛋白复合物中的新作用

Kramerova, Irina; Kudryashova, Elena; Wu, Benjamin; Ottenheijm, Coen; Granzier, Henk; Spencer, Melissa J