日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Protocol for in vivo analysis of muscle function in porcine models for muscular dystrophies

猪肌营养不良模型体内肌肉功能分析方案

Hristov, Hristiyan; Blasi, Michaela; Neves Barbosa, Igor; Kemter, Elisabeth; Kurome, Mayuko; Kessler, Barbara; Zakhartchenko, Valeri; Klymiuk, Nikolai; Stirm, Michael; Jaudas, Florian; Wolf, Eckhard

Assessing the Function of Porcine A Kinase-Interacting Protein 1 (AKIP1) In Vitro-A Central Regulator of Oxidative Stress and Mitochondrial Functions.

体外评估猪 A 激酶相互作用蛋白 1 (AKIP1) 的功能——氧化应激和线粒体功能的中心调节因子

Bak Agnieszka, Hinrichs Arne, Schwaiger Anna, Fromme Tobias, Fischer Andrea, Kurome Mayuko, Zakhartchenko Valeri, Kessler Barbara, Klingenspor Martin, Wolf Eckhard, Schnieke Angelika, Fischer Konrad

Perinatal death in pig models of hypertrophic cardiomyopathy carrying sarcomere pathogenic variants.

携带肌节致病变异的肥厚型心肌病猪模型出现围产期死亡

Flisikowska Tatiana, Petersen Björn, Mearini Giulia, Huber Daniela, Kurome Mayuko, Stoff Melanie, Schlossarek Saskia, Lucas-Hahn Andrea, Wolf Eckhard, Montag Judith, Schnieke Angelika, Carrier Lucie

Reduced Muscle Force in Dystrophic DMDΔ52 Pigs Is Incompletely Restored by Systemic Transcript Reframing (DMDΔ51-52)

系统性转录重组(DMDΔ51-52)不能完全恢复患有营养不良型DMDΔ52猪的肌肉力量。

Blasi, Michaela; Hristov, Hristiyan; Stöckl, Jan B; Kraetzl, Martin; Fiedler, Sonja; Kemter, Elisabeth; Kurome, Mayuko; Kessler, Barbara; Cambra, Josep M; Zakhartchenko, Valeri; Walter, Maggie C; Kupatt, Christian; Klymiuk, Nikolai; Fröhlich, Thomas; Blutke, Andreas; Stirm, Michael; Jaudas, Florian; Wolf, Eckhard

What Genetic Modifications of Source Pigs Are Essential and Sufficient for Cell, Tissue, and Organ Xenotransplantation?

对于细胞、组织和器官异种移植而言,来源猪的哪些基因改造是必要且充分的?

Ali, Asghar; Kurome, Mayuko; Kessler, Barbara; Kemter, Elisabeth; Wolf, Eckhard

Phenotypic features of dystrophin gene knockout pigs harboring a human artificial chromosome containing the entire dystrophin gene

携带含有完整肌营养不良蛋白基因的人类人工染色体的肌营养不良蛋白基因敲除猪的表型特征

Masahito Watanabe, Hitomaru Miyamoto, Kazutoshi Okamoto, Kazuaki Nakano, Hitomi Matsunari, Kanako Kazuki, Koki Hasegawa, Ayuko Uchikura, Shuko Takayanagi, Kazuhiro Umeyama, Yosuke Hiramuki, Elisabeth Kemter, Nikolai Klymuik, Mayuko Kurome, Barbara Kessler, Eckhard Wolf, Yasuhiro Kazuki, Hiroshi Naga

Phenotypic features of genetically modified DMD-XKOXWT pigs

转基因DMD-XKOXWT猪的表型特征

Kazutoshi Okamoto, Hitomi Matsunari, Kazuaki Nakano, Kazuhiro Umeyama, Koki Hasegawa, Ayuko Uchikura, Shuko Takayanagi, Masahito Watanabe, Jun Ohgane, Michael Stirm, Mayuko Kurome, Nikolai Klymiuk, Masaki Nagaya, Eckhard Wolf, Hiroshi Nagashima

Systemic deletion of DMD exon 51 rescues clinically severe Duchenne muscular dystrophy in a pig model lacking DMD exon 52

在缺乏 DMD 外显子 52 的猪模型中,系统性删除 DMD 外显子 51 可挽救临床严重的杜氏肌营养不良症

Michael Stirm, Bachuki Shashikadze, Andreas Blutke, Elisabeth Kemter, Andreas Lange, Jan B Stöckl, Florian Jaudas, Laeticia Laane, Mayuko Kurome, Barbara Keßler, Valeri Zakhartchenko, Andrea Bähr, Nikolai Klymiuk, Hiroshi Nagashima, Maggie C Walter, Wolfgang Wurst, Christian Kupatt, Thomas Fröhlich,

A humanized minipig model for the toxicological testing of therapeutic recombinant antibodies

用于治疗性重组抗体毒理学测试的人源化小型猪模型

Tatiana Flisikowska #, Jerome Egli #, Krzysztof Flisikowski, Marlene Stumbaum, Erich Küng, Martin Ebeling, Roland Schmucki, Guy Georges, Thomas Singer, Mayuko Kurome, Barbara Kessler, Valeri Zakhartchenko, Eckhard Wolf, Felix Weber, Angelika Schnieke #, Antonio Iglesias #

Sequential in vivo labeling of insulin secretory granule pools in INS-SNAP transgenic pigs.

对 INS-SNAP 转基因猪体内胰岛素分泌颗粒池进行连续体内标记

Kemter Elisabeth, Müller Andreas, Neukam Martin, Ivanova Anna, Klymiuk Nikolai, Renner Simone, Yang Kaiyuan, Broichhagen Johannes, Kurome Mayuko, Zakhartchenko Valeri, Kessler Barbara, Knoch Klaus-Peter, Bickle Marc, Ludwig Barbara, Johnsson Kai, Lickert Heiko, Kurth Thomas, Wolf Eckhard, Solimena Michele