日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Efficacy of tranilast in preventing exacerbating cardiac function and death from heart failure in muscular dystrophy patients with advanced-stage heart failure: a single-arm, open-label, multicenter study

曲尼司特预防晚期心力衰竭肌营养不良症患者心脏功能恶化和心力衰竭死亡的疗效:一项单臂、开放标签、多中心研究

Matsumura, Tsuyoshi; Fukudome, Takayasu; Motoyoshi, Yasufumi; Nakamura, Akinori; Kuru, Satoshi; Segawa, Kazuhiko; Kitao, Ruriko; Watanabe, Chigusa; Tamura, Takuhisa; Takahashi, Toshiaki; Hashimoto, Hiroya; Sekimizu, Masahiro; Saito, Akiko M; Asakura, Masanori; Kimura, Koichi; Iwata, Yuko

Plasma Neurofilament Light Chain and Phosphorylated Tau Are Elevated in Myotonic Dystrophy Type 1

肌强直性营养不良1型患者血浆神经丝轻链和磷酸化tau蛋白水平升高

Takahashi, Masanori P; Tatebe, Harutsugu; Takada, Hiroto; Nakayama, Takahiro; Kobayashi, Michio; Yoshida, Kosuke; Kuru, Satoshi; Kira, Natsuki; Kubota, Tomoya; Mizutani, Yasuaki; Watanabe, Hirohisa; Takado, Yuhei; Tokuda, Takahiko

Association of the immunogenicity of intramuscular SARS-CoV-2 mRNA vaccination with computed tomography muscle images in patients with muscular disorders

肌肉注射SARS-CoV-2 mRNA疫苗的免疫原性与肌肉疾病患者的计算机断层扫描肌肉图像之间的关联

Naka, Tomoaki; Funato, Michinori; Yasuda, Kunihiko; Nakayama, Takahiro; Kuru, Satoshi

The Association Between Physical Activity/Heart Rate Variability Data Obtained Using a Wearable Device and Timed Motor Functional Tests in Patients with Duchenne Muscular Dystrophy: A Pilot Study

利用可穿戴设备获取的身体活动/心率变异性数据与杜氏肌营养不良症患者定时运动功能测试之间的关联性:一项初步研究

Nakamura, Akinori; Matsumura, Tsuyoshi; Takeshima, Yasuhiro; Kuru, Satoshi; Imazaki, Manami; Nonomura, Hidenori; Kaiya, Hisanobu

Natural history of Becker muscular dystrophy: a multicenter study of 225 patients

贝克尔肌营养不良症的自然史:一项纳入225例患者的多中心研究

Nakamura, Akinori; Matsumura, Tsuyoshi; Ogata, Katsuhisa; Mori-Yoshimura, Madoka; Takeshita, Eri; Kimura, Koichi; Kawashima, Takahiro; Tomo, Yui; Arahata, Hajime; Miyazaki, Daigo; Takeshima, Yasuhiro; Takahashi, Toshiaki; Ishigaki, Keiko; Kuru, Satoshi; Wakisaka, Akiko; Awano, Hiroyuki; Funato, Michinori; Sato, Tatsuharu; Saito, Yoshiaki; Takada, Hiroto; Sugie, Kazuma; Kobayashi, Michio; Ozasa, Shiro; Fujii, Tatsuya; Maegaki, Yoshihiro; Oi, Hideki; Tachimori, Hisateru; Komaki, Hirofumi

Early immunological responses to the mRNA SARS-CoV-2 vaccine in patients with neuromuscular disorders

神经肌肉疾病患者对mRNA SARS-CoV-2疫苗的早期免疫反应

Iwayama, Hideyuki; Ishihara, Naoko; Kawahara, Kohei; Madokoro, Yuta; Togawa, Yasuko; Muramatsu, Kanji; Murakami, Ayuka; Kuru, Satoshi; Kumagai, Toshiyuki; Ohashi, Wataru; Nanya, Kengo; Hasegawa, Shinji; Katsuno, Masahisa; Okumura, Akihisa

Tranilast for advanced heart failure in patients with muscular dystrophy: a single-arm, open-label, multicenter study

曲尼司特治疗肌营养不良症晚期心力衰竭患者:一项单臂、开放标签、多中心研究

Matsumura, Tsuyoshi; Hashimoto, Hiroya; Sekimizu, Masahiro; Saito, Akiko M; Motoyoshi, Yasufumi; Nakamura, Akinori; Kuru, Satoshi; Fukudome, Takayasu; Segawa, Kazuhiko; Takahashi, Toshiaki; Tamura, Takuhisa; Komori, Tetsuo; Watanabe, Chigusa; Asakura, Masanori; Kimura, Koichi; Iwata, Yuko

Founder genetic variants of ABCC4 and ABCC11 in the Japanese population are not associated with the development of subacute myelo-optico-neuropathy (SMON).

日本人群中 ABCC4 和 ABCC11 的创始基因变异与亚急性脊髓视神经病变 (SMON) 的发展无关

Matsumoto Hideki, Sasai Hideo, Kawamoto Norio, Katsuyama Masato, Minamiyama Makoto, Kuru Satoshi, Fukao Toshiyuki, Ohnishi Hidenori

A recurrent homozygous ACTN2 variant associated with core myopathy

一种与核心肌病相关的复发性纯合ACTN2变异

Inoue, Michio; Noguchi, Satoru; Sonehara, Kyuto; Nakamura-Shindo, Keiko; Taniguchi, Akira; Kajikawa, Hiroyuki; Nakamura, Hisayoshi; Ishikawa, Keiko; Ogawa, Megumu; Hayashi, Shinichiro; Okada, Yukinori; Kuru, Satoshi; Iida, Aritoshi; Nishino, Ichizo

A web-based questionnaire survey on the influence of coronavirus disease-19 on the care of patients with muscular dystrophy

一项关于冠状病毒病-19对肌营养不良症患者护理影响的网络问卷调查

Matsumura, Tsuyoshi; Takada, Hiroto; Kobayashi, Michio; Nakajima, Takashi; Ogata, Katsuhisa; Nakamura, Akinori; Funato, Michinori; Kuru, Satoshi; Komai, Kiyonobu; Futamura, Naonobu; Adachi, Yoshiki; Arahata, Hajime; Fukudome, Takayasu; Ishizaki, Masatoshi; Suwazono, Shugo; Aoki, Masashi; Matsuura, Tohru; Takahashi, Masanori P; Sunada, Yoshihide; Hanayama, Kouzou; Hashimoto, Hiroya; Nakamura, Harumasa