The cyclophilin inhibitor Debio 025 normalizes mitochondrial function, muscle apoptosis and ultrastructural defects in Col6a1-/- myopathic mice
环丝氨酸蛋白酶抑制剂 Debio 025 可使 Col6a1-/- 肌病小鼠的线粒体功能、肌肉凋亡和超微结构缺陷恢复正常
期刊:British Journal of Pharmacology
影响因子:6.8
doi:10.1111/j.1476-5381.2009.00316.x
T Tiepolo, A Angelin, E Palma, P Sabatelli, L Merlini, L Nicolosi, F Finetti, P Braghetta, G Vuagniaux, J-M Dumont, C T Baldari, P Bonaldo, P Bernardi