日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

New Validated Staging System for Light Chain (AL) Amyloidosis With Stage IIIC Defining Ultra-Poor Risk: AL International Staging System

新的经验证的轻链(AL)淀粉样变性分期系统,其中IIIC期定义了超高危:AL国际分期系统

Khwaja, Jahanzaib; Kirkwood, Amy A; Milani, Paolo; Yohannan, Binoy; Theodorakakou, Foteini; Weverling, Flores; Di Simone, Valeria; Ravichandran, Sriram; Kumar, Shaji; Petropoulos, Ioannis; Mussinelli, Roberta; Cohen, Oliver; Oerlemans, Marish I F J; Muchtar, Eli; Stamatelopoulos, Kimon; Lachmann, Helen J; Gillmore, Julian D; Briasoulis, Alexandros; Gertz, Morie; Whelan, Carol; Venneri, Lucia; Fontana, Marianna; Mahmood, Shameem; Schwotzer, Rahel; Minnema, Monique C; Dispenzieri, Angela; Palladini, Giovanni; Kastritis, Efstathios; Wechalekar, Ashutosh

Efficacy of Suppression of Serum Transthyretin With Patisiran and Vutrisiran in Variant ATTR Amyloidosis: An Observational Crossover Study

帕替西兰和伏特西兰抑制血清转甲状腺素蛋白治疗变异型ATTR淀粉样变性的疗效:一项观察性交叉研究

Razvi, Yousuf; Rauf, Muhammad Umaid; Porcari, Aldostefano; Mansell, Josephine; Sheikh, Awais; Ioannou, Adam; Whelan, Carol J; Venneri, Lucia; Martinez-Naharro, Ana; Hutt, David F; Rowczenio, Dorota; Gilbertson, Janet A; Wechalekar, Ashutosh D; Lachmann, Helen J; Hawkins, Philip N; Fontana, Marianna; Gillmore, Julian D

Transthyretin amyloid cardiomyopathy: natural history and treatment response assessed by cardiovascular magnetic resonance

转甲状腺素蛋白淀粉样变性心肌病:心血管磁共振评估其自然病程和治疗反应

Patel, Rishi K; Ioannou, Adam; Sheikh, Awais; Razvi, Yousuf; Mansell, Josephine; Martinez-Naharro, Ana; Knight, Daniel; Kotecha, Tushar; Porcari, Aldostefano; Chacko, Liza; Brown, James; Manisty, Charlotte; Moon, James C; Lachmann, Helen J; Wechalekar, Ashutosh; Whelan, Carol; Venneri, Lucia; Kellman, Peter; Hawkins, Philip N; Gillmore, Julian D; Fontana, Marianna

Revised renal stratification and progression models for predicting long-term renal outcomes in immunoglobulin light chain amyloidosis

修订的肾脏分层和进展模型用于预测免疫球蛋白轻链淀粉样变性的长期肾脏结局

Rauf, Muhammad Umaid; Law, Steven; Santostefano, Marisa; Hawkins, Philip N; Petrie, Aviva; Cappelli, Francesco; Perfetto, Federico; Razvi, Yousuf; Porcari, Aldostefano; Ravichandran, Sriram; Ioannou, Adam; Bomsztyk, Joshua; Argirò, Alessia; Gaudio, Costanza; Antonioli, Elisabetta; Barilaro, Alessandro; Delsante, Marco; Di Maso, Vittorio; Chiappini, Maria G; Ogunbiyi, Olabisi; Cohen, Oliver C; Martinez-Naharro, Ana; Whelan, Carol; Lachmann, Helen J; Wechalekar, Ashutosh D; Alberici, Federico; Fontana, Marianna; Allinovi, Marco; Gillmore, Julian D

Ethnicity in systemic AL amyloidosis may impact risk stratification

系统性AL淀粉样变性患者的种族因素可能影响风险分层

Khwaja, Jahanzaib; Ravichandran, Sriram; Cohen, Oliver; Foard, Darren; Martinez-Naharro, Ana; Venneri, Lucia; Whelan, Carol; Hawkins, Philip N; Gillmore, Julian; Lachmann, Helen J; Mahmood, Shameem; Fontana, Marianna; Wechalekar, Ashutosh

A retrospective study of isatuximab-pomalidomidedexamethasone in relapsed/refractory systemic AL amyloidosis

一项关于伊沙妥昔单抗-泊马度胺地塞米松治疗复发/难治性系统性AL淀粉样变性的回顾性研究

Vohra, Sargam Rachit; Ravichandran, Sriram; Foard, Darren; Martinez-Naharro, Ana; Venneri, Lucia; Fontana, Marianna; Whelan, Carol J; Hawkins, Philip N; Gillmore, Julian; Lachmann, Helen J; Mahmood, Shameem; Wechalekar, Ashutosh D

Outcomes of daratumumab-bortezomib-thalidomide-dexamethasone in treatment-naive systemic AL amyloidosis

达雷妥尤单抗-硼替佐米-沙利度胺-地塞米松治疗初治系统性AL淀粉样变性的疗效

Khwaja, Jahanzaib; Ravichandran, Sriram; Cohen, Oliver; Foard, Darren; Low, May; Martinez-Naharro, Ana; Venneri, Lucia; Fontana, Marianna; Hawkins, Philip N; Gillmore, Julian; Lachmann, Helen J; Whelan, Carol; Mahmood, Shameem; Wechalekar, Ashutosh

Advancing Care for AA Amyloidosis with Biomarker-Based Staging

利用生物标志物分期推进AA型淀粉样变性的治疗

Lachmann, Helen J

Limited utility of Mayo 2012 cardiac staging system for risk stratification of patients with advanced cardiac AL amyloidosis - analysis of a uniformly treated cohort of 1,275 patients

Mayo 2012心脏分期系统在晚期心脏AL淀粉样变性患者风险分层中的应用有限——对1275例接受统一治疗的患者队列的分析

Khwaja, Jahanzaib; Ravichandran, Sriram; Bomsztyk, Joshua; Cohen, Oliver; Foard, Darren; Martinez-Naharro, Ana; Venneri, Lucia; Fontana, Marianna; Hawkins, Philip N; Gillmore, Julian; Lachmann, Helen J; Mahmood, Shameem; Whelan, Carol; Kirkwood, Amy A; Wechalekar, Ashutosh

Tc-99m labelled bone scintigraphy in suspected cardiac amyloidosis

疑似心脏淀粉样变性患者的Tc-99m标记骨闪烁显像

Rauf, Muhammad Umaid; Hawkins, Philip N; Cappelli, Francesco; Perfetto, Federico; Zampieri, Mattia; Argiro, Alessia; Petrie, Aviva; Law, Steven; Porcari, Aldostefano; Razvi, Yousuf; Bomsztyk, Joshua; Ravichandran, Sriram; Ioannou, Adam; Patel, Rishi; Starr, Neasa; Hutt, David F; Mahmood, Shameem; Wisniowski, Brendan; Martinez-Naharro, Ana; Venneri, Lucia; Whelan, Carol; Roczenio, Dorota; Gilbertson, Janet; Lachmann, Helen J; Wechalekar, Ashutosh D; Rapezzi, Claudio; Serenelli, Matteo; Massa, Paolo; Caponetti, Angelo Giuseppe; Ponziani, Alberto; Accietto, Antonella; Giovannetti, Alessandro; Saturi, Giulia; Sguazzotti, Maurizio; Gagliardi, Christian; Biagini, Elena; Longhi, Simone; Fontana, Marianna; Gillmore, Julian D