日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Acute severe cholestatic hepatitis and lymphopenia characterize pediatric hepatitis-associated aplastic anemia

急性重症胆汁淤积性肝炎和淋巴细胞减少症是儿童肝炎相关性再生障碍性贫血的特征。

Tegtmeyer, Daniel; Tsaka, Sofia; Lehmberg, Kai; Höfs, Michaela; Beime, Jan; Briem-Richter, Andrea; Oh, Jun; Lainka, Elke; Schulz-Jürgensen, Sebastian

Hepatic Phenotype in NBAS-Associated Disease: Clinical Course, Prognostic Factors and Outcome in 230 Patients

NBAS相关疾病的肝脏表型:230例患者的临床病程、预后因素和结局

Peters, Bianca; Schlieben, Lea Dewi; Brennenstuhl, Heiko; Arikan, Cigdem; Bedoyan, Sarah M; Bulut, Fatma Derya; Crushell, Ellen; Dionisi-Vici, Carlo; Drab, Ada; Fichtner, Alexander; Garcia, Aixa Gonzalez; Fry, Deanna; Garbade, Sven F; Hammann, Nicole; Hadzic, Nedim; Hegarty, Robert; Jørgensen, Marianne Hørby; Laaß, Martin; Lainka, Elke; Leghlam, Lina; Lurz, Eberhard; Mungan, Halise Neslihan Önenli; Pietrobattista, Andrea; Polo, Begona; Socha, Piotr; Squires, James E; Sun, Tian; Vogel, Georg F; Prokisch, Holger; Kölker, Stefan; Hoffmann, Georg F; Staufner, Christian; Lenz, Dominic

Odevixibat after liver transplant in patients with progressive familial intrahepatic cholestasis type 1: A case series

肝移植后接受奥德维西巴治疗进行性家族性肝内胆汁淤积症1型患者:病例系列研究

Vogel, Georg-Friedrich; Kathemann, Simone; Pietrobattista, Andrea; Maggiore, Giuseppe; Aldrian, Denise; Sciveres, Marco; Verkade, Henkjan J; Sokal, Etienne; Jannone, Giulia; Salcedo, Magdalena; Rauschkolb, Peter; Maucksch, Christof; Valcheva, Velichka; Lainka, Elke

Paediatric acute liver failure: A prospective, nationwide, population-based surveillance study in Germany

德国一项前瞻性、全国性、基于人群的儿童急性肝衰竭监测研究

Lenz, Dominic; Abdulaziz, Muhammad; Peters, Bianca; Wagner, Matias; Schlieben, Lea D; Corman, Victor M; Baumann, Ulrich; Bufler, Philip; Dattner, Tal; Ganschow, Rainer; Genzel, Kristin; Hammann, Nicole; Hartleif, Steffen; Hegen, Bianca; Henning, Stephan; Hoerning, André; Jankofsky, Martin; Junge, Norman; Kathemann, Simone; Knoppke, Birgit; Kohl-Sobania, Martina; Laass, Martin; Lainka, Elke; Lurz, Eberhard; Melter, Michael; Müller, Hanna; Pilic, Denisa; Ries, Markus; Schiefele, Lisa; Schwerd, Tobias; Sturm, Ekkehard; Wegner, Mechtild; Urschitz, Michael S; Garbade, Sven F; Wenning, Daniel; Drosten, Christian; Fichtner, Alexander; Kölker, Stefan; Hoffmann, Georg F; Prokisch, Holger; Staufner, Christian

Paediatric liver transplantation-improving health care through needs assessment, screening and interventions: protocol for a mixed-methods study

儿童肝移植——通过需求评估、筛查和干预改善医疗保健:一项混合方法研究方案

Higgen, Sanna; Winzig, Jana; Johannsen, Lene Marie; Hegen, Bianca; Kraft, Stefanie; Oh, Jun; Lainka, Elke; Buchholz, Angela; Inhestern, Laura

The role of LSR gene variants in early onset intrahepatic cholestasis: a case series with treatment options

LSR基因变异在早发性肝内胆汁淤积症中的作用:病例系列及治疗方案

Ohlsson, Sinja; Zaufel, Alex; Qvartskhava, Natalia; Stock, Friedrich; Hinreiner, Sophie; Baba, Hideo A; Prusinskas, Benas; Kubitz, Ralf; Görg, Boris; Herebian, Diran; Lainka, Elke; Kathemann, Simone

Assessment of Donor-Specific Human Leukocyte Antigen Antibodies Following Pediatric Liver Transplantation: Predictors, Protectors, and Clinical Relevance

儿童肝移植后供体特异性人类白细胞抗原抗体的评估:预测因子、保护因子和临床意义

Kanaan, Evelien; Ohlsson, Sinja; Kathemann, Simone; Prusinskas, Benas; Tsaka, Sofia; Heinemann, Falko M; Heinold, Andreas; Schulze, Maren; Pape, Lars; Lainka, Elke

Intrauterine intestinal obstruction in a preterm infant with severe mevalonate kinase deficiency - a case report

一例伴有严重甲羟戊酸激酶缺乏症的早产儿发生宫内肠梗阻的病例报告

Hoermann, Henrike; Franzel, Julia; Tautz, Juliane; Oommen, Prasad T; Lainka, Elke; Mayatepek, Ertan; Hoehn, Thomas

[Position paper of the Society for Paediatric Gastroenterology and Nutrition (GPGE) on the off-label use of biologics and signal inhibitors in children and adolescents with IBD that have already been approved for adults]

[儿科胃肠病学和营养学会 (GPGE) 关于在已获准用于成人的 IBD 儿童和青少年中使用生物制剂和信号抑制剂的立场文件]

Däbritz, Jan; Classen, Martin; Krohn, Kathrin; Krahl, Andreas; Buderus, Stephan; Lainka, Elke; de Laffolie, Jan; Posovszky, Carsten

[Correction: Position paper of the Society for Paediatric Gastroenterology and Nutrition (GPGE) on the off-label use of biologics and signal inhibitors in children and adolescents with IBD that have already been approved for adults]

[更正:儿科胃肠病学和营养学会 (GPGE) 关于在已获准用于成人的 IBD 儿童和青少年中使用生物制剂和信号抑制剂的立场文件]

Däbritz, Jan; Classen, Martin; Krohn, Kathrin; Krahl, Andreas; Buderus, Stephan; Lainka, Elke; de Laffolie, Jan; Posovszky, Carsten