日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

IKBKB reduces huntingtin aggregation by phosphorylating serine 13 via a non-canonical IKK pathway

IKBKB 通过非经典 IKK 通路磷酸化丝氨酸 13,从而减少亨廷顿蛋白的聚集

Cristina Cariulo, Paola Martufi, Margherita Verani, Leticia Toledo-Sherman, Ramee Lee, Celia Dominguez, Lara Petricca, Andrea Caricasole

TBK1 phosphorylates mutant Huntingtin and suppresses its aggregation and toxicity in Huntington's disease models

TBK1 磷酸化突变型亨廷顿蛋白并抑制其在亨廷顿病模型中的聚集和毒性

Ramanath Narayana Hegde, Anass Chiki, Lara Petricca, Paola Martufi, Nicolas Arbez, Laurent Mouchiroud, Johan Auwerx, Christian Landles, Gillian P Bates, Malvindar K Singh-Bains, Mike Dragunow, Maurice A Curtis, Richard Lm Faull, Christopher A Ross, Andrea Caricasole, Hilal A Lashuel

Striatal infusion of cholesterol promotes dose-dependent behavioral benefits and exerts disease-modifying effects in Huntington's disease mice

纹状体输注胆固醇可促进亨廷顿氏病小鼠的剂量依赖性行为益处并发挥疾病改善作用

Giulia Birolini #, Marta Valenza #, Eleonora Di Paolo #, Elena Vezzoli, Francesca Talpo, Claudia Maniezzi, Claudio Caccia, Valerio Leoni, Franco Taroni, Vittoria D Bocchi, Paola Conforti, Elisa Sogne, Lara Petricca, Cristina Cariulo, Margherita Verani, Andrea Caricasole, Andrea Falqui, Gerardo Biell

Inhibiting pathologically active ADAM10 rescues synaptic and cognitive decline in Huntington's disease

抑制病理活性 ADAM10 可挽救亨廷顿氏病中的突触和认知衰退

Elena Vezzoli, Ilaria Caron, Francesca Talpo, Dario Besusso, Paola Conforti, Elisa Battaglia, Elisa Sogne, Andrea Falqui, Lara Petricca, Margherita Verani, Paola Martufi, Andrea Caricasole, Alberto Bresciani, Ottavia Cecchetti, Pia Rivetti di Val Cervo, Giulio Sancini, Olaf Riess, Hoa Nguyen, Lisa S

Phospho-S129 Alpha-Synuclein Is Present in Human Plasma but Not in Cerebrospinal Fluid as Determined by an Ultrasensitive Immunoassay

超灵敏免疫测定法测定发现,磷酸化 S129 α-突触核蛋白存在于人血浆中,但不存在于脑脊液中

Cristina Cariulo, Paola Martufi, Margherita Verani, Lucia Azzollini, Giordana Bruni, Andreas Weiss, Sean M Deguire, Hilal A Lashuel, Eugenia Scaricamazza, Giulia Maria Sancesario, Tommaso Schirinzi, Nicola Biagio Mercuri, Giuseppe Sancesario, Andrea Caricasole, Lara Petricca

Phosphorylation of huntingtin at residue T3 is decreased in Huntington's disease and modulates mutant huntingtin protein conformation

亨廷顿舞蹈症中残基 T3 处的亨廷顿蛋白磷酸化降低,并调节突变亨廷顿蛋白的构象

Cristina Cariulo, Lucia Azzollini, Margherita Verani, Paola Martufi, Roberto Boggio, Anass Chiki, Sean M Deguire, Marta Cherubini, Silvia Gines, J Lawrence Marsh, Paola Conforti, Elena Cattaneo, Iolanda Santimone, Ferdinando Squitieri, Hilal A Lashuel, Lara Petricca, Andrea Caricasole

Development of an ELISA assay for the quantification of soluble huntingtin in human blood cells

开发用于定量人类血细胞中可溶性亨廷顿蛋白的 ELISA 检测方法

Luisa Massai, Lara Petricca, Letizia Magnoni, Luca Rovetini, Salman Haider, Ralph Andre, Sarah J Tabrizi, Sigurd D Süssmuth, Bernhard G Landwehrmeyer, Andrea Caricasole, Giuseppe Pollio, Simonetta Bernocco

Cholesterol defect is marked across multiple rodent models of Huntington's disease and is manifest in astrocytes

胆固醇缺陷在亨廷顿氏病的多种啮齿动物模型中都有明显表现,并在星形胶质细胞中有所体现

Marta Valenza, Valerio Leoni, Joanna M Karasinska, Lara Petricca, Jianjia Fan, Jeffrey Carroll, Mahmoud A Pouladi, Elisa Fossale, Huu Phuc Nguyen, Olaf Riess, Marcy MacDonald, Cheryl Wellington, Stefano DiDonato, Michael Hayden, Elena Cattaneo