Ribosomal Frameshifting Selectively Modulates the Assembly, Function, and Pharmacological Rescue of a Misfolded CFTR Variant
核糖体移码选择性地调节错误折叠的 CFTR 变体的组装、功能和药理学拯救
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doi:10.1101/2023.05.02.539166
Patrick Carmody, Francis J Roushar, Austin Tedman, Wei Wang, Madeline Herwig, Minsoo Kim, Eli F McDonald, Karen Noguera, Jennifer Wong-Roushar, Jon-Luc Poirier, Nathan B Zelt, Ben T Pockrass, Andrew G McKee, Charles P Kuntz, S Vamsee Raju, Lars Plate, Wesley D Penn, Jonathan P Schlebach