日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Management of pulmonary arterial hypertension in systemic sclerosis: from classical treatments to new horizons

系统性硬化症肺动脉高压的治疗:从传统疗法到新方向

Villa, Annalisa; Sanges, Sébastien; Sobanski, Vincent; Lamblin, Nicolas; Rosato, Edoardo; Godinas, Laurent; Hachulla, Eric; Delcroix, Marion; Montani, David; Launay, David

Janus kinase and calcineurin-inhibitor combination in anti-MDA5 dermatomyositis: No significant survival benefit but reassuring safety profile

Janus激酶抑制剂和钙调磷酸酶抑制剂联合治疗抗MDA5皮肌炎:未见显著生存获益,但安全性良好

Pagis, Valentine; Astouati, Quentin; Pacoureau, Lucas; Nguyen, Yann; Bay, Pierre; Roux, Antoine; Gallay, Laure; Cottin, Vincent; Terrier, Benjamin; Meyer, Alain; Cerf, Charles; Neuville, Mathilde; Hervier, Baptiste; Renaud, Arthur; Suzon, Benoit; Schleinitz, Nicolas; Papo, Thomas; Priou, Pascaline; Mekinian, Arsène; Ullmer, Audrey; Oehler, Erwan; Gensous, Noémie; Berezne, Alice; Martin, Luc De Saint; Marhadour, Thierry; Martin, Mickaël; Servettaz, Amélie; Samson, Maxime; Gilardin, Laurent; Charles, Pierre; Woessner, Juliette; Carmoi, Thierry; Dilly, Baptiste; Mauhin, Wladimir; Baillet, Nicolas; Humbert, Sébastien; Thoreau, Benjamin; Lemaitre, Marine; Pendu, Claire Le; Loiseau, Pierre; Quemeneur, Thomas; Blanchard, Elodie; Voermans, Nicol; Launay, David; Nunes, Hilario; Benveniste, Olivier; Uzunhan, Yurdagul; Allenbach, Yves

A Treat-to-Target approach in hereditary angioedema: expert consensus from a European committee

遗传性血管性水肿的达标治疗策略:欧洲委员会专家共识

Cancian, Mauro; Caballero, Teresa; Boccon-Gibod, Isabelle; Buttgereit, Thomas; Cohn, Danny; Eren, Efrem; Kiani-Alikhan, Sorena; Launay, David; Mandelin, Johanna; Zanichelli, Andrea; Farkas, Henriette

Is hereditary angioedema associated with deficits in emotion regulation? A quantitative study in adult patients

遗传性血管性水肿是否与情绪调节缺陷有关?一项针对成年患者的定量研究

Duprez, Christelle; Christophe, Véronique; Citerne, Isabelle; Raguet, Michel; Richez, Louise; Sanges, Sébastien; Launay, David

Ocular multimodal imaging of a patient with malignant atrophic papulosis (Degos disease)

恶性萎缩性丘疹病(德戈斯病)患者的眼部多模态成像

Barbé, Alexandre; El Maamar, Yasmine; Farhat, Meryem-Maud; Launay, David; Hachulla, Éric; Ledoult, Emmanuel

Clinician underprescription of and patient nonadherence to clinical practice guideline-recommended medications for peripheral artery disease: a systematic review and meta-analysis

临床医生对外周动脉疾病药物处方不足以及患者对临床实践指南推荐药物的依从性差:系统评价和荟萃分析

Kirkham, Aidan M; Paquet, Maude; Fergusson, Dean A; Graham, Ian D; Presseau, Justin; McIsaac, Daniel I; Nagpal, Sudhir K; de Launay, David; Abdul, Sami Aftab; Shorr, Risa; Grimshaw, Jeremy M; Roberts, Derek J

Characteristics and outcomes associated with CD2 and CD25 expression on bone marrow mast cells in patients with systemic mastocytosis

系统性肥大细胞增生症患者骨髓肥大细胞上CD2和CD25表达的特征和相关结局

Rossignol, Julien; Georgin-Lavialle, Sophie; Canioni, Danielle; Beganovic, Omer; Brouzes, Chantal; Fain, Olivier; Heiblig, Maël; Gourguechon, Clément; Guilpain, Philippe; Bulai-Livideanu, Cristina; Barete, Stéphane; Agopian, Julie; Brenet, Fabienne; Dubreuil, Patrice; Lemal, Richard; Tournilhac, Olivier; Terriou, Louis; Launay, David; Bouillet, Laurence; Chatain, Catharina; Damaj, Ghandi; Ballul, Thomas; Greco, Celine; Polivka, Laura; Frenzel, Laurent; Meni, Cécile; Bouktit, Hassiba; Benabou, Dina; Devin, Clotilde; Gaudy-Marqueste, Caroline; Gousseff, Marie; Le Mouel, Edwige; Neel, Antoine; Ranta, Dana; Jaussaud, Roland; Jo Molina, Thierry; Bruneau, Julie; Javier, Rose-Marie; Pelletier, Fabien; Castelain, Florence; Retornaz, Frederique; Cabrera, Quentin; Zunic, Patricia; Gourin, Marie Pierre; Wierzbicka-Hainaut, Ewa; Viallard, Jean François; Lavigne, Christian; Hoarau, Cyrille; Durieu, Isabelle; Dimicoli-Salazar, Sophie; Torregrosa-Diaz, Jose Miguel; Duval, Audrey; Garcelon, Nicolas; Lespinasse, Jeremie; Soria, Angèle; Chantran, Yannick; Arock, Michel; Bodemer, Christine; Lortholary, Olivier; Asnafi, Vahid; Hermine, Olivier; Lhermitte, Ludovic

Diagnosis, Characteristics, and Outcome of Selective Anti-polysaccharide Antibody Deficiencies In A Retrospective Cohort of 55 Adult Patients

55例成年患者回顾性队列研究中选择性抗多糖抗体缺乏症的诊断、特征和预后

Perrard, Nicolas; Stabler, Sarah; Sanges, Sébastien; Terriou, Louis; Lamblin, Catherine; Gaillard, Sacha; Vuotto, Fanny; Chenivesse, Cécile; Mortuaire, Geoffrey; Batteux, Frédéric; Mirgot, Floriane; Collet, Aurore; Lopez, Benjamin; Dubucquoi, Sylvain; Labalette, Myriam; Hachulla, Eric; Launay, David; Lefèvre, Guillaume

Thrombin generation test as a useful tool for improving disease severity stratification in antiphospholipid syndrome

凝血酶生成试验可作为改善抗磷脂综合征疾病严重程度分层的有效工具。

Yelnik, Cecile; Bauters, Anne; Labreuche, Julien; Desvages, Maximilien; Launay, David; Hachulla, Eric; Dubucquoi, Sylvain; Lancel, Steve; Frimat, Marie; Lambert, Marc

Immunoglobulins G from Patients with Systemic Sclerosis Modify the Molecular Signatures of Endothelial Cells.

系统性硬化症患者的免疫球蛋白G可改变内皮细胞的分子特征

Chepy Aurélien, Vivier Solange, Bray Fabrice, Chauvet Clément, Lescoat Alain, Elhannani Abderrahmane, Figeac Martin, Guilbert Lucile, Leprêtre Frédéric, Bourel Louisa, Hachulla Eric, Rolando Christian, Lecureur Valérie, Dubucquoi Sylvain, Launay David, Sobanski Vincent