日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

A mouse model of cardiac immunoglobulin light chain amyloidosis reveals insights into tissue accumulation and toxicity of amyloid fibrils

小鼠心脏免疫球蛋白轻链淀粉样变性模型揭示了淀粉样原纤维在组织中的积累和毒性

Martinez-Rivas, Gemma; Ayala, Maria Victoria; Bender, Sebastien; Codo, Gilles Roussine; Swiderska, Weronika Karolina; Lampis, Alessio; Pedroza, Laura; Merdanovic, Melisa; Sicard, Pierre; Pinault, Emilie; Richard, Laurence; Lavatelli, Francesca; Giorgetti, Sofia; Canetti, Diana; Rinsant, Alexa; Kaaki, Sihem; Ory, Cécile; Oblet, Christelle; Pollet, Justine; Naser, Eyad; Carpinteiro, Alexander; Roussel, Muriel; Javaugue, Vincent; Jaccard, Arnaud; Bonaud, Amélie; Delpy, Laurent; Ehrmann, Michael; Bridoux, Frank; Sirac, Christophe

Cryo-EM of cardiac AL-224L amyloid reveals shared features in λ6 light chain fibril folds

心脏AL-224L淀粉样蛋白的冷冻电镜分析揭示了λ6轻链原纤维折叠的共同特征

Hicks, Chad W; Prokaeva, Tatiana; Spencer, Brian; Jayaraman, Shobini; Huda, Noorul; Wong, Sherry; Chen, Hui; Sanchorawala, Vaishali; Lavatelli, Francesca; Gursky, Olga

Truncation of the constant domain drives amyloid formation by immunoglobulin light chains

恒定区截短驱动免疫球蛋白轻链形成淀粉样蛋白

Lavatelli, Francesca; Natalello, Antonino; Marchese, Loredana; Ami, Diletta; Corazza, Alessandra; Raimondi, Sara; Mimmi, Maria Chiara; Malinverni, Silvia; Mangione, P Patrizia; Palmer, Manel Terrones; Lampis, Alessio; Concardi, Monica; Verona, Guglielmo; Canetti, Diana; Arbustini, Eloisa; Bellotti, Vittorio; Giorgetti, Sofia

AA-amyloidosis in cats (Felis catus) housed in shelters.

收容所内猫(Felis catus)的 AA 淀粉样变性

Ferri Filippo, Ferro Silvia, Porporato Federico, Callegari Carolina, Guglielmetti Chiara, Mazza Maria, Ferrero Marta, Crinò Chiara, Gallo Enrico, Drigo Michele, Coppola Luigi Michele, Gerardi Gabriele, Schulte Tim Paul, Ricagno Stefano, Vogel Monique, Storni Federico, Bachmann Martin F, Vogt Anne-Cathrine, Caminito Serena, Mazzini Giulia, Lavatelli Francesca, Palladini Giovanni, Merlini Giampaolo, Zini Eric

Amyloid Formation by Globular Proteins: The Need to Narrow the Gap Between in Vitro and in Vivo Mechanisms

球状蛋白的淀粉样蛋白形成:缩小体外和体内机制之间差距的必要性

Faravelli, Giulia; Mondani, Valentina; Mangione, P Patrizia; Raimondi, Sara; Marchese, Loredana; Lavatelli, Francesca; Stoppini, Monica; Corazza, Alessandra; Canetti, Diana; Verona, Guglielmo; Obici, Laura; Taylor, Graham W; Gillmore, Julian D; Giorgetti, Sofia; Bellotti, Vittorio

Protease-sensitive regions in amyloid light chains: what a common pattern of fragmentation across organs suggests about aggregation

淀粉样轻链中的蛋白酶敏感区域:不同器官中常见的片段化模式揭示了聚集的哪些信息

Mazzini, Giulia; Ricagno, Stefano; Caminito, Serena; Rognoni, Paola; Milani, Paolo; Nuvolone, Mario; Basset, Marco; Foli, Andrea; Russo, Rosaria; Merlini, Giampaolo; Palladini, Giovanni; Lavatelli, Francesca

Clinical Amyloid Typing by Proteomics: Performance Evaluation and Data Sharing Between Two Centres

基于蛋白质组学的临床淀粉样蛋白分型:两中心间的性能评估和数据共享

Canetti, Diana; Brambilla, Francesca; Rendell, Nigel B; Nocerino, Paola; Gilbertson, Janet A; Di Silvestre, Dario; Bergamaschi, Andrea; Lavatelli, Francesca; Merlini, Giampaolo; Gillmore, Julian D; Bellotti, Vittorio; Mauri, Pierluigi; Taylor, Graham W

Dissecting the Molecular Features of Systemic Light Chain (AL) Amyloidosis: Contributions from Proteomics

剖析系统性轻链(AL)淀粉样变性的分子特征:蛋白质组学的贡献

Rognoni, Paola; Mazzini, Giulia; Caminito, Serena; Palladini, Giovanni; Lavatelli, Francesca

Indicators of profound hematologic response in AL amyloidosis: complete response remains the goal of therapy

AL淀粉样变性患者出现显著血液学反应的指标:完全缓解仍然是治疗目标。

Milani, Paolo; Basset, Marco; Nuvolone, Mario; Benigna, Francesca; Rodigari, Lara; Lavatelli, Francesca; Foli, Andrea; Merlini, Giampaolo; Palladini, Giovanni

Systemic amyloidoses and proteomics: The state of the art

系统性淀粉样变性和蛋白质组学:最新进展

Lavatelli, Francesca; di Fonzo, Andrea; Palladini, Giovanni; Merlini, Giampaolo