日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

D178N prion protein mutation endows RML prions with new strain properties that do not mimic human genetic prion diseases

D178N朊病毒蛋白突变赋予RML朊病毒新的毒株特性,这些特性并不模拟人类遗传性朊病毒疾病。

Masone, Antonio; Grasso, Anna; Comerio, Liliana; Bruno, Rosalia; Lavigna, Giada; Vanni, Ilaria; D'Agostino, Claudia; Orrù, Christina D; Caughey, Byron; Altmeppen, Hermann C; Castilla, Joaquín; Giaccone, Giorgio; Tagliavini, Fabrizio; Di Bari, Michele A; Nonno, Romolo; Chiesa, Roberto

Enhanced lysosomal activity prevents infection with PrP(Sc) and the seeding activity of α-synuclein & tau prions

溶酶体活性增强可阻止 PrP(Sc) 感染以及 α-突触核蛋白和 tau 朊病毒的播散活性。

Mercer, Robert C C; Le, Nhat T T; Mirza-Romero, Nadia A; Orbe, Isabel C; Flaherty, Erin; DeFranco, Joseph P; Lavigna, Giada; Gatdula, Jean R P; Fraser, Douglas G; Sundaravadivelu, Aravind; Vultaggio, Janelle S; Beeler, Aaron B; Chiesa, Roberto; Telling, Glenn C; Harris, David A

Tau oligomers impair memory and synaptic plasticity through the cellular prion protein.

Tau 寡聚体通过细胞朊病毒蛋白损害记忆和突触可塑性

Balducci Claudia, Orsini Franca, Cerovic Milica, Beeg Marten, Rocutto Beatrice, Dacomo Letizia, Masone Antonio, Busani Eleonora, Raimondi Ilaria, Lavigna Giada, Chen Po-Tao, Leva Susanna, Colombo Laura, Zucchelli Chiara, Musco Giovanna, Kanaan Nicholas M, Gobbi Marco, Chiesa Roberto, Fioriti Luana, Forloni Gianluigi

Lysosomal Enhancement Prevents Infection with PrP(Sc), α-Synuclein & Tau Prions.

溶酶体增强可预防 PrP(Sc)、α-突触核蛋白和 Tau 朊病毒的感染

Mercer Robert C C, Le Nhat T T, Mirza-Romero Nadia A, Flaherty Erin, DeFranco Joseph P, Lavigna Giada, Orbe Isabel C, Gatdula Jean R P, Fraser Douglas G, Sundaravadivelu Aravind, Vultaggio Janelle S, Beeler Aaron B, Chiesa Roberto, Telling Glenn C, Harris David A

The cellular prion protein mediates Tau oligomer‐induced memory impairment in mice

细胞朊病毒蛋白介导小鼠Tau寡聚体诱导的记忆障碍

Lalucque, Hervé; Malagnac, Fabienne; Brun, Sylvain; Kicka, Sébastien; Silar, Philippe; Forloni, Gianluigi; Balducci, Claudia; Orsini, Franca; Cerovic, Milica; Masone, Antonio; Raimondi, Ilaria; Lavigna, Giada; Zucchelli, Chiara; Beeg, Marten; Colombo, Laura; Musco, Giovanna; Gobbi, Marco; Chiesa, Roberto; Fioriti, Luana

Erratum: A tetracationic porphyrin with dual anti-prion activity

勘误:一种具有双重抗朊病毒活性的四阳离子卟啉

Masone, Antonio; Zucchelli, Chiara; Caruso, Enrico; Lavigna, Giada; Eraña, Hasier; Giachin, Gabriele; Tapella, Laura; Comerio, Liliana; Restelli, Elena; Raimondi, Ilaria; Elezgarai, Saioa R; De Leo, Federica; Quilici, Giacomo; Taiarol, Lorenzo; Oldrati, Marvin; Lorenzo, Nuria L; García-Martínez, Sandra; Cagnotto, Alfredo; Lucchetti, Jacopo; Gobbi, Marco; Vanni, Ilaria; Nonno, Romolo; Di Bari, Michele A; Tully, Mark D; Cecatiello, Valentina; Ciossani, Giuseppe; Pasqualato, Sebastiano; Van Anken, Eelco; Salmona, Mario; Castilla, Joaquín; Requena, Jesús R; Banfi, Stefano; Musco, Giovanna; Chiesa, Roberto

Doxycycline rescues recognition memory and circadian motor rhythmicity but does not prevent terminal disease in fatal familial insomnia mice

强力霉素可以挽救致命性家族性失眠小鼠的识别记忆和昼夜节律运动功能,但不能阻止其最终患病。

Lavigna, Giada; Masone, Antonio; Bouybayoune, Ihssane; Bertani, Ilaria; Lucchetti, Jacopo; Gobbi, Marco; Porcu, Luca; Zordan, Stefano; Rigamonti, Mara; Imeri, Luca; Restelli, Elena; Chiesa, Roberto