日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

TDP-43 seeding activity in the olfactory mucosa of patients with amyotrophic lateral sclerosis

肌萎缩侧索硬化症患者嗅黏膜中TDP-43种子活性

Vizziello, Maria; Dellarole, Ilaria Linda; Ciullini, Arianna; Pascuzzo, Riccardo; Lombardo, Annalisa; Bellandi, Floriana; Celauro, Luigi; Battipaglia, Claudia; Ciusani, Emilio; Rizzo, Ambra; Catania, Marcella; Devigili, Grazia; Della Seta, Sara Adriana; Margiotta, Valentina; Consonni, Monica; Faltracco, Veronica; Tiraboschi, Pietro; Riva, Nilo; Portaleone, Sara Maria Silvia; Zanusso, Gianluigi; Legname, Giuseppe; Lauria, Giuseppe; Dalla Bella, Eleonora; Moda, Fabio

Detection of TDP-43 seeds in CSF of presymptomatic and symptomatic genetic FTD/ALS

在无症状和有症状的遗传性额颞叶痴呆/肌萎缩侧索硬化症患者的脑脊液中检测到TDP-43种子

Dellarole, Ilaria Linda; Aprea, Vittoria; Catania, Marcella; Battipaglia, Claudia; Romeo, Aurora; Villa, Cristina; Burato, Anna; Celauro, Luigi; Bella, Eleonora Dalla; Riva, Nilo; Salvi, Erika; Rossi, Giacomina; Fede, Giuseppe Di; Legname, Giuseppe; De Houwer, Julie F H; Alberici, Antonella; Borroni, Barbara; Seelaar, Harro; van Swieten, John C; Moda, Fabio; Caroppo, Paola

Substitution of histidine 95 by tyrosine in the prion protein causes spontaneous neurodegeneration in transgenic mice

朊病毒蛋白中组氨酸95被酪氨酸取代会导致转基因小鼠出现自发性神经退行性变。

Torres, Juan-María; Marín-Moreno, Alba; Espinosa, Juan-Carlos; Canoyra, Sara; Burato, Anna; Ciullini, Arianna; De Luca, Chiara Maria Giulia; Bistaffa, Edoardo; Moda, Fabio; Legname, Giuseppe

Comparing Prion Proteins Across Species: Is Zebrafish a Useful Model?

比较不同物种的朊病毒蛋白:斑马鱼是有用的模型吗?

Burato, Anna; Legname, Giuseppe

The Role of Prion Protein in Reelin/Dab1 Signaling: Implications for Neurodegeneration.

朊病毒蛋白在 Reelin/Dab1 信号传导中的作用:对神经退行性疾病的影响

Rolle Irene Giulia, Burato Anna, Bacınoğlu Merve Begüm, Moda Fabio, Legname Giuseppe

How Sup35 monomer conformation and amyloid fibril polymorphism determine yeast strain phenotypes

Sup35单体构象和淀粉样原纤维多态性如何决定酵母菌株表型

Tanaka, Motomasa; Nomura, Takashi; Boyer, David; Komi, Yusuke; Ge, Peng; Maillard, Rodrigo A; Rodriguez, Piere; Yamagata, Atsushi; Shirouzu, Mikako; Legname, Giuseppe; Samori, Bruno; Eisenberg, David

Prion protein alters viral control and enhances pathology after perinatal cytomegalovirus infection

朊病毒蛋白改变病毒控制并增强围产期巨细胞病毒感染后的病理

Dubravka Karner, Daria Kvestak, Paola Kucan Brlic, Maja Cokaric Brdovcak, Berislav Lisnic, Ilija Brizic, Vanda Juranic Lisnic, Mijo Golemac, Jelena Tomac, Astrid Krmpotic, Esma Karkeni, Valentina Libri, Sebastien Mella, Giuseppe Legname, Hermann C Altmeppen, Milena Hasan, Stipan Jonjic, Tihana Lenac

Oxidative stress-related cellular aging causes dysfunction of the Kv3.1/KCNC1 channel reverted by melatonin

氧化应激相关的细胞衰老导致 Kv3.1/KCNC1 通道功能障碍,而褪黑激素可逆转该功能

Sara Spinelli, Alessia Remigante, Raffaella Liuni, Gianluca Mantegna, Giuseppe Legname, Angela Marino, Rossana Morabito, Silvia Dossena

Tau seeding activity in skin biopsy differentiates tauopathies from synucleinopathies

皮肤活检中的 Tau 播种活性可区分 Tau 蛋白病和突触核蛋白病

Ilaria Linda Dellarole #, Elena Vacchi #, Inigo Ruiz-Barrio, Sandra Pinton, Andrea Raimondi, Stefania Rossi, Sara Morandi, Giovanni Bianco, Merve Begum Bacinoglu, Annalisa Lombardo, Luigi Celauro, Claudio Staedler, Salvatore Galati, Javier Pagonabarraga, Jaime Kulisevsky, Giuseppe Legname, Claudio G

Transmission of Norwegian reindeer CWD to sheep by intracerebral inoculation results in an unusual phenotype and prion distribution

挪威驯鹿慢性疾病 (CWD) 通过脑内接种传播给绵羊,导致异常表型和朊病毒分布

Erez Harpaz #, Federico Angelo Cazzaniga #, Linh Tran, Tram T Vuong, Giuseppe Bufano, Øyvind Salvesen, Maiken Gravdal, Devin Aldaz, Julianna Sun, Sehun Kim, Luigi Celauro, Giuseppe Legname, Glenn C Telling, Michael A Tranulis, Sylvie L Benestad, Arild Espenes, Fabio Moda #, Cecilie Ersdal #