日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Destabilization of cardiac myosin acetylation and sequestration with type 2 diabetes mellitus

2型糖尿病导致心肌肌球蛋白乙酰化不稳定和隔离

Degezelle, Mahault Mathilde; Chaami, Chahida; Lewis, Christopher T A; Zhang, Chengxin; Hessel, Anthony L; Rainer, Peter P; Kirk, Jonathan A; Stokke, Mathis Korseberg; Seaborne, Robert A E; Ochala, Julien

Dysregulated skeletal muscle myosin super-relaxation and energetics in male participants with type 2 diabetes mellitus.

2 型糖尿病男性患者骨骼肌肌球蛋白超松弛和能量代谢失调

Lewis Christopher T A, Moreno-Justicia Roger, Savoure Lola, Calvo Enrique, Bak Agata, Laitila Jenni, Seaborne Robert A E, Larsen Steen, Iwamoto Hiroyuki, Cefis Marina, Morais Jose A, Gouspillou Gilles, Alegre-Cebollada Jorge, Hawke Thomas J, Vazquez Jesús, Adrover Miquel, Marcangeli Vincent, Hammad Rami, Granet Jordan, Gaudreau Pierrette, Aubertin-Leheudre Mylène, Bélanger Marc, Robitaille Richard, Deshmukh Atul S, Ochala Julien

Heterogeneous Dysregulation of Myosin Super-Relaxation and Energetics in Hypertrophic Cardiomyopathy

肥厚型心肌病中肌球蛋白超松弛和能量代谢的异质性失调

Ochala, Julien; Feng, Miao; Wang, Qian; Chaami, Chahida; Nollet, Edgar E; Lewis, Christopher T A; Hessel, Anthony L; Michels, Michelle; Bedi, Kenneth C Jr; Margulies, Kenneth B; Pinto, Jose R; Campbell, Kenneth S; Kuster, Diederik W D; van der Velden, Jolanda

Site-specific quantification of the in vivo UFMylome reveals myosin modification in ALS.

针对体内 UFMylome 的位点特异性定量分析揭示了 ALS 中的肌球蛋白修饰

Blazev Ronnie, Zee Barry M, Peckham Hayley, Ng Yaan-Kit, Lewis Christopher T A, Zhang Chengxin, McNamara James W, Goodman Craig A, Gregorevic Paul, Ochala Julien, Steyn Frederik J, Ngo Shyuan T, Stokes Matthew P, Parker Benjamin L

Pathogenic TNNT1 variants are associated with aberrant thin filament compliance and myofibre hyper-contractility.

致病性 TNNT1 变异与细丝顺应性异常和肌纤维过度收缩有关

Laitila Jenni, Lewis Christopher T A, Hessel Anthony L, Primiano Guido, Hernandez-Lain Aurelio, Fiorillo Chiara, Lawlor Michael W, Ottenheijm Coen A C, Jungbluth Heinz, Man Ka Fu, Fornili Arianna, Ochala Julien

Super-relaxed myosins contribute to respiratory muscle hibernation in mechanically ventilated patients

肌球蛋白过度松弛会导致机械通气患者的呼吸肌进入休眠状态。

van den Berg, Marloes; Shi, Zhonghua; Claassen, Wout J; Hooijman, Pleuni; Lewis, Christopher T A; Andersen, Jesper L; van der Pijl, Robbert J; Bogaards, Sylvia J P; Conijn, Stefan; Peters, Eva L; Begthel, Leon P L; Uijterwijk, Bas; Lindqvist, Johan; Langlais, Paul R; Girbes, Armand R J; Stapel, Sandra; Granzier, Henk; Campbell, Kenneth S; Ma, Weikang; Irving, Thomas; Hwee, Darren T; Hartman, James J; Malik, Fady I; Paul, Marinus; Beishuizen, Albertus; Ochala, Julien; Heunks, Leo; Ottenheijm, Coen A C

Remodeling of skeletal muscle myosin metabolic states in hibernating mammals

冬眠哺乳动物骨骼肌肌球蛋白代谢状态的重塑

Lewis, Christopher T A; Melhedegaard, Elise G; Ognjanovic, Marija M; Olsen, Mathilde S; Laitila, Jenni; Seaborne, Robert A E; Gronset, Magnus; Zhang, Changxin; Iwamoto, Hiroyuki; Hessel, Anthony L; Kuehn, Michel N; Merino, Carla; Amigo, Nuria; Frobert, Ole; Giroud, Sylvain; Staples, James F; Goropashnaya, Anna V; Fedorov, Vadim B; Barnes, Brian; Toien, Oivind; Drew, Kelly; Sprenger, Ryan J; Ochala, Julien

Predominant myosin superrelaxed state in canine myocardium with naturally occurring dilated cardiomyopathy

犬自然发生扩张型心肌病的心肌中以肌球蛋白超松弛状态为主

Ochala, Julien; Lewis, Christopher T A; Beck, Thomas; Iwamoto, Hiroyuki; Hessel, Anthony L; Campbell, Kenneth S; Pyle, W Glen