日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

IL12RB1 Deficiency Appearing in North America: Expanding the Clinical Phenotypes

IL12RB1 缺乏症在北美出现:临床表型不断扩展

Wang, Chen; Marciano, Beatriz E; Harris, Annalie J; Johnston, Alicia M; Apaydin Arikan, Evsen; Bayer, Diana K; Solomon, Benjamin D; Price, Nathan B; Platt, Craig D; Modi, Arunkumar J; Shaker, Marcus S; Seroogy, Christine M; Johnson, Daniel; Kleiner, David E; Chirombo Kluczynski, Lavenda; Anderson, Victoria L; Daub, Janine R; Berghout, Joanne; Oler, Andrew J; Walkiewicz, Magdalena A; Similuk, Morgan; Lewis, David B; Galgiani, John N; Freeman, Alexandra F; Rosen, Lindsey B; Hsu, Amy P; Zerbe, Christa S; Holland, Steven M

γδ T cell antigen receptor polyspecificity enables T cell responses to a broad range of immune challenges.

γδ T 细胞抗原受体多特异性使 T 细胞能够对广泛的免疫挑战做出反应。

Guo Jing, Chowdhury Roshni Roy, Mallajosyula Vamsee, Xie Jianming, Dubey Megha, Liu Yuanyuan, Li Jing, Wei Yu-Ling, Palanski Brad A, Wang Conghua, Qiu Lingfeng, Ohanyan Mané, Kask Oliver, Sola Elsa, Kamalyan Lilit, Lewis David B, Scriba Thomas J, Davis Mark M, Dodd Dylan, Zeng Xun, Chien Yueh-Hsiu

Single-cell transcriptomics reveal different maturation stages and sublineage commitment of human thymic invariant natural killer T cells

单细胞转录组学揭示了人类胸腺不变自然杀伤T细胞的不同成熟阶段和亚谱系分化

Maas-Bauer, Kristina; Köhler, Natalie; Stell, Anna-Verena; Zwick, Melissa; Acharya, Swati; Rensing-Ehl, Anne; König, Christoph; Kroll, Johannes; Baker, Jeanette; Koßmann, Stefanie; Pradier, Amandine; Wang, Sisi; Docquier, Mylène; Lewis, David B; Negrin, Robert S; Simonetta, Federico

Case report: Refractory Evans syndrome in two patients with spondyloenchondrodysplasia with immune dysregulation treated successfully with JAK1/JAK2 inhibition

病例报告:两例伴有免疫失调的脊椎软骨发育不良患者的难治性埃文斯综合征,经JAK1/JAK2抑制剂治疗后获得成功

Gernez, Yael; Narula, Mansi; Cepika, Alma-Martina; Valdes Camacho, Juanita; Hoyte, Elisabeth G; Mouradian, Kirsten; Glader, Bertil; Singh, Deepika; Sathi, Bindu; Rao, Latha; Tolin, Ana L; Weinberg, Kenneth I; Lewis, David B; Bacchetta, Rosa; Weinacht, Katja G

Benthic jellyfish act as suction pumps to facilitate release of interstitial porewater

底栖水母起到吸水泵的作用,促进孔隙水的释放。

Durieux, David M; Scrogham, Gabrielle D; Fender, Christian; Lewis, David B; Deban, Stephen M; Gemmell, Brad J

Sequential Stem Cell-Kidney Transplantation in Schimke Immuno-osseous Dysplasia

Schimke免疫骨发育不良的序贯干细胞-肾移植

Bertaina, Alice; Grimm, Paul C; Weinberg, Kenneth; Parkman, Robertson; Kristovich, Karen M; Barbarito, Giulia; Lippner, Elizabeth; Dhamdhere, Girija; Ramachandran, Vasavi; Spatz, Jordan M; Fathallah-Shaykh, Sahar; Atkinson, T Prescott; Al-Uzri, Amira; Aubert, Geraldine; van der Elst, Kim; Green, Sean G; Agarwal, Rajni; Slepicka, Priscila F; Shah, Ami J; Roncarolo, Maria G; Gallo, Amy; Concepcion, Waldo; Lewis, David B

Immunogenicity and tolerability of COVID-19 messenger RNA vaccines in primary immunodeficiency patients with functional B-cell defects

COVID-19信使RNA疫苗在原发性免疫缺陷伴功能性B细胞缺陷患者中的免疫原性和耐受性

Pham, Michele N; Murugesan, Kanagavel; Banaei, Niaz; Pinsky, Benjamin A; Tang, Monica; Hoyte, Elisabeth; Lewis, David B; Gernez, Yael

Increased double-negative αβ+ T-cells reveal adult-onset autoimmune lymphoproliferative syndrome in a patient with IgG4-related disease

双阴性αβ+ T细胞增多提示IgG4相关疾病患者患有成人起病的自身免疫性淋巴增生综合征

Brar, Nivaz; Spinner, Michael A; Baker, Matthew C; Advani, Ranjana H; Natkunam, Yasodha; Lewis, David B; Silva, Oscar

Immunogenicity of a third COVID-19 messenger RNA vaccine dose in primary immunodeficiency disorder patients with functional B-cell defects

在伴有功能性B细胞缺陷的原发性免疫缺陷病患者中,第三剂COVID-19信使RNA疫苗的免疫原性

Gernez, Yael; Murugesan, Kanagavel; Cortales, Cristina R; Banaei, Niaz; Hoyte, Lisa; Pinsky, Benjamin A; Lewis, David B; Pham, Michele N

Single-Cell Analysis of the Neonatal Immune System Across the Gestational Age Continuum

胎龄连续体中新生儿免疫系统的单细胞分析

Peterson, Laura S; Hedou, Julien; Ganio, Edward A; Stelzer, Ina A; Feyaerts, Dorien; Harbert, Eliza; Adusumelli, Yamini; Ando, Kazuo; Tsai, Eileen S; Tsai, Amy S; Han, Xiaoyuan; Ringle, Megan; Houghteling, Pearl; Reiss, Jonathan D; Lewis, David B; Winn, Virginia D; Angst, Martin S; Aghaeepour, Nima; Stevenson, David K; Gaudilliere, Brice