日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

PTBP1 inhibition reprograms myogenesis to rescue impaired muscle regeneration in mdx mice through correcting E2A splicing

PTBP1抑制通过纠正E2A剪接重编程肌生成,从而挽救mdx小鼠受损的肌肉再生能力。

Fan, Shusheng; Liu, Xiaoyun; Pan, Qian; Tong, Haowei; Gui, Qiaoqiao; Guo, Guangyao; Hong, Huitao; Hu, Wanting; Huang, Xiaofei; Zhao, Lei; Li, Xihua; Yu, Qinwei; Zhang, Luyong; Jiang, Zhenzhou

RUNX2 Activation in Fibro/Adipogenic Progenitors Promotes Muscle Fibrosis in Muscular Dystrophy.

RUNX2 在纤维/脂肪生成祖细胞中的激活促进肌营养不良症中的肌肉纤维化。

Wu Pengkai, Zhang Zehua, Zheng Kai, Zhu Ziqi, Zhu Yong, Kiram Abdukahar, Zhao Lei, Chen Huihui, Xu Zhu, Li Xihua, Sun Beicheng, Li Zhijian, Xu Dengqiu

A natural history study of Chinese individuals with Duchenne muscular dystrophy: Results from 2 years of follow-up and beyond

中国杜氏肌营养不良症患者自然史研究:2年及以后的随访结果

Li, Xihua; Yang, Xinying; Chang, Xingzhi; Wang, Zhiqiang; Hong, Siqi; Zhu, Wenhua; Shen, Qi; Zhou, Yangmei; Zhu, Shuiqing; Gao, Ying Xu; Jia, Caiping

Oestrogen Receptor Alpha in Myocyte Maintains Muscle Regeneration in Duchenne Muscular Dystrophy.

肌细胞中的雌激素受体α维持杜氏肌营养不良症的肌肉再生

Huang Xiaofei, Li Sijia, Wang Huna, Zhao Lei, Li Xihua, Fan Shusheng, Hu Wanting, Tong Haowei, Guo Guangyao, Xu Dengqiu, Zhang Luyong, Jiang Zhenzhou, Yu Qinwei

From shadows to clarity: A new paradigm for comprehensive variant detection in undiagnosed dystrophinopathy using combined long-read and RNA sequencing

从阴影到清晰:结合长读长测序和RNA测序技术,为未确诊的肌营养不良症患者提供全面的变异检测新范式

Zhao, Lei; Pan, Shirang; Hu, Chaoping; Shi, Yiyun; Li, Xihua

Admission NIHSS score and diabetes as independent predictors of in-hospital early neurological improvement following mechanical thrombectomy: a retrospective cohort study

入院时NIHSS评分和糖尿病作为机械取栓术后院内早期神经功能改善的独立预测因子:一项回顾性队列研究

Zhao, Chenyang; Li, Xihua; Han, Yi; Ren, Xuefei; Sun, Yaxuan

Comparison of hemodynamics and respiratory function between ciprofol-remifentanil and propofol-remifentanil in obese patients undergoing gastrointestinal endoscopic anesthesia: a randomized controlled trial

比较肥胖患者行胃肠内镜麻醉时环丙酚-瑞芬太尼与丙泊酚-瑞芬太尼的血流动力学和呼吸功能:一项随机对照试验

Jian, Chunfang; Zhang, Minghua; Zhong, Xiaochun; Li, Xihua; Fu, Hangxiang; Chen, Ying; Shen, Yi

A 1-year analysis from a natural history study in Chinese individuals with Duchenne muscular dystrophy

一项针对中国杜氏肌营养不良症患者的自然史研究的1年分析

Li, Xihua; Lv, Junlan; Zhu, Wenhua; Hong, Siqi; Wang, Zhiqiang; Chang, Xingzhi; Gao, Ying Xu; Zhou, Yangmei; Jia, Caiping; Fang, Jia; Patterson, Terrell A

Clinical, Pathologic, and Genetic Spectrum of Collagen VI-Related Disorder in China-A Retrospective Observational Multicenter Study.

中国胶原蛋白VI相关疾病的临床、病理和遗传谱——一项回顾性观察多中心研究

Hu Chaoping, Shi Yiyun, Zhao Lei, Zhu Wenhua, Jiao Kexin, Yu Lifei, Li Xihua, Wang Yi

Comprehensive analysis of 2097 patients with dystrophinopathy based on a database from 2011 to 2021

基于2011年至2021年数据库,对2097例肌营养不良症患者进行综合分析

Zhao, Lei; Shi, Yiyun; Hu, Chaoping; Zhou, Shuizhen; Li, Hui; Zhang, Lifeng; Qian, Chuang; Zhou, Yiyao; Wang, Yi; Li, Xihua