日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Comparative Efficacy and Safety of Anakinra and Canakinumab in Patients With VEXAS Syndrome: An International Multicenter Study

阿那白滞素和卡那单抗治疗VEXAS综合征患者的疗效和安全性比较:一项国际多中心研究

Eviatar, Tali; Capelusnik, Dafne; Campochiaro, Corrado; Lacombe, Valentin; Jachiet, Vincent; Zisapel, Michael; Sagy, Iftach; Tayer-Shifman, Oshrat E; Ozeri, David; Kivity, Shaye; Tomelleri, Alessandro; Terrier, Benjamin; Peleg, Hagit; Comont, Thibault; Sacre, Karim; Woaye-Hune, Pascal; Arnaud, Laurent; Lazaro, Estibaliz; Grobost, Vincent; Lifermann, Francois; Samson, Maxime; Ardois, Samuel; Garnier, Alice; Maria, Alexandre; Cantagrel, Alain; Meyer, Aurore; Bouaziz, Jean-David; Heiblig, Mael; Dagna, Lorenzo; Diral, Elisa; Kosmider, Olivier; Elkayam, Ori; Hadjadj, Jérôme; Georgin-Lavialle, Sophie; Fain, Olivier; Mekinian, Arsene

Anti-RNApol3-Associated myocarditis: an emerging disease linking autoimmunity and infection

抗RNA聚合酶3相关性心肌炎:一种将自身免疫和感染联系起来的新兴疾病

Quentric, Paul; Charuel, Jean-Luc; Moyon, Quentin; Hékimian, Guillaume; Dorgham, Karim; Lifermann, François; Kerneis, Mathieu; Mathian, Alexis; Aacha, Karim; Melki, Isabelle; Chommeloux, Juliette; Petit, Matthieu; Gautier, Melchior; Bay, Pierre; Rouvier, Philippe; Charpentier, Etienne; da Mata-Jardin, Omaira; Lefevre, Lucie; Parizot, Christophe; Saura, Ouriel; Levy, David; Ortuno, Sofia; Schmidt, Matthieu; Luyt, Charles-Edouard; Gorochov, Guy; Amoura, Zahir; Combes, Alain; Pineton de Chambrun, Marc

Concordance between presenting features and relapse in granulomatosis with polyangiitis: implications for risk assessment and counselling

肉芽肿性多血管炎的临床表现与复发的一致性:对风险评估和咨询的启示

Iudici, Michele; Salis, Zubeyir; Cohen, Pascal; Néel, Antoine; Aouba, Achille; Lifermann, Francois; Ruivard, Marc; Aumaître, Olivier; Bonnotte, Bernard; Samson, Maxime; Maurier, Francois; Le Gallou, Thomas; Hachulla, Eric; Karras, Alexandre; Cottin, Vincent; Jourde-Chiche, Noemie; Viallard, Jean-François; Perier, Amandine; Godmer, Pascal; Quéméneur, Thomas; de Moreuil, Claire; Guillevin, Loïc; Terrier, Benjamin; Puéchal, Xavier

VEXAS syndrome is characterized by inflammasome activation and monocyte dysregulation

VEXAS 综合征的特征是炎症小体激活和单核细胞失调

Olivier Kosmider #, Céline Possémé, Marie Templé, Aurélien Corneau, Francesco Carbone, Eugénie Duroyon, Paul Breillat, Twinu-Wilson Chirayath, Bénédicte Oules, Pierre Sohier, Marine Luka, Camille Gobeaux, Estibaliz Lazaro, Roderau Outh, Guillaume Le Guenno, François Lifermann, Marie Berleur, Melchio

Long-term outcome and prognosis of mixed histiocytosis (Erdheim-Chester disease and Langerhans Cell Histiocytosis)

混合型组织细胞增生症(埃尔德海姆-切斯特病和朗格汉斯细胞组织细胞增生症)的长期结果和预后

Pegoraro, Francesco; Papo, Matthias; Cohen-Aubart, Fleur; Peyronel, Francesco; Lugli, Gianmarco; Trambusti, Irene; Baulier, Gildas; de Menthon, Mathilde; Le Scornet, Tanguy; Oziol, Eric; Ferreira-Maldent, Nicole; Hermine, Olivier; Faucher, Benoit; Koschel, Dirk; Straetmans, Nicole; Abisror, Noémie; Terrier, Benjamin; Lifermann, François; Razanamahery, Jerome; Allenbach, Yves; Keraen, Jeremy; Bulifon, Sophie; Hervier, Baptiste; Buccoliero, Annamaria; Charlotte, Frederic; Monzani, Quentin; Boussouar, Samia; Shor, Natalia; Tondo, Annalisa; Barete, Stephane; Idbaih, Ahmed; Tazi, Abdellatif; Sieni, Elena; Amoura, Zahir; Emile, Jean-François; Vaglio, Augusto; Haroche, Julien

In Multiple Myeloma, High-Risk Secondary Genetic Events Observed at Relapse Are Present From Diagnosis in Tiny, Undetectable Subclonal Populations

在多发性骨髓瘤中,复发时观察到的高风险继发性遗传事件,从诊断时就已存在于微小、无法检测的亚克隆群体中。

Lannes, Romain; Samur, Mehmet; Perrot, Aurore; Mazzotti, Celine; Divoux, Marion; Cazaubiel, Titouan; Leleu, Xavier; Schavgoulidze, Anaïs; Chretien, Marie-Lorraine; Manier, Salomon; Adiko, Didier; Orsini-Piocelle, Frederique; Lifermann, François; Brechignac, Sabine; Gastaud, Lauris; Bouscary, Didier; Macro, Margaret; Cleynen, Alice; Mohty, Mohamad; Munshi, Nikhil; Corre, Jill; Avet-Loiseau, Hervé

Efficacy of daratumumab in refractory primary Sjögren disease

达雷妥尤单抗治疗难治性原发性干燥综合征的疗效

Nocturne, Gaetane; Marmontel, Oriane; di Filippo, Mathilde; Chretien, Pascale; Krzysiek, Roman; Lifermann, Francois; Rahal, Nawal; Belkhir, Rakiba; Moulin, Philippe; Mariette, Xavier

Rituximab vs Cyclophosphamide Induction Therapy for Patients With Granulomatosis With Polyangiitis

利妥昔单抗与环磷酰胺诱导治疗肉芽肿性多血管炎患者的比较

Puéchal, Xavier; Iudici, Michele; Perrodeau, Elodie; Bonnotte, Bernard; Lifermann, François; Le Gallou, Thomas; Karras, Alexandre; Blanchard-Delaunay, Claire; Quéméneur, Thomas; Aouba, Achille; Aumaître, Olivier; Cottin, Vincent; Hamidou, Mohamed; Ruivard, Marc; Cohen, Pascal; Mouthon, Luc; Guillevin, Loïc; Ravaud, Philippe; Porcher, Raphaël; Terrier, Benjamin

Cutaneous manifestations of lymphoid-variant hypereosinophilic syndrome

淋巴细胞变异型嗜酸性粒细胞增多症的皮肤表现

Laurent, Claire; Lefèvre, Guillaume; Kahn, Jean-Emmanuel; Staumont-Salle, Delphine; Felten, Renaud; Puget, Marie; Moulinet, Thomas; Machelart, Irène; Launay, David; Charvet, Estelle; Bouaziz, Jean David; Jachiet, Marie; Espitia, Alexandra; Mahr, Alfred; Le Clech, Christian; Malphettes, Marion; Morice, Cécile; Mourah, Samia; Moins-Teisserenc, Hélène; Lifermann, François; Soulier-Guérin, Karine; Villate, Alban; Baillou, Chloé; Grados, Aurélie; Robbins, Ailsa; Abisror, Noemie; Bagot, Martine; Boutboul, David; Panel, Kewin; Vignon-Pennamen, Marie-Dominique; Rivet, Jacqueline; Battistella, Maxime; Groh, Matthieu; de Masson, Adèle

Comparative study of granulomatosis with polyangiitis subsets according to ANCA status: data from the French Vasculitis Study Group Registry

根据ANCA状态对肉芽肿性多血管炎亚型进行比较研究:来自法国血管炎研究组登记处的数据

Puéchal, Xavier; Iudici, Michele; Pagnoux, Christian; Cohen, Pascal; Hamidou, Mohamed; Aouba, Achille; Lifermann, François; Ruivard, Marc; Aumaître, Olivier; Bonnotte, Bernard; Maurier, Francois; Le Gallou, Thomas; Hachulla, Eric; Karras, Alexandre; Khouatra, Chahéra; Jourde-Chiche, Noémie; Viallard, Jean-François; Blanchard-Delaunay, Claire; Godmer, Pascal; Le Quellec, Alain; Quéméneur, Thomas; de Moreuil, Claire; Mouthon, Luc; Terrier, Benjamin; Guillevin, Loïc