日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Reduced IL-10 production by FoxP3+IL-10+ Treg cells is partially compensated by complosome-associated induction of regulatory FoxP3-IL-10+ T cells in allergic eosinophilic asthma

在过敏性嗜酸性哮喘中,FoxP3+IL-10+ Treg 细胞产生的 IL-10 减少可通过复合体相关诱导的调节性 FoxP3-IL-10+ T 细胞部分补偿。

Stichova, Julie; Slanina, Peter; Chovancova, Zita; Baros, Jan; Litzman, Marek; Litzman, Jiri; Vlkova, Marcela

First report from the Czech national registry of inborn errors of immunity (2012-2025)

捷克国家先天性免疫缺陷登记处第一份报告(2012-2025 年)

Chovancova, Zita; Hlavackova, Eva; Hakl, Roman; Milota, Tomas; Kralickova, Pavlina; Malkusova, Ivana; Hutyrova, Beata; Safarova, Michaela; Vydlakova, Jana; Jilek, Dalibor; Novak, Jiri; Schneiderova, Helena; Kralova, Petra; Zimulova, Alena; Novak, Vitezslav; Bystron, Jaromir; Zaveska, Dita; Latalova, Vendula; Kopriva, Frantisek; Kasl, Milan; Kracik, Vladimir; Formankova, Renata; Sedlacek, Petr; Vytiskova, Karolina; Svoboda, Michal; Novakova, Hana; Litzman, Jiri

Bronchiectasis, Low IgG Levels and Lack of Vaccination are Risk Factors for Covid-19 Hospitalization in X-linked Agammaglobulinemia - A Retrospective Multicenter Study

支气管扩张、低IgG水平和未接种疫苗是X连锁无丙种球蛋白血症患者新冠肺炎住院的危险因素——一项回顾性多中心研究

Stenlander, Caroline; Lindahl, Hannes; Wahren-Borgström, Emelie; Geier, Christoph B; Sediva, Anna; Fevang, Børre; Milito, Cinzia; Varandas, Cláudia; Roca-Oporto, Cristina; Pulvirenti, Federica; Hodl, Isabel; Malkusova, Ivana; Rivière, Jacques G; Litzman, Jiri; Walter, Jolan E; Hanitsch, Leif G; Neth, Olaf; Kralickova, Pavlina; Miller, Rahim; Shaffren, Serena; Silva, Susana L; Katzenstein, Terese; Martelius, Timi; Steiner, Urs C; Smith, C I Edvard; Warnatz, Klaus; Bergman, Peter

Beyond TREC: Pivotal role of tandem TREC/KREC assay in Czech SCID NBS pilot programme

超越TREC:串联TREC/KREC检测在捷克SCID新生儿筛查试点项目中的关键作用

Bloomfield, Markéta; Hlaváčková, Eva; Schneiderová, Helena; Turnovec, Marek; Tichý, Lukáš; Čech, Zbyněk; Chrastina, Petr; Dvořáková, Lenka; Pešková, Karolína; Formánková, Renata; Říha, Petr; Vlková, Marcela; Bejdák, Petr; Havlišová, Magdaléna; Froňková, Eva; Kalina, Tomáš; Bíly, Viktor; Říčná, Dita; Grombiříková, Hana; Sedláček, Petr; Litzman, Jiří; Freiberger, Tomáš; Šedivá, Anna; Klocperk, Adam

Low CD46 expression on activated CD4+ T cells predict improved Th1 cell reactivity to calcitriol in majority of patients with allergic eosinophilic asthma and healthy donors

在大多数过敏性嗜酸性哮喘患者和健康供体中,活化的 CD4+ T 细胞上 CD46 表达低预示着 Th1 细胞对骨化三醇的反应性增强。

Julie Stichova ,Peter Slanina ,Zita Chovancova ,Jan Baros ,Marek Litzman ,Jiri Litzman ,Marcela Vlkova

Customizing subcutaneous immunoglobulin administration in primary antibody deficiency: patient-centric care perspectives

针对原发性抗体缺乏症患者,制定个性化的皮下注射免疫球蛋白方案:以患者为中心的护理视角

Kobayashi, Roger H; Maltese, Joanna; Litzman, Jiří; Kreuwel, Huub; Zekoll, Theresa; Kobayashi, Ai Lan; Gupta, Sudhir

Systematic Approach Revealed SERPING1 Splicing-Affecting Variants to be Highly Represented in the Czech National HAE Cohort

系统性研究发现,SERPING1剪接影响变异体在捷克国家HAE队列中高度普遍存在

Grombirikova, Hana; Bily, Viktor; Soucek, Premysl; Kramarek, Michal; Hakl, Roman; Ballonova, Lucie; Ravcukova, Barbora; Ricna, Dita; Kozena, Karolina; Kratochvilova, Lucie; Sobotkova, Marta; Zachova, Radana; Kuklinek, Pavel; Kralickova, Pavlina; Krcmova, Irena; Hanzlikova, Jana; Vachova, Martina; Krystufkova, Olga; Dankova, Eva; Jesenak, Milos; Novackova, Martina; Svoboda, Michal; Litzman, Jiri; Freiberger, Tomas

Intraoral and maxillofacial abnormalities in patients with autosomal dominant hyper-IgE syndrome

常染色体显性高IgE综合征患者的口腔颌面部异常

Tar, Ildikó; Szegedi, Márta; Krasuska-Sławińska, Ewa; Heropolitańska-Pliszka, Edyta; Bernatowska, Ewa A; Öncü, Elif; Keles, Sevgi; Guner, Sukru N; Reisli, Ismail; Gesheva, Nevena; Naumova, Elissaveta; Izakovicova-Holla, Lydie; Litzman, Jiri; Savchak, Igor; Kostyuchenko, Larysa; Erdõs, Melinda

Corrigendum: Clinical efficacy, safety and tolerability of a new subcutaneous immunoglobulin 16.5% (Octanorm [Cutaquig(®)]) in the treatment of patients with primary immunodeficiencies

更正:一种新型皮下注射免疫球蛋白16.5%(奥克坦诺姆[Cutaquig®])治疗原发性免疫缺陷患者的临床疗效、安全性和耐受性

Kobayashi, Roger H; Gupta, Sudhir; Melamed, Isaac; Mandujano, J Fernando; Kobayashi, Ai Lan; Ritchie, Bruce; Geng, Bob; Atkinson, Thomas Prescott; Rehman, Syed; Turpel-Kantor, Eva; Litzman, Jiří

Do common infections trigger disease-onset or -severity in CTLA-4 insufficiency?

常见感染是否会引发 CTLA-4 不足症或加重疾病?

Máté Krausz, Noriko Mitsuiki, Valeria Falcone, Johanna Komp, Sara Posadas-Cantera, Hanns-Martin Lorenz, Jiri Litzman, Daniel Wolff, Maria Kanariou, Anita Heinkele, Carsten Speckmann, Georg Häcker, Hartmut Hengel, Laura Gámez-Díaz, Bodo Grimbacher