日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Molecules and Experimental Models in Mitochondrial Disorders

线粒体疾病中的分子和实验模型

Loguercio Polosa, Paola; Bruni, Francesco

Mitochondria Deregulations in Cancer Offer Several Potential Targets of Therapeutic Interventions

癌症中的线粒体功能失调为治疗干预提供了多个潜在靶点

Musicco, Clara; Signorile, Anna; Pesce, Vito; Loguercio Polosa, Paola; Cormio, Antonella

Molecular Investigation of Mitochondrial RNA19 Role in the Pathogenesis of MELAS Disease

线粒体 RNA19 在 MELAS 病发病机制中的作用的分子研究

Paola Loguercio Polosa, Francesco Capriglia, Francesco Bruni

Three-dimensional structure of human cyclooxygenase (hCOX)-1

人环氧合酶 (hCOX)-1 的三维结构

Miciaccia, Morena; Belviso, Benny Danilo; Iaselli, Mariaclara; Cingolani, Gino; Ferorelli, Savina; Cappellari, Marianna; Loguercio Polosa, Paola; Perrone, Maria Grazia; Caliandro, Rocco; Scilimati, Antonio

Exploring the Ability of LARS2 Carboxy-Terminal Domain in Rescuing the MELAS Phenotype

探索LARS2羧基末端结构域在挽救MELAS表型中的能力

Capriglia, Francesco; Rizzo, Francesca; Petrosillo, Giuseppe; Morea, Veronica; d'Amati, Giulia; Cantatore, Palmiro; Roberti, Marina; Loguercio Polosa, Paola; Bruni, Francesco

Fine-tuning of the respiratory complexes stability and supercomplexes assembly in cells defective of complex III

复合物 III 缺陷细胞中呼吸复合物稳定性和超复合物组装的微调

Concetta V Tropeano, Serena J Aleo, Claudia Zanna, Marina Roberti, Letizia Scandiffio, Paola Loguercio Polosa, Jessica Fiori, Emanuele Porru, Aldo Roda, Valerio Carelli, Stefan Steimle, Fevzi Daldal, Michela Rugolo, Anna Ghelli

Mice lacking the mitochondrial exonuclease MGME1 accumulate mtDNA deletions without developing progeria

缺乏线粒体核酸外切酶 MGME1 的小鼠会积累线粒体 DNA 缺失,但不会患上早衰症

Stanka Matic, Min Jiang, Thomas J Nicholls, Jay P Uhler, Caren Dirksen-Schwanenland, Paola Loguercio Polosa, Marie-Lune Simard, Xinping Li, Ilian Atanassov, Oliver Rackham, Aleksandra Filipovska, James B Stewart, Maria Falkenberg, Nils-Göran Larsson, Dusanka Milenkovic

POLRMT regulates the switch between replication primer formation and gene expression of mammalian mtDNA

POLRMT 调控哺乳动物线粒体 DNA 复制引物形成与基因表达之间的转换

Inge Kühl, Maria Miranda, Viktor Posse, Dusanka Milenkovic, Arnaud Mourier, Stefan J Siira, Nina A Bonekamp, Ulla Neumann, Aleksandra Filipovska, Paola Loguercio Polosa, Claes M Gustafsson, Nils-Göran Larsson

Parsing the differences in affected with LHON: genetic versus environmental triggers of disease conversion

解析LHON患者的差异:疾病转化的遗传因素与环境因素

Carelli, Valerio; d'Adamo, Pio; Valentino, Maria Lucia; La Morgia, Chiara; Ross-Cisneros, Fred N; Caporali, Leonardo; Maresca, Alessandra; Loguercio Polosa, Paola; Barboni, Piero; De Negri, Annamaria; Sadun, Federico; Karanjia, Rustum; Salomao, Solange R; Berezovsky, Adriana; Chicani, Filipe; Moraes, Milton; Moraes Filho, Milton; Belfort, Rubens Jr; Sadun, Alfredo A

Cigarette toxicity triggers Leber's hereditary optic neuropathy by affecting mtDNA copy number, oxidative phosphorylation and ROS detoxification pathways

香烟毒性通过影响线粒体DNA拷贝数、氧化磷酸化和活性氧解毒途径,诱发莱伯氏遗传性视神经病变。

Giordano, L; Deceglie, S; d'Adamo, P; Valentino, M L; La Morgia, C; Fracasso, F; Roberti, M; Cappellari, M; Petrosillo, G; Ciaravolo, S; Parente, D; Giordano, C; Maresca, A; Iommarini, L; Del Dotto, V; Ghelli, A M; Salomao, S R; Berezovsky, A; Belfort, R Jr; Sadun, A A; Carelli, V; Loguercio Polosa, P; Cantatore, P