日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Charles Weissmann (1931–2025), an outstanding and captivating molecular biologist

查尔斯·魏斯曼(1931–2025),一位杰出而富有魅力的分子生物学家

van Rheenen, Wouter; van der Spek, Rick A A; Bakker, Mark K; van Vugt, Joke J F A; Hop, Paul J; Zwamborn, Ramona A J; de Klein, Niek; Westra, Harm-Jan; Bakker, Olivier B; Deelen, Patrick; Shireby, Gemma; Hannon, Eilis; Moisse, Matthieu; Baird, Denis; Restuadi, Restuadi; Dolzhenko, Egor; Dekker, Annelot M; Gawor, Klara; Westeneng, Henk-Jan; Tazelaar, Gijs H P; van Eijk, Kristel R; Kooyman, Maarten; Byrne, Ross P; Doherty, Mark; Heverin, Mark; Al Khleifat, Ahmad; Iacoangeli, Alfredo; Shatunov, Aleksey; Ticozzi, Nicola; Cooper-Knock, Johnathan; Smith, Bradley N; Gromicho, Marta; Chandran, Siddharthan; Pal, Suvankar; Morrison, Karen E; Shaw, Pamela J; Hardy, John; Orrell, Richard W; Sendtner, Michael; Meyer, Thomas; Başak, Nazli; van der Kooi, Anneke J; Ratti, Antonia; Fogh, Isabella; Gellera, Cinzia; Lauria, Giuseppe; Corti, Stefania; Cereda, Cristina; Sproviero, Daisy; D'Alfonso, Sandra; Sorarù, Gianni; Siciliano, Gabriele; Filosto, Massimiliano; Padovani, Alessandro; Chiò, Adriano; Calvo, Andrea; Moglia, Cristina; Brunetti, Maura; Canosa, Antonio; Grassano, Maurizio; Beghi, Ettore; Pupillo, Elisabetta; Logroscino, Giancarlo; Nefussy, Beatrice; Osmanovic, Alma; Nordin, Angelica; Lerner, Yossef; Zabari, Michal; Gotkine, Marc; Baloh, Robert H; Bell, Shaughn; Vourc'h, Patrick; Corcia, Philippe; Couratier, Philippe; Millecamps, Stéphanie; Meininger, Vincent; Salachas, François; Mora Pardina, Jesus S; Assialioui, Abdelilah; Rojas-García, Ricardo; Dion, Patrick A; Ross, Jay P; Ludolph, Albert C; Weishaupt, Jochen H; Brenner, David; Freischmidt, Axel; Bensimon, Gilbert; Brice, Alexis; Durr, Alexandra; Payan, Christine A M; Saker-Delye, Safa; Wood, Nicholas W; Topp, Simon; Rademakers, Rosa; Tittmann, Lukas; Lieb, Wolfgang; Franke, Andre; Ripke, Stephan; Braun, Alice; Kraft, Julia; Whiteman, David C; Olsen, Catherine M; Uitterlinden, Andre G; Hofman, Albert; Rietschel, Marcella; Cichon, Sven; Nöthen, Markus M; Amouyel, Philippe; Traynor, Bryan J; Singleton, Andrew B; Mitne Neto, Miguel; Cauchi, Ruben J; Ophoff, Roel A; Wiedau-Pazos, Martina; Lomen-Hoerth, Catherine; van Deerlin, Vivianna M; Grosskreutz, Julian; Roediger, Annekathrin; Gaur, Nayana; Jörk, Alexander; Barthel, Tabea; Theele, Erik; Ilse, Benjamin; Stubendorff, Beatrice; Witte, Otto W; Steinbach, Robert; Hübner, Christian A; Graff, Caroline; Brylev, Lev; Fominykh, Vera; Demeshonok, Vera; Ataulina, Anastasia; Rogelj, Boris; Koritnik, Blaž; Zidar, Janez; Ravnik-Glavač, Metka; Glavač, Damjan; Stević, Zorica; Drory, Vivian; Povedano, Monica; Blair, Ian P; Kiernan, Matthew C; Benyamin, Beben; Henderson, Robert D; Furlong, Sarah; Mathers, Susan; McCombe, Pamela A; Needham, Merrilee; Ngo, Shyuan T; Nicholson, Garth A; Pamphlett, Roger; Rowe, Dominic B; Steyn, Frederik J; Williams, Kelly L; Mather, Karen A; Sachdev, Perminder S; Henders, Anjali K; Wallace, Leanne; de Carvalho, Mamede; Pinto, Susana; Petri, Susanne; Weber, Markus; Rouleau, Guy A; Silani, Vincenzo; Curtis, Charles J; Breen, Gerome; Glass, Jonathan D; Brown, Robert H Jr; Landers, John E; Shaw, Christopher E; Andersen, Peter M; Groen, Ewout J N; van Es, Michael A; Pasterkamp, R Jeroen; Fan, Dongsheng; Garton, Fleur C; McRae, Allan F; Davey Smith, George; Gaunt, Tom R; Eberle, Michael A; Mill, Jonathan; McLaughlin, Russell L; Hardiman, Orla; Kenna, Kevin P; Wray, Naomi R; Tsai, Ellen; Runz, Heiko; Franke, Lude; Al-Chalabi, Ammar; Van Damme, Philip; van den Berg, Leonard H; Veldink, Jan H; Borst, Piet; Flavell, Richard A

Long-Term Tofersen in SOD1 Amyotrophic Lateral Sclerosis

托弗森治疗SOD1肌萎缩侧索硬化症的长期疗效

Miller, Timothy M; Cudkowicz, Merit E; Shaw, Pamela J; Genge, Angela; Sobue, Gen; Bucelli, Robert C; Chiò, Adriano; Van Damme, Philip; Ludolph, Albert C; Glass, Jonathan D; Andrews, Jinsy A; Babu, Suma; Benatar, Michael; McDermott, Christopher J; Salachas, François; Bruneteau, Gaëlle; Al-Chalabi, Ammar; Amorin, Matthew; Nestorov, Ivan; Graham, Danielle; Lin, Luan; Sun, Peng; McNeill, Manjit; Malek, Sohail; Inra, Jennifer; Garafalo, Steve; Fradette, Stephanie

Early brain-wide disruption of sleep microarchitecture in amyotrophic lateral sclerosis

肌萎缩侧索硬化症早期全脑睡眠微结构紊乱

Lang, Christina; Guillot, Simon J; Lule, Dorothee; Balz, Luisa T; Knehr, Antje; Weydt, Patrick; Dorst, Johannes; Kandler, Katharina; Muller, Hans-Peter; Kassubek, Jan; Wassermann, Laura; Da Cruz, Sandrine; Roselli, Francesco; Ludolph, Albert C; Bolborea, Matei; Dupuis, Luc

Incidence and Survival Rates of Frontotemporal Lobar Degeneration: Population-Based Registry Study

额颞叶变性的发病率和生存率:基于人群的登记研究

Nagel, Gabriele; Peter, Raphael Simon; Uzelac, Zeljko; Wernecke, Deborah; Niehaus, Ludwig; Trottenberg, Thomas; Jöbges, Michael; Dettmers, Christian; Bäzner, Hansjörg; Börtlein, Andreas; Althaus, Katharina; Mayer-Freitag, Kristina; Ratzka, Peter; Naumann, Markus; Lindner, Alfred; Chatzikonstantinou, Anastasios; Andres, Frank; Arnold, Guy; Blickhan, Marko; Opherk, Christian; Knier, Benjamin; Ertl, Michael; Metrikat, Jens; Huber, Roman; Thomas, Christine; Kozian, Ralf; Kimmig, Hubert; Demuth, Klaus; Hecht, Martin; Foerch, Christian; Kloetsch, Christof; Reinhard, Matthias; Bengel, Dietmar; Neuhaus, Oliver; Buttmann, Mathias; Volkmann, Jens; Pinkhardt, Elmar; Lichy, Christoph; Laske, Christoph; Beattie, James; Häckert, Jan; Jesse, Sarah; Brenner, David; Weishaupt, Jochen; Otto, Markus; Uttner, Ingo; Anderl-Straub, Sarah; Lulé, Dorothée E; Rothenbacher, Dietrich; Rosenbohm, Angela; Ludolph, Albert Christian

Disruption of the angiopoietin-like system connects lipid homeostasis and hypothalamic dysfunction in ALS

血管生成素样系统的紊乱将脂质稳态与肌萎缩侧索硬化症(ALS)中的下丘脑功能障碍联系起来。

Krishnamurthy, Sruthi Sankari; Buzatto, Adriana Zardini; Campkin, Caley; Müller, Hans-Peter; Wiesner, Diana; Weishaupt, Jochen; Klose, Veronika; Wiesenfarth, Maximilian; Elmas, Zeynep; Herrmann, Christine; Parlak, Özlem; Günther, Kornelia; Saad, Rami; Weiland, Ulrike; Dupuis, Luc; Ludolph, Albert; Li, Liang; Kassubek, Jan; Dorst, Johannes; Roselli, Francesco

Increased transmembrane protein 119 (TMEM119) levels in the cerebrospinal fluid of patients with mild cognitive impairment due to Alzheimer's disease suggest early microglial involvement

阿尔茨海默病引起的轻度认知障碍患者脑脊液中跨膜蛋白119 (TMEM119) 水平升高提示小胶质细胞早期参与。

Klassen, Paula; Alexudis, Christoforos; Klose, Veronika; de San José, Nerea Gómez; Huss, André; Bachhuber, Franziska; Soylu, Önder; Fazeli, Badrieh; Erhart, Deborah; Laible, Mona; Anderl-Straub, Sarah; Jesse, Sarah; Otto, Markus; Ludolph, Albert C; Tumani, Hayrettin; Halbgebauer, Steffen

Reldesemtiv in Amyotrophic Lateral Sclerosis: Results From the COURAGE-ALS Randomized Clinical Trial

Reldesemtiv治疗肌萎缩侧索硬化症:COURAGE-ALS随机临床试验结果

Shefner, Jeremy M; Cudkowicz, Merit E; Genge, Angela; Hardiman, Orla; Al-Chalabi, Ammar; Andrews, Jinsy A; Chio, Adriano; Corcia, Philippe; Couratier, Philippe; de Carvalho, Mamede; Heiman-Patterson, Terry; Henderson, Robert D; Ingre, Caroline; Johnston, Wendy; Ludolph, Albert; Maragakis, Nicholas J; Miller, Timothy M; Mora, Jesus S; Petri, Susanne; Simmons, Zachary; van den Berg, Leonard H; Zinman, Lorne; Kupfer, Stuart; Malik, Fady I; Meng, Lisa; Simkins, Tyrell J; Wei, Jenny; Wolff, Andrew A; Rudnicki, Stacy A

CREB3 gain of function variants protect against ALS.

CREB3 功能获得性变异可预防 ALS

Megat Salim, Marques Christine, Hernán-Godoy Marina, Sellier Chantal, Stuart-Lopez Geoffrey, Dirrig-Grosch Sylvie, Gorin Charlotte, Brunet Aurore, Fischer Mathieu, Keime Céline, Kessler Pascal, Mendoza-Parra Marco Antonio, Zwamborn Ramona A J, Veldink Jan H, Scholz Sonja W, Ferrucci Luigi, Ludolph Albert, Traynor Bryan, Chio Adriano, Dupuis Luc, Rouaux Caroline

Disturbed Spatial WNT Activation-A Potential Driver of the Reticularized Skin Phenotype in Systemic Sclerosis.

空间 WNT 激活紊乱——系统性硬化症网状皮肤表型的潜在驱动因素

Fakhouri Sara Chenguiti, Zhu Honglin, Li Yi-Nan, Ronicke Moritz, Rigau Aleix Rius, Dees Clara, Konstantinidis Laura, Schmid Ralf, Matei Alexandru-Emil, Eckstein Markus, Geppert Carol, Ludolph Ingo, Kreuter Alexander, Sticherling Michael, Berking Carola, Horch Raymund E, Schett Georg, Distler Jörg H W, Bergmann Christina

Comparative analysis of cerebrospinal fluid neurofilament medium, light and heavy chain in neurodegenerative diseases using an in-house assay for the detection of neurofilament medium chain.

利用内部开发的检测神经丝中链的方法,对神经退行性疾病中脑脊液神经丝中链、轻链和重链进行比较分析。

Fazeli Badrieh, Botzenhardt Sara, Bachhuber Franziska, Klassen Paula, Klose Veronika, Dorst Johannes, Wiesenfarth Maximilian, Uzelac Zeljko, Jesse Sarah, Brenner David, Anderl-Straub Sarah, Ludolph Albert C, Otto Markus, Weishaupt Jochen, Tumani Hayrettin, Halbgebauer Steffen