Electrophysiological Abnormalities in VLCAD Deficient hiPSC-Cardiomyocytes Can Be Improved by Lowering Accumulation of Fatty Acid Oxidation Intermediates
降低脂肪酸氧化中间体的积累可以改善 VLCAD 缺陷型 hiPSC 心肌细胞的电生理异常
期刊:International Journal of Molecular Sciences
影响因子:0.7
doi:10.3390/ijms21072589
Suzan J G Knottnerus, Isabella Mengarelli, Rob C I Wüst, Antonius Baartscheer, Jeannette C Bleeker, Ruben Coronel, Sacha Ferdinandusse, Kaomei Guan, Lodewijk IJlst, Wener Li, Xiaojing Luo, Vincent M Portero, Ying Ulbricht, Gepke Visser, Ronald J A Wanders, Frits A Wijburg, Arie O Verkerk, Riekelt H