A Y374X TDP43 truncation leads to an altered metabolic profile in amyotrophic lateral sclerosis fibroblasts driven by pyruvate and TCA cycle intermediate alterations
Y374X TDP43 截断导致肌萎缩侧索硬化成纤维细胞的代谢特征发生改变,这是由丙酮酸和 TCA 循环中间体改变引起的
期刊:Frontiers in Aging Neuroscience
影响因子:4.1
doi:10.3389/fnagi.2023.1151848
Scott P Allen, Afnan Al Sultan, Elaine Kabucho Kibirige, Erin Tonkiss, Keaton J Hamer, Lydia M Castelli, Ya-Hui Lin, Sarah Roscoe, Nikolaos Stefanidis, Richard J Mead, J Robin Highley, Johnathan Cooper-Knock, Guillaume M Hautbergue, Paul R Heath, Janine Kirby, Pamela J Shaw