日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Transforming growth factor-beta (TGF-β) in the pathogenesis of hereditary thoracic aneurysm disorders

转化生长因子-β (TGF-β) 在遗传性胸主动脉瘤疾病发病机制中的作用

Espinoza Camejo, Wendy A; Bramel, Emily E; MacFarlane, Elena Gallo

Map2k6 is a potent genetic modifier of arterial rupture in vascular Ehlers-Danlos syndrome mice.

Map2k6 是血管型埃勒斯-当洛斯综合征小鼠动脉破裂的强效遗传修饰因子

Bowen Caitlin J, Sorber Rebecca, Calderón Giadrosic Juan Francisco, Doyle Jefferson J, Rykiel Graham, Burger Zachary, Zhang Xiaoyan, Espinoza Camejo Wendy A, Anderson Nicole, Sabnis Simone, Bellini Chiara, MacFarlane Elena Gallo, Dietz Harry C

Intrinsic Gata4 expression sensitizes the aortic root to dilation in a Loeys-Dietz syndrome mouse model.

在 Loeys-Dietz 综合征小鼠模型中,内在 Gata4 表达使主动脉根部对扩张更加敏感

Bramel Emily E, Camejo Wendy A Espinoza, Creamer Tyler J, Restrepo Leda, Saqib Muzna, Bagirzadeh Rustam, Zeng Anthony, Mitchell Jacob T, Stein-O'Brien Genevieve L, Pedroza Albert J, Fischbein Michael P, Dietz Harry C, MacFarlane Elena Gallo

Early clinical outcomes and molecular smooth muscle cell phenotyping using a prophylactic aortic arch replacement strategy in Loeys-Dietz syndrome.

采用预防性主动脉弓置换策略治疗 Loeys-Dietz 综合征的早期临床结果和分子平滑肌细胞表型分析

Pedroza Albert J, Cheng Paul, Dalal Alex R, Baeumler Kathrin, Kino Aya, Tognozzi Emily, Shad Rohan, Yokoyama Nobu, Nakamura Ken, Mitchel Olivia, Hiesinger William, MacFarlane Elena Gallo, Fleischmann Dominik, Woo Y Joseph, Quertermous Thomas, Fischbein Michael P

Oxytocin antagonism prevents pregnancy-associated aortic dissection in a mouse model of Marfan syndrome

在马凡综合征小鼠模型中,催产素拮抗作用可预防妊娠相关性主动脉夹层。

Habashi, Jennifer Pardo; MacFarlane, Elena Gallo; Bagirzadeh, Rustam; Bowen, Caitlin; Huso, Nicholas; Chen, Yichun; Bedja, Djahida; Creamer, Tyler J; Rykiel, Graham; Manning, Maurice; Huso, David; Dietz, Harry C

Ectopic calcification in pseudoxanthoma elasticum responds to inhibition of tissue-nonspecific alkaline phosphatase

假性黄色瘤中的异位钙化对组织非特异性碱性磷酸酶抑制剂有反应

Ziegler, Shira G; Ferreira, Carlos R; MacFarlane, Elena Gallo; Riddle, Ryan C; Tomlinson, Ryan E; Chew, Emily Y; Martin, Ludovic; Ma, Chen-Ting; Sergienko, Eduard; Pinkerton, Anthony B; Millán, José Luis; Gahl, William A; Dietz, Harry C

TGF-β Family Signaling in Connective Tissue and Skeletal Diseases

TGF-β家族信号在结缔组织和骨骼疾病中的作用

MacFarlane, Elena Gallo; Haupt, Julia; Dietz, Harry C; Shore, Eileen M