Induced pluripotent stem cell models of Zellweger spectrum disorder show impaired peroxisome assembly and cell type-specific lipid abnormalities
泽尔韦格谱系障碍的诱导性多能干细胞模型显示过氧化物酶体组装受损和细胞类型特异性脂质异常
期刊:Stem Cell Research
影响因子:7.1
doi:10.1186/s13287-015-0149-3
Xiao-Ming Wang, Wing Yan Yik, Peilin Zhang, Wange Lu, Ning Huang, Bo Ram Kim, Darryl Shibata, Madison Zitting, Robert H Chow, Ann B Moser, Steven J Steinberg, Joseph G Hacia2