C9orf72 arginine-rich dipeptide proteins interact with ribosomal proteins in vivo to induce a toxic translational arrest that is rescued by eIF1A
C9orf72 富含精氨酸的二肽蛋白在体内与核糖体蛋白相互作用,诱导毒性翻译停滞,而 eIF1A 可挽救这种停滞
期刊:Acta Neuropathologica
影响因子:9.3
doi:10.1007/s00401-018-1946-4
Thomas G Moens, Teresa Niccoli, Katherine M Wilson, Magda L Atilano, Nicol Birsa, Lauren M Gittings, Benedikt V Holbling, Miranda C Dyson, Annora Thoeng, Jacob Neeves, Idoia Glaria, Lu Yu, Julia Bussmann, Erik Storkebaum, Mercedes Pardo, Jyoti S Choudhary, Pietro Fratta, Linda Partridge, Adrian M Is