日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

The missense mutation C667F in murine β-dystroglycan causes embryonic lethality, myopathy and blood-brain barrier destabilization

小鼠 β-肌营养不良症蛋白聚糖中的错义突变 C667F 导致胚胎致死、肌病和血脑屏障不稳定

Rui Lois Tan, Francesca Sciandra, Wolfgang Hübner, Manuela Bozzi, Jens Reimann, Susanne Schoch, Andrea Brancaccio, Sandra Blaess

Analysis of the GFP-labelled β-dystroglycan interactome in HEK-293 transfected cells reveals novel intracellular networks

HEK-293 转染细胞中 GFP 标记的 β-dystroglycan 相互作用组的分析揭示了新的细胞内网络

Francesca Sciandra, Claudia Desiderio, Federica Vincenzoni, Simona Viscuso, Manuela Bozzi, Wolfgang Hübner, Guadalupe Elizabeth Jimenez-Gutierrez, Bulmaro Cisneros, Andrea Brancaccio

Verbascoside Elicits Its Beneficial Effects by Enhancing Mitochondrial Spare Respiratory Capacity and the Nrf2/HO-1 Mediated Antioxidant System in a Murine Skeletal Muscle Cell Line

毛蕊花苷通过增强小鼠骨骼肌细胞系中的线粒体备用呼吸能力和 Nrf2/HO-1 介导的抗氧化系统发挥其有益作用

Francesca Sciandra, Patrizia Bottoni, Marinella De Leo, Alessandra Braca, Andrea Brancaccio, Manuela Bozzi

The enzymatic processing of α-dystroglycan by MMP-2 is controlled by two anchoring sites distinct from the active site

MMP-2 对 α-肌营养不良症聚糖的酶促加工由两个不同于活性位点的锚定位点控制

Magda Gioia, Giovanni Francesco Fasciglione, Diego Sbardella, Francesca Sciandra, MariaLuisa Casella, Serena Camerini, Marco Crescenzi, Alessandro Gori, Umberto Tarantino, Paola Cozza, Andrea Brancaccio, Massimo Coletta, Manuela Bozzi

Structural flexibility of human α-dystroglycan

人类 α-肌营养不良蛋白聚糖的结构灵活性

Sonia Covaceuszach, Manuela Bozzi, Maria Giulia Bigotti, Francesca Sciandra, Petr Valeryevich Konarev, Andrea Brancaccio, Alberto Cassetta

Evaluation of the effect of a floxed Neo cassette within the dystroglycan (Dag1) gene

评估 dystroglycan (Dag1) 基因中 floxed Neo 盒的作用

Francesca Sciandra, Bianca Maria Scicchitano, Giulia Signorino, Maria Giulia Bigotti, Barbara Tavazzi, Francesca Lombardi, Manuela Bozzi, Gigliola Sica, Bruno Giardina, Sandra Blaess, Andrea Brancaccio

The Structure of the T190M Mutant of Murine α-Dystroglycan at High Resolution: Insight into the Molecular Basis of a Primary Dystroglycanopathy

小鼠 α-Dystroglycan 的 T190M 突变体的高分辨率结构:深入了解原发性 Dystroglycan 病的分子基础

Manuela Bozzi, Alberto Cassetta, Sonia Covaceuszach, Maria Giulia Bigotti, Saskia Bannister, Wolfgang Hübner, Francesca Sciandra, Doriano Lamba, Andrea Brancaccio

Proteasome Activity Is Affected by Fluctuations in Insulin-Degrading Enzyme Distribution

蛋白酶体活性受胰岛素降解酶分布波动的影响

Diego Sbardella, Grazia Raffaella Tundo, Francesca Sciandra, Manuela Bozzi, Magda Gioia, Chiara Ciaccio, Umberto Tarantino, Andrea Brancaccio, Massimo Coletta, Stefano Marini

Probing the stability of the "naked" mucin-like domain of human α-dystroglycan

探索人类 α-肌营养不良症聚糖“裸露”粘蛋白样结构域的稳定性

Manuela Bozzi, Enrico Di Stasio, Giovanni Luca Scaglione, Claudia Desiderio, Claudia Martelli, Bruno Giardina, Francesca Sciandra, Andrea Brancaccio