日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

ABC-transporter CFTR folds with high fidelity through a modular, stepwise pathway

ABC 转运蛋白 CFTR 通过模块化、逐步的途径高保真地折叠

Jisu Im, Tamara Hillenaar, Hui Ying Yeoh, Priyanka Sahasrabudhe, Marjolein Mijnders, Marcel van Willigen, Azib Hagos, Eduardo de Mattos, Peter van der Sluijs #, Ineke Braakman #

The CFTR P67L variant reveals a key role for N-terminal lasso helices in channel folding, maturation, and pharmacologic rescue

CFTR P67L 变体揭示了 N 端套索螺旋在通道折叠、成熟和药物拯救中的关键作用

Carleen Mae Sabusap, Disha Joshi, Luba Simhaev, Kathryn E Oliver, Hanoch Senderowitz, Marcel van Willigen, Ineke Braakman, Andras Rab, Eric J Sorscher, Jeong S Hong

Folding-function relationship of the most common cystic fibrosis-causing CFTR conductance mutants

最常见的囊性纤维化致病 CFTR 传导突变体的折叠功能关系

Marcel van Willigen, Annelotte M Vonk, Hui Ying Yeoh, Evelien Kruisselbrink, Bertrand Kleizen, Cornelis K van der Ent, Maarten R Egmond, Hugo R de Jonge, Ineke Braakman, Jeffrey M Beekman, Peter van der Sluijs