ADA-deficient SCID is associated with a specific microenvironment and bone phenotype characterized by RANKL/OPG imbalance and osteoblast insufficiency
ADA 缺陷型严重联合免疫缺陷症 (SCID) 与特定的微环境和骨表型有关，其特征是 RANKL/OPG 失衡和成骨细胞功能不足
期刊:Blood
影响因子:21
doi:10.1182/blood-2009-03-209221
Aisha V Sauer, Emanuela Mrak, Raisa Jofra Hernandez, Elena Zacchi, Francesco Cavani, Miriam Casiraghi, Eyal Grunebaum, Chaim M Roifman, Maria C Cervi, Alessandro Ambrosi, Filippo Carlucci, Maria Grazia Roncarolo, Anna Villa, Alessandro Rubinacci, Alessandro Aiuti
