Glutamine Synthetase 1 Increases Autophagy Lysosomal Degradation of Mutant Huntingtin Aggregates in Neurons, Ameliorating Motility in a Drosophila Model for Huntington's Disease
谷氨酰胺合成酶 1 可增强神经元中突变型亨廷顿蛋白聚集体的自噬溶酶体降解,从而改善亨廷顿氏病果蝇模型的运动能力
期刊:Cells
影响因子:5.1
doi:10.3390/cells9010196
Luisa Vernizzi, Chiara Paiardi, Giusimaria Licata, Teresa Vitali, Stefania Santarelli, Martino Raneli, Vera Manelli, Manuela Rizzetto, Mariarosa Gioria, Maria E Pasini, Daniela Grifoni, Maria A Vanoni, Cinzia Gellera, Franco Taroni, Paola Bellosta
信号转导
神经
细胞生物学
WB
Autophagy
Drosophila