日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

GM1 Oligosaccharide Ameliorates Rett Syndrome Phenotypes In Vitro and In Vivo via Trk Receptor Activation

GM1 寡糖通过激活 Trk 受体在体内和体外改善 Rett 综合征表型

Maria Fazzari, Giulia Lunghi, Emma Veronica Carsana, Manuela Valsecchi, Eleonora Spiombi, Martina Breccia, Silvia Rosanna Casati, Silvia Pedretti, Nico Mitro, Laura Mauri, Maria Grazia Ciampa, Sandro Sonnino, Nicoletta Landsberger, Angelisa Frasca, Elena Chiricozzi

GM1 oligosaccharide efficacy against α-synuclein aggregation and toxicity in vitro

GM1 寡糖体外对抗 α-突触核蛋白聚集和毒性的功效

Maria Fazzari, Erika Di Biase, Ludovica Zaccagnini, Alexandre Henriques, Noëlle Callizot, Maria Grazia Ciampa, Laura Mauri, Emma Veronica Carsana, Nicoletta Loberto, Massimo Aureli, Luigi Mari, Monica Civera, Francesca Vasile, Sandro Sonnino, Tim Bartels, Elena Chiricozzi, Giulia Lunghi

GM1 Oligosaccharide Efficacy in Parkinson's Disease: Protection against MPTP

GM1寡糖对帕金森病的疗效:预防MPTP

Maria Fazzari, Giulia Lunghi, Alexandre Henriques, Noëlle Callizot, Maria Grazia Ciampa, Laura Mauri, Simona Prioni, Emma Veronica Carsana, Nicoletta Loberto, Massimo Aureli, Luigi Mari, Sandro Sonnino, Elena Chiricozzi, Erika Di Biase

GM1 ganglioside exerts protective effects against glutamate-excitotoxicity via its oligosaccharide in wild-type and amyotrophic lateral sclerosis motor neurons

GM1 神经节苷脂通过其寡糖在野生型和肌萎缩侧索硬化症运动神经元中发挥对谷氨酸兴奋性毒性的保护作用

Giulia Lunghi, Erika Di Biase, Emma Veronica Carsana, Alexandre Henriques, Noelle Callizot, Laura Mauri, Maria Grazia Ciampa, Luigi Mari, Nicoletta Loberto, Massimo Aureli, Sandro Sonnino, Michael Spedding, Elena Chiricozzi, Maria Fazzari

Gangliosides in the differentiation process of primary neurons: the specific role of GM1-oligosaccharide

神经节苷脂在原代神经元分化过程中的作用:GM1-寡糖的具体作用

Erika Di Biase, Giulia Lunghi, Maria Fazzari, Margherita Maggioni, Diego Yuri Pomè, Manuela Valsecchi, Maura Samarani, Pamela Fato, Maria Grazia Ciampa, Simona Prioni, Laura Mauri, Sandro Sonnino, Elena Chiricozzi

GM1 Oligosaccharide Crosses the Human Blood-Brain Barrier In Vitro by a Paracellular Route

GM1 寡糖通过旁细胞途径体外穿过人类血脑屏障

Erika Di Biase, Giulia Lunghi, Margherita Maggioni, Maria Fazzari, Diego Yuri Pomè, Nicoletta Loberto, Maria Grazia Ciampa, Pamela Fato, Laura Mauri, Emmanuel Sevin, Fabien Gosselet, Sandro Sonnino, Elena Chiricozzi

Parkinson's disease recovery by GM1 oligosaccharide treatment in the B4galnt1+/- mouse model

GM1 寡糖治疗 B4galnt1+/- 小鼠模型中的帕金森病康复情况

Elena Chiricozzi, Laura Mauri, Giulia Lunghi, Erika Di Biase, Maria Fazzari, Margherita Maggioni, Manuela Valsecchi, Simona Prioni, Nicoletta Loberto, Diego Yuri Pomè, Maria Grazia Ciampa, Pamela Fato, Gianluca Verlengia, Stefano Cattaneo, Robert Assini, Gusheng Wu, Samar Alselehdar, Robert W Ledeen

Aminoglycoside drugs induce efficient read-through of CDKL5 nonsense mutations, slightly restoring its kinase activity

氨基糖苷类药物可诱导 CDKL5 无义突变的有效读通,略微恢复其激酶活性

Maria Fazzari, Angelisa Frasca, Francesco Bifari, Nicoletta Landsberger

Splicing Mutations Impairing CDKL5 Expression and Activity Can be Efficiently Rescued by U1snRNA-Based Therapy

基于 U1snRNA 的疗法可有效挽救损害 CDKL5 表达和活性的剪接突变

Dario Balestra, Domenico Giorgio, Matteo Bizzotto, Maria Fazzari, Bruria Ben Zeev, Mirko Pinotti, Nicoletta Landsberger, Angelisa Frasca

CDKL5 localizes at the centrosome and midbody and is required for faithful cell division

CDKL5 定位于着丝粒和中体,是细胞忠实分裂所必需的

Isabella Barbiero, Davide Valente, Chetan Chandola, Fiorenza Magi, Anna Bergo, Laura Monteonofrio, Marco Tramarin, Maria Fazzari, Silvia Soddu, Nicoletta Landsberger, Cinzia Rinaldo, Charlotte Kilstrup-Nielsen