日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

High mobility group box 1 (HMGB1) is a potential disease biomarker in cell and mouse models of Duchenne muscular dystrophy

高迁移率族蛋白 1 (HMGB1) 是杜氏肌营养不良症细胞和小鼠模型中的潜在疾病生物标志物

Rebecca A Slick, Jessica Sutton, Margaret Haberman, Benjamin S O'Brien, Jennifer A Tinklenberg, Aashay Mardikar, Mariah J Prom, Margaret Beatka, Melanie Gartz, Mark A Vanden Avond, Emily Siebers, David L Mack, J Patrick Gonzalez, Allison D Ebert, Kanneboyina Nagaraju, Michael W Lawlor

Aberrations in Energetic Metabolism and Stress-Related Pathways Contribute to Pathophysiology in the Neb Conditional Knockout Mouse Model of Nemaline Myopathy

能量代谢和应激相关途径的异常导致 Neb 条件性基因敲除小鼠模型的杆状体肌病病理生理学

Rebecca A Slick, Jennifer A Tinklenberg, Jessica Sutton, Liwen Zhang, Hui Meng, Margaret J Beatka, Mark Vanden Avond, Mariah J Prom, Emily Ott, Federica Montanaro, James Heisner, Rafael Toro, Henk Granzier, Aron M Geurts, David F Stowe, R Blake Hill, Michael W Lawlor

Different Mouse Models of Nemaline Myopathy Harboring Acta1 Mutations Display Differing Abnormalities Related to Mitochondrial Biology

携带 Acta1 突变的线粒体肌病不同小鼠模型表现出与线粒体生物学相关的不同异常

Jennifer A Tinklenberg, Rebecca A Slick, Jessica Sutton, Liwen Zhang, Hui Meng, Margaret J Beatka, Mark Vanden Avond, Mariah J Prom, Emily Ott, Federica Montanaro, James Heisner, Rafael Toro, Edna C Hardeman, Aron M Geurts, David F Stowe, R Blake Hill, Michael W Lawlor

Muscle-directed gene therapy corrects Pompe disease and uncovers species-specific GAA immunogenicity

肌肉导向基因治疗可纠正庞贝病并揭示物种特异性 GAA 免疫原性

Michelle Eggers, Charles H Vannoy, Jianyong Huang, Pravinkumar Purushothaman, Jacqueline Brassard, Carlos Fonck, Hui Meng, Mariah J Prom, Michael W Lawlor, Justine Cunningham, Chanchal Sadhu, Fulvio Mavilio

Adherence to and changes in mental and physiological health during an 8-week yoga intervention: A pilot study

周瑜伽干预期间心理和生理健康的依从性和变化:一项初步研究

Bethany Forseth, Michele Polfuss, Michael Brondino, Stacy D Hunter, Michael W Lawlor, Margaret J Beatka, Mariah J Prom, Janis Eells, Jeri-Ann Lyons

Cardiomyocyte-produced miR-339-5p mediates pathology in Duchenne muscular dystrophy cardiomyopathy

心肌细胞产生的 miR-339-5p 介导杜氏肌营养不良症心肌病的病理

Melanie Gartz, Margaret Beatka, Mariah J Prom, Jennifer L Strande, Michael W Lawlor

Association between yoga, physiologic and psychologic health: A cross sectional study

瑜伽与生理和心理健康之间的关系:一项横断面研究

Bethany Forseth, Michele Polfuss, Michael Brondino, Michael W Lawlor, Margaret J Beatka, Mariah J Prom, Janis Eells, Jeri-Ann Lyons

Voluntary wheel running complements microdystrophin gene therapy to improve muscle function in mdx mice

自愿跑轮训练补充微肌营养不良蛋白基因疗法以改善 mdx 小鼠的肌肉功能

Shelby E Hamm, Daniel D Fathalikhani, Katherine E Bukovec, Adele K Addington, Haiyan Zhang, Justin B Perry, Ryan P McMillan, Michael W Lawlor, Mariah J Prom, Mark A Vanden Avond, Suresh N Kumar, Kirsten E Coleman, J B Dupont, David L Mack, David A Brown, Carl A Morris, J Patrick Gonzalez, Robert W G