日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Cold Exposure Exacerbates Cardiac Dysfunction in a Model of Heart Failure with Preserved Ejection Fraction in Male and Female C57Bl/6J Mice

在射血分数保留的心力衰竭模型中,寒冷暴露会加剧雄性和雌性C57Bl/6J小鼠的心脏功能障碍

Thibodeau, Sara-Ève; Legros, Marie-Lune; Labbé, Emylie-Ann; Walsh-Wilkinson, Élisabeth; Morin-Grandmont, Audrey; Beji, Sarra; Arsenault, Marie; Caron, Alexandre; Couet, Jacques

Mice lacking the mitochondrial exonuclease MGME1 develop inflammatory kidney disease with glomerular dysfunction

缺乏线粒体核酸外切酶 MGME1 的小鼠会患上伴有肾小球功能障碍的炎症性肾病

Dusanka Milenkovic, Adrián Sanz-Moreno, Julia Calzada-Wack, Birgit Rathkolb, Oana Veronica Amarie, Raffaele Gerlini, Antonio Aguilar-Pimentel, Jelena Misic, Marie-Lune Simard, Eckhard Wolf, Helmut Fuchs, Valerie Gailus-Durner, Martin Hrabě de Angelis, Nils-Göran Larsson

Genome editing in mitochondria corrects a pathogenic mtDNA mutation in vivo

线粒体基因组编辑可纠正体内致病的线粒体DNA突变

Payam A Gammage, Carlo Viscomi, Marie-Lune Simard, Ana S H Costa, Edoardo Gaude, Christopher A Powell, Lindsey Van Haute, Beverly J McCann, Pedro Rebelo-Guiomar, Raffaele Cerutti, Lei Zhang, Edward J Rebar, Massimo Zeviani, Christian Frezza, James B Stewart, Michal Minczuk

Mice lacking the mitochondrial exonuclease MGME1 accumulate mtDNA deletions without developing progeria

缺乏线粒体核酸外切酶 MGME1 的小鼠会积累线粒体 DNA 缺失,但不会患上早衰症

Stanka Matic, Min Jiang, Thomas J Nicholls, Jay P Uhler, Caren Dirksen-Schwanenland, Paola Loguercio Polosa, Marie-Lune Simard, Xinping Li, Ilian Atanassov, Oliver Rackham, Aleksandra Filipovska, James B Stewart, Maria Falkenberg, Nils-Göran Larsson, Dusanka Milenkovic

A novel histochemistry assay to assess and quantify focal cytochrome c oxidase deficiency

一种用于评估和定量局灶性细胞色素c氧化酶缺乏症的新型组织化学检测方法

Simard, Marie-Lune; Mourier, Arnaud; Greaves, Laura C; Taylor, Robert W; Stewart, James B

A Phenotype-Driven Approach to Generate Mouse Models with Pathogenic mtDNA Mutations Causing Mitochondrial Disease

利用表型驱动方法构建携带致病性线粒体DNA突变的小鼠模型,以治疗线粒体疾病

Kauppila, Johanna H K; Baines, Holly L; Bratic, Ana; Simard, Marie-Lune; Freyer, Christoph; Mourier, Arnaud; Stamp, Craig; Filograna, Roberta; Larsson, Nils-Göran; Greaves, Laura C; Stewart, James B

Noninvasive imaging of endogenous neural stem cell mobilization in vivo using positron emission tomography

使用正电子发射断层扫描对体内内源性神经干细胞动员进行无创成像

Maria Adele Rueger, Heiko Backes, Maureen Walberer, Bernd Neumaier, Roland Ullrich, Marie-Lune Simard, Beata Emig, Gereon Rudolf Fink, Mathias Hoehn, Rudolf Graf, Michael Schroeter