日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

A Drug Combination Rescues Frataxin-Dependent Neural and Cardiac Pathophysiology in FA Models

药物组合挽救了 FA 模型中 Frataxin 依赖的神经和心脏病理生理学

Rosella Abeti, Mittal Jasoliya, Sahar Al-Mahdawi, Mark Pook, Cristina Gonzalez-Robles, Chun Kiu Hui, Gino Cortopassi, Paola Giunti

DNA methylation in Friedreich ataxia silences expression of frataxin isoform E

弗里德赖希共济失调中的 DNA 甲基化抑制了 frataxin 异构体 E 的表达

Layne N Rodden, Kaitlyn M Gilliam, Christina Lam, Teerapat Rojsajjakul, Clementina Mesaros, Chiara Dionisi, Mark Pook, Massimo Pandolfo, David R Lynch, Ian A Blair, Sanjay I Bidichandani

HMTase Inhibitors as a Potential Epigenetic-Based Therapeutic Approach for Friedreich's Ataxia

HMTase 抑制剂作为弗里德赖希共济失调的潜在表观遗传治疗方法

Mursal Sherzai, Adamo Valle, Nicholas Perry, Ester Kalef-Ezra, Sahar Al-Mahdawi, Mark Pook, Sara Anjomani Virmouni

Dimethyl fumarate dosing in humans increases frataxin expression: A potential therapy for Friedreich's Ataxia

富马酸二甲酯在人体中的给药会增加 frataxin 的表达:一种治疗弗里德赖希共济失调的潜在疗法

Mittal Jasoliya, Francesco Sacca, Sunil Sahdeo, Frederic Chedin, Chiara Pane, Vincenzo Brescia Morra, Alessandro Filla, Mark Pook, Gino Cortopassi

Cytokine therapy-mediated neuroprotection in a Friedreich's ataxia mouse model

细胞因子治疗介导的弗里德赖希共济失调小鼠模型中的神经保护作用

Kevin C Kemp, Nadia Cerminara, Kelly Hares, Juliana Redondo, Amelia J Cook, Harry R Haynes, Bronwen R Burton, Mark Pook, Richard Apps, Neil J Scolding, Alastair Wilkins

Frataxin deficiency increases cyclooxygenase 2 and prostaglandins in cell and animal models of Friedreich's ataxia

Frataxin 缺乏会导致弗里德赖希共济失调细胞和动物模型中的环氧合酶 2 和前列腺素增加

Genki Hayashi, Yan Shen, Theresa L Pedersen, John W Newman, Mark Pook, Gino Cortopassi