Evaluation of mitochondrial bioenergetics, dynamics, endoplasmic reticulum-mitochondria crosstalk, and reactive oxygen species in fibroblasts from patients with complex I deficiency
评估复合物 I 缺乏症患者成纤维细胞中的线粒体生物能量学、动力学、内质网-线粒体串扰和活性氧
期刊:Scientific Reports
影响因子:3.8
doi:10.1038/s41598-018-19543-3
Guilhian Leipnitz, Al-Walid Mohsen, Anuradha Karunanidhi, Bianca Seminotti, Vera Y Roginskaya, Desiree M Markantone, Mateus Grings, Stephanie J Mihalik, Peter Wipf, Bennett Van Houten, Jerry Vockley