Evidence for the Misfolding of the A1 Domain within Multimeric von Willebrand Factor in Type 2 von Willebrand Disease
型血管性血友病中多聚体血管性血友病因子 A1 结构域错误折叠的证据
期刊:Journal of Molecular Biology
影响因子:4.7
doi:10.1016/j.jmb.2019.09.022
Alexander Tischer, Maria A Brehm, Venkata R Machha, Laurie Moon-Tasson, Linda M Benson, Katelynn J Nelton, Rachel R Leger, Tobias Obser, Marina Martinez-Vargas, Steven T Whitten, Dong Chen, Rajiv K Pruthi, H Robert Bergen 3rd, Miguel A Cruz, Reinhard Schneppenheim, Matthew Auton