日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

The International/Canadian hereditary angioedema guideline

国际/加拿大遗传性血管性水肿指南

Betschel, Stephen; Binkley, Karen; Borici-Mazi, Rozita; Chapdelaine, Hugo; Hébert, Jacques; Kanani, Amin; Keith, Paul K; Lacuesta, Gina; Waserman, Susan; Yang, William; Palda, Valerie; Lang-Robertson, Kelly; Aygören-Pürsün, Emel; Banerji, Aleena; Bernstein, Jonathan A; Caballero, Teresa; Farkas, Henriette; Grumach, Anete S; Hide, Michihiro; Katelaris, Connie; Longhurst, Hilary J; Magerl, Markus; Riedl, Marc; Zanichelli, Andrea; Zuraw, Bruce; Adatia, Adil; Boursiquot, Jean-Nicolas; Connors, Lori; Cook, Victoria; Cooper, Michelle; Fu, Lisa; Gill, Parwinder; Goodyear, Dawn; Jagdis, Amanda; Jeimy, Samira; Kalicinsky, Chrystyna; Kamra, Palinder; Kan, Manstein; Kim, Harold; Laramée, Benoît; Lee, Erika; Leith, Eric; Marois, Louis; McCusker, Christine; O'Keefe, Andrew; Othman, Ibraheem; Poon, Man-Chiu; St-Pierre, Charles; Stepaniuk, Peter; Tsai, Ellie; Uminski, Kelsey

Multiomics dissection of human RAG deficiency reveals distinctive patterns of immune dysregulation but a common inflammatory signature.

对人类 RAG 缺陷的多组学分析揭示了独特的免疫失调模式,但具有共同的炎症特征。

Bosticardo Marita, Dobbs Kerry, Delmonte Ottavia M, Martins Andrew J, Pala Francesca, Kawai Tomoki, Kenney Heather, Magro Gloria, Rosen Lindsey B, Yamazaki Yasuhiro, Yu Hsin-Hui, Calzoni Enrica, Lee Yu Nee, Liu Can, Stoddard Jennifer, Niemela Julie, Fink Danielle, Castagnoli Riccardo, Ramba Meredith, Cheng Aristine, Riley Deanna, Oikonomou Vasileios, Shaw Elana, Belaid Brahim, Keles Sevgi, Al-Herz Waleed, Cancrini Caterina, Cifaldi Cristina, Baris Safa, Sharapova Svetlana, Schuetz Catharina, Gennery Andrew R, Freeman Alexandra F, Somech Raz, Choo Sharon, Giliani Silvia C, Güngör Tayfun, Drozdov Daniel, Meyts Isabelle, Moshous Despina, Neven Benedicte, Abraham Roshini S, El-Marsafy Aisha, Kanariou Maria, King Alejandra, Licciardi Francesco, Cruz-Muñoz Mario E, Palma Paolo, Poli Cecilia, Adeli Mehdi, Algeri Mattia, Alroqi Fayhan J, Bastard Paul, Bergerson Jenna R E, Booth Claire, Brett Ana, Burns Siobhan O, Butte Manish J, Padem Nurcicek, de la Morena M, Dbaibo Ghassan, de Ravin Suk See, Dimitrova Dimana, Djidjik Reda, Dorna Mayra B, Dutmer Cullen M, Elfeky Reem, Facchetti Fabio, Fuleihan Ramsay L, Geha Raif S, Gonzalez-Granado Luis I, Haljasmägi Liis, Ale Hanadys, Hayward Anthony, Hifanova Anna M, Ip Winnie, Kaplan Blanka, Kapoor Neena, Karakoc-Aydiner Elif, Kärner Jaanika, Keller Michael D, Dávila Saldaña Blachy J, Kiykim Ayça, Kuijpers Taco W, Kuznetsova Elena E, Latysheva Elena A, Leiding Jennifer W, Locatelli Franco, Alva-Lozada Guisela, McCusker Christine, Celmeli Fatih, Morsheimer Megan, Ozen Ahmet, Parvaneh Nima, Pasic Srdjan, Plebani Alessandro, Preece Kahn, Prockop Susan, Sakovich Inga S, Starkova Elena E, Torgerson Troy, Verbsky James, Walter Jolan E, Ward Brant, Wisner Elizabeth L, Draper Deborah, Myint-Hpu Katherine, Truong Pooi M, Lionakis Michail S, Similuk Morgan B, Walkiewicz Magdalena A, Klion Amy, Holland Steven M, Oguz Cihan, Bogunovic Dusan, Kisand Kai, Su Helen C, Tsang John S, Kuhns Douglas, Villa Anna, Rosenzweig Sergio D, Pittaluga Stefania, Notarangelo Luigi D

Anaphylaxis Management in Paediatric Patients Undergoing Milk Oral Immunotherapy

接受牛奶口服免疫疗法的儿科患者的过敏反应管理

Buyansky, Dimitry; Khalaf, Roy; Gabrielli, Sofianne; Upton, Julia; Grunebaum, Eyal; Chan, Edmond S; Baerg, Ingrid; Beaudette, Liane; Ke, Danbing; Mazer, Bruce; McCusker, Christine; Lejtenyi, Duncan; Ben-Shoshan, Moshe

Inborn errors of immunity (primary immunodeficiencies)

先天性免疫缺陷(原发性免疫缺陷)

Kim, Vy H D; Upton, Julia E M; Derfalvi, Beata; Hildebrand, Kyla J; McCusker, Christine

Clinical relevant Bruton's X-linked tyrosine kinase deficiency in a female with extreme X-chromosome inactivation

具有临床意义的布鲁顿氏X连锁酪氨酸激酶缺乏症,发生于一名患有极端X染色体失活的女性

NoorSaeed, Sundus M; Alrafiaah, Abdulaziz S; Alghamdi, Manar; Shapiro, Adam J; McCusker, Christine

Diagnostic Accuracy of Tryptase Levels for Pediatric Anaphylaxis: A Case-Control Study

类胰蛋白酶水平在儿童过敏反应诊断中的准确性:一项病例对照研究

Khalaf, Roy; Prosty, Connor; McCusker, Christine; Bretholz, Adam; Kaouache, Mohammed; Clarke, Ann E; Ben-Shoshan, Moshe

Symptomatology and Management of Adult Anaphylaxis according to Trigger: A Cross-Sectional Study

根据诱因划分的成人过敏反应的症状学和治疗:一项横断面研究

Khalaf, Roy; Prosty, Connor; McCusker, Christine; Bretholz, Adam; Kaouache, Mohammed; Clarke, Ann E; Morris, Judy; Lim, Rodrick; Chan, Edmond S; Goldman, Ran D; O'Keefe, Andrew; Gerdts, Jennifer; Chu, Derek K; Upton, Julia; Hochstadter, Elana; Moisan, Jocelyn; Zhang, Xun; Protudier, Jennifer L P; Abrams, Elissa; Simons, Elinor; Ruiz, Juan; Ben-Shoshan, Moshe

Comparing Two Peanut Desensitization Protocols in Preschool Children: A Real-World Clinical Practice

比较两种花生脱敏方案在学龄前儿童中的应用:一项真实世界的临床实践

Al Ali, Adnan; Sigman, Karen; Khalaf, Roy; Sillcox, Carly; Kaouache, Mohammed; Shand, Greg; Saker, Sarife; McCusker, Christine; Ben-Shoshan, Moshe

Comparing Two Oral Immunotherapy Strategies for Sesame Allergy: Baked Goods with Sesame Paste versus Crushed Sesame Seeds

比较两种治疗芝麻过敏的口服免疫疗法:芝麻酱烘焙食品与碎芝麻

Khalaf, Roy; Mulé, Pasquale; Kaouache, Mohammed; Sigman, Karen; McCusker, Christine; Saker, Sarife; Zhang, Xun; Ben-Shoshan, Moshe

Predicting Cow's Milk Challenge Outcomes in Children: Multivariate Analysis of Clinical Predictors.

预测儿童牛奶挑战试验结果:临床预测因素的多变量分析

Delli Colli Luca, Yu Joshua, Lanoue Derek, Mir Adhora, Cohen Casey G, Toscano-Rivero Diana, Sacksner Justin, Mazer Bruce, McCusker Christine, Ke Danbing, Laboccetta Vera, Lejtenyi Duncan, Beaudette Liane, Chan Edmond S, Baerg Ingrid, Upton Julia, Grunebaum Eyal, Bégin Philippe, Clarke Ann E, Jones Aaron, Ben-Shoshan Moshe