日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Perinatal death in pig models of hypertrophic cardiomyopathy carrying sarcomere pathogenic variants.

携带肌节致病变异的肥厚型心肌病猪模型出现围产期死亡

Flisikowska Tatiana, Petersen Björn, Mearini Giulia, Huber Daniela, Kurome Mayuko, Stoff Melanie, Schlossarek Saskia, Lucas-Hahn Andrea, Wolf Eckhard, Montag Judith, Schnieke Angelika, Carrier Lucie

Next-Generation Percutaneous Catheter-Based Closed-Loop Perfusion Concept Enables High-Precision Organ Delivery of Advanced Therapies

新一代经皮导管闭环灌注概念可实现先进疗法的高精度器官输送

Emmert, Maximilian Y; Holzmeister, Johannes; Blank, Ole; Meyborg, Heike; Jomard, Anne; Mearini, Giulia; Vono, Maria; Weisskopf, Miriam; Michalski, Marco; Nagaraju, Chandan Kadur; Dehdashtian, Mark; Hollamby, Dominic; Rusconi, Chris; Zelenkofske, Steven; Falk, Volkmar; Ayuso, Eduard; El Andari, Josef; Cesarovic, Nikola

Disease modeling of a mutation in α-actinin 2 guides clinical therapy in hypertrophic cardiomyopathy

α-辅肌动蛋白2基因突变的疾病模型指导肥厚型心肌病的临床治疗

Prondzynski, Maksymilian; Lemoine, Marc D; Zech, Antonia Tl; Horváth, András; Di Mauro, Vittoria; Koivumäki, Jussi T; Kresin, Nico; Busch, Josefine; Krause, Tobias; Krämer, Elisabeth; Schlossarek, Saskia; Spohn, Michael; Friedrich, Felix W; Münch, Julia; Laufer, Sandra D; Redwood, Charles; Volk, Alexander E; Hansen, Arne; Mearini, Giulia; Catalucci, Daniele; Meyer, Christian; Christ, Torsten; Patten, Monica; Eschenhagen, Thomas; Carrier, Lucie

Rescue of cardiomyopathy through U7snRNA-mediated exon skipping in Mybpc3-targeted knock-in mice

在Mybpc3靶向敲入小鼠中,U7snRNA介导的外显子跳跃可挽救心肌病

Gedicke-Hornung, Christina; Behrens-Gawlik, Verena; Reischmann, Silke; Geertz, Birgit; Stimpel, Doreen; Weinberger, Florian; Schlossarek, Saskia; Précigout, Guillaume; Braren, Ingke; Eschenhagen, Thomas; Mearini, Giulia; Lorain, Stéphanie; Voit, Thomas; Dreyfus, Patrick A; Garcia, Luis; Carrier, Lucie

BSE-associated prion-amyloid cardiomyopathy in primates

灵长类动物中与疯牛病相关的朊病毒淀粉样变性心肌病

Krasemann, Susanne; Mearini, Giulia; Krämer, Elisabeth; Wagenführ, Katja; Schulz-Schaeffer, Walter; Neumann, Melanie; Bodemer, Walter; Kaup, Franz-Josef; Beekes, Michael; Carrier, Lucie; Aguzzi, Adriano; Glatzel, Markus

Repair of Mybpc3 mRNA by 5'-trans-splicing in a Mouse Model of Hypertrophic Cardiomyopathy

在肥厚型心肌病小鼠模型中,Mybpc3 mRNA 通过 5' 反式剪接进行修复

Mearini, Giulia; Stimpel, Doreen; Krämer, Elisabeth; Geertz, Birgit; Braren, Ingke; Gedicke-Hornung, Christina; Précigout, Guillaume; Müller, Oliver J; Katus, Hugo A; Eschenhagen, Thomas; Voit, Thomas; Garcia, Luis; Lorain, Stéphanie; Carrier, Lucie

Atrogin-1 and MuRF1 regulate cardiac MyBP-C levels via different mechanisms

Atrogin-1 和 MuRF1 通过不同的机制调节心脏 MyBP-C 水平

Mearini, Giulia; Gedicke, Christina; Schlossarek, Saskia; Witt, Christian C; Krämer, Elisabeth; Cao, Peirang; Gomes, Marcelo D; Lecker, Stewart H; Labeit, Siegfried; Willis, Monte S; Eschenhagen, Thomas; Carrier, Lucie

Inhibition of Poly(ADP-ribose)polymerase impairs Epstein Barr Virus lytic cycle progression

抑制聚(ADP-核糖)聚合酶会损害EB病毒的裂解周期进程。

Mattiussi, Stefania; Tempera, Italo; Matusali, Giulia; Mearini, Giulia; Lenti, Luisa; Fratarcangeli, Silvia; Mosca, Luciana; D'Erme, Maria; Mattia, Elena

Localization and dynamics of small circular DNA in live mammalian nuclei

活体哺乳动物细胞核内小环状DNA的定位和动态变化

Mearini, Giulia; Nielsen, Peter E; Fackelmayer, Frank O