日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Erdheim-Chester disease associated with myeloid neoplasm: Clinical features, molecular landscape, and treatment outcomes

Erdheim-Chester病合并髓系肿瘤:临床特征、分子图谱和治疗结果

Le Pogam, Ambroise; Papo, Matthias; Hirsch, Pierre; Cohen-Aubart, Fleur; Emile, Jean-François; Delhommeau, François; Duffau, Pierre; Razanamahery, Jérôme; Nguyen-Khac, Florence; Nunes Gomes, Christopher; Triboulet, Felicien; de La Rochefoucauld, Jeanne; McAvoy, Chloé; Lazaro, Estibaliz; Hage-Sleiman, Mehdi; Roos-Weil, Damien; Chasset, François; Jachiet, Vincent; Mekinian, Arsène; Fain, Olivier; Amoura, Zahir; Hadjadj, Jérôme; Haroche, Julien

Lupuslike Manifestations in Myelodysplastic Syndromes and Chronic Myelomonocytic Leukemia

骨髓增生异常综合征和慢性粒单核细胞白血病中的狼疮样表现

Chauffier, Jeanne; Jachiet, Vincent; Battistella, Maxime; Romero, Pierre; Fenaux, Pierre; Zakine, Eve; Zhao, Lin Pierre; Mahévas, Thibault; Bouaziz, Jean-David; Hadjadj, Jerome; Amoura, Zahir; Mathian, Alexis; Breillat, Paul; Hirsch, Pierre; Bourguiba, Rim; De Voeght, Adrien; Grobost, Vincent; Begon, Edouard; Jandus, Peter; Brenaut, Emilie; Laumondais, Victoire; Fain, Olivier; Moguelet, Philippe; Mekinian, Arsene; Chasset, François

Comparative Efficacy and Safety of Anakinra and Canakinumab in Patients With VEXAS Syndrome: An International Multicenter Study

阿那白滞素和卡那单抗治疗VEXAS综合征患者的疗效和安全性比较:一项国际多中心研究

Eviatar, Tali; Capelusnik, Dafne; Campochiaro, Corrado; Lacombe, Valentin; Jachiet, Vincent; Zisapel, Michael; Sagy, Iftach; Tayer-Shifman, Oshrat E; Ozeri, David; Kivity, Shaye; Tomelleri, Alessandro; Terrier, Benjamin; Peleg, Hagit; Comont, Thibault; Sacre, Karim; Woaye-Hune, Pascal; Arnaud, Laurent; Lazaro, Estibaliz; Grobost, Vincent; Lifermann, Francois; Samson, Maxime; Ardois, Samuel; Garnier, Alice; Maria, Alexandre; Cantagrel, Alain; Meyer, Aurore; Bouaziz, Jean-David; Heiblig, Mael; Dagna, Lorenzo; Diral, Elisa; Kosmider, Olivier; Elkayam, Ori; Hadjadj, Jérôme; Georgin-Lavialle, Sophie; Fain, Olivier; Mekinian, Arsene

American College of Rheumatology Guidance Statement for Diagnosis and Management of VEXAS Developed by the International VEXAS Working Group Expert Panel

美国风湿病学会关于VEXAS诊断和治疗的指导声明,由国际VEXAS工作组专家组制定

Mekinian, Arsene; Georgin-Lavialle, Sophie; Ferrada, Marcela A; Savic, Sinisa; Koster, Matthew J; Kosmider, Olivier; Comont, Thibault; Heiblig, Mael; Arostegui, Juan I; Bosco, Annmarie; Bourguiba, Rim; Calvo, Katherine R; Cargo, Catherine; Cattaneo, Chiara; Chasset, François; Coelho, Henrique; Campochiaro, Corrado; Crisafulli, Francesca; Ducharme-Benard, Stephanie; Faria, Raquel; Franceschini, Franco; Frassi, Micol; Groarke, Emma M; Gurnari, Carmelo; Hakobyan, Yervand; Jamilloux, Yvan; Jurcut, Ciprian; Kirino, Yohei; Kulasekararaj, Austin; Kunimoto, Hiroyoshi; Madigan, Lauren M; Mann, Heřman F; Marvisi, Chiara; Milchert, Marcin; Morais, Sara; Sockel, Katja; Muratore, Francesco; Nakajima, Hideaki; Patnaik, Mrinal M; Regadas, Luísa; Robin, Marie; Rutgers, Abraham; Salvarani, Carlo; Sammel, Anthony M; Seebach, Joerg; Sujobert, Pierre; Tomelleri, Alessandro; Urbanski, Geoffrey; Vandergheynst, Frédéric; Vieira, Romana; Viswanatha, David S; Więsik-Szewczyk, Ewa; Diral, Elisa; Terrier, Benjamin; Patel, Bhavisha A; Fenaux, Pierre; Grayson, Peter C; Beck, David B

Exome sequencing enables molecular diagnosis in 10% of early-onset or familial systemic lupus erythematosus cases

外显子组测序可对 10% 的早发性或家族性系统性红斑狼疮病例进行分子诊断。

Tusseau, Maud; Khaldi-Plassart, Samira; Labalme, Audrey; Mathieu, Anne-Laure; Riller, Quentin; Molitor, Corentin; Simonet, Thomas; Viel, Sebastien; Gaboriaud, Christine; Thielens, Nicole; Heiser, Lionel; Chopin, Emilie; Rouvet, Isabelle; Fabien, Nicole; Goncalves, David; Fremeaux-Bacchi, Véronique; El-Sissy, Carine; Pottier, Nicolas; Larrue, Romain; Ranchin, Bruno; Laurent, Audrey; Fouillet-Desjonqueres, Marine; Jouret, Maurine; Mekinian, Arsène; Yamashita, Motoi; Morio, Tomohiro; Hachulla, Eric; Melki, Isabelle; Kone-Paut, Isabelle; Ballot, Claire; Reumaux, Heloise; Pillet, Pascal; Harambat, Jerome; Richez, Christophe; Richer, Olivier; Hatchuel, Yves; Louillet, Ferielle; Lega, Jean-Christophe; Durieu, Isabelle; Welfringer-Morin, Anne; Picard, Capucine; Messadi, Wassila; Sarrot-Reynauld, Françoise; Sanlaville, Damien; Bader-Meunier, Brigitte; Walzer, Thierry; Lesca, Gaëtan; Rieux-Laucat, Frédéric; Belot, Alexandre

Janus kinase and calcineurin-inhibitor combination in anti-MDA5 dermatomyositis: No significant survival benefit but reassuring safety profile

Janus激酶抑制剂和钙调磷酸酶抑制剂联合治疗抗MDA5皮肌炎:未见显著生存获益,但安全性良好

Pagis, Valentine; Astouati, Quentin; Pacoureau, Lucas; Nguyen, Yann; Bay, Pierre; Roux, Antoine; Gallay, Laure; Cottin, Vincent; Terrier, Benjamin; Meyer, Alain; Cerf, Charles; Neuville, Mathilde; Hervier, Baptiste; Renaud, Arthur; Suzon, Benoit; Schleinitz, Nicolas; Papo, Thomas; Priou, Pascaline; Mekinian, Arsène; Ullmer, Audrey; Oehler, Erwan; Gensous, Noémie; Berezne, Alice; Martin, Luc De Saint; Marhadour, Thierry; Martin, Mickaël; Servettaz, Amélie; Samson, Maxime; Gilardin, Laurent; Charles, Pierre; Woessner, Juliette; Carmoi, Thierry; Dilly, Baptiste; Mauhin, Wladimir; Baillet, Nicolas; Humbert, Sébastien; Thoreau, Benjamin; Lemaitre, Marine; Pendu, Claire Le; Loiseau, Pierre; Quemeneur, Thomas; Blanchard, Elodie; Voermans, Nicol; Launay, David; Nunes, Hilario; Benveniste, Olivier; Uzunhan, Yurdagul; Allenbach, Yves

Salvage therapy with JAK inhibitors in refractory Takayasu arteritis: a multicentre experience

JAK抑制剂在难治性大动脉炎挽救治疗中的应用:一项多中心经验

Mekinian, Arsène; Meneses, Sarah; Biard, Lucie; Dagna, Lorenzo; Novikov, Pavel; Salvarani, Carlo; Espitia, Olivier; Hernández-Rodríguez, José; Sacre, Karim; Lioger, Bertrand; Dufrost, Virginie; Audemard-Verger, Alexandra; Tomelleri, Alessandro; Kuwana, Masataka; Mukuchyan, Vahan; Dellal, Azeddine; Muratore, Francesco; Campochiaro, Corrado; Moiseev, Sergey; Cacoub, Patrice; Fain, Olivier; Saadoun, David

PAXIS: A Randomized, Double-Blind, Placebo-Controlled, Dose-Finding Phase 2 Study (Part 1) Followed by an Open-Label Period (Part 2) to Assess the Efficacy and Safety of Pacritinib in Patients with VEXAS Syndrome

PAXIS:一项随机、双盲、安慰剂对照、剂量探索性 II 期研究(第一部分)及后续开放标签期(第二部分),旨在评估帕克替尼治疗 VEXAS 综合征患者的疗效和安全性

Beck, David B; Heiblig, Maël; Savic, Sinisa; Ferrada, Marcela A; Mekinian, Arsène; Chowdhury, Onima; Hammond, Danielle; Weeks, Lachelle D; Gurnari, Carmelo; Kirino, Yohei; Georgin-Lavialle, Sophie; Buckley, Sarah A; Garcha, Raman; Harder, Bryan G; Koster, Matthew J

Association between parenthood and survival among 30,386 patients hospitalized with COVID-19

为人父母与新冠肺炎住院患者生存率之间的关联(30386例)

Audureau, Etienne; Jean, Charline; Layese, Richard; Neuraz, Antoine; Brasseur, Paul; Oubaya, Nadia; Polivka, Laura; Mekinian, Arsène; Hermine, Olivier; Rossignol, Julien

Efficacy of erythroid-stimulating agent and luspatercept in VEXAS syndrome: A multicenter retrospective study by the FRENVEX group

红细胞刺激剂和鲁斯帕西普治疗VEXAS综合征的疗效:FRENVEX研究组的一项多中心回顾性研究

Heiblig, Maël; Jachiet, Vincent; Hadjadj, Jérôme; Zhao, Lin Pierre; Comont, Thibault; Lobbes, Hervé; Lacombe, Valentin; Boutin, Anne Blandine; Galland, Joris; Terrier, Benjamin; Georgin-Lavialle, Sophie; Fenaux, Pierre; Mekinian, Arsène