Increased Alveolar Heparan Sulphate and Reduced Pulmonary Surfactant Amount and Function in the Mucopolysaccharidosis IIIA Mouse
粘多糖贮积症 IIIA 小鼠肺泡硫酸肝素增加,肺表面活性物质数量和功能减少
期刊:Cells
影响因子:5.1
doi:10.3390/cells10040849
Tamara L Paget, Emma J Parkinson-Lawrence, Paul J Trim, Chiara Autilio, Madhuriben H Panchal, Grielof Koster, Mercedes Echaide, Marten F Snel, Anthony D Postle, Janna L Morrison, Jésus Pérez-Gil, Sandra Orgeig