日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Correction: The chemical chaperone 4-phenylbutyric acid rescues molecular cell defects of COL3A1 mutations that cause vascular Ehlers Danlos Syndrome

更正:化学伴侣4-苯基丁酸可挽救COL3A1基因突变导致的血管型埃勒斯-当洛斯综合征的分子细胞缺陷。

Omar, Ramla; Lee, Michelle Aw; Gonzalez-Trueba, Laura; Thomson, Cameron R; Hansen, Uwe; Lianos, Spyridonas; Hazarika, Snoopy; El Abdallah, Omar Hmeh; Ammar, Malak A; Cassels, Jennifer; Michie, Alison M; Bulleid, Neil J; Malfait, Fransiska; Van Agtmael, Tom

The chemical chaperone 4-phenylbutyric acid rescues molecular cell defects of COL3A1 mutations that cause vascular Ehlers Danlos Syndrome.

化学伴侣 4-苯基丁酸可挽救导致血管型埃勒斯-当洛斯综合征的 COL3A1 突变的分子细胞缺陷

Omar Ramla, Lee Michelle Aw, Gonzalez-Trueba Laura, Thomson Cameron R, Hansen Uwe, Lianos Spyridonas, Hazarika Snoopy, El Abdallah Omar Hmeh, Ammar Malak A, Cassels Jennifer, Michie Alison M, Bulleid Neil J, Malfait Fransiska, Van Agtmael Tom

mTORC1-selective activation of translation elongation promotes disease progression in chronic lymphocytic leukemia

mTORC1选择性激活翻译延伸促进慢性淋巴细胞白血病的疾病进展

Malik, Natasha; Hay, Jodie; Almuhanna, Hassan N B; Dunn, Karen M; Lees, Jamie; Cassels, Jennifer; Li, Jiatian; Nakagawa, Rinako; Sansom, Owen J; Michie, Alison M

PKCβ Facilitates Leukemogenesis in Chronic Lymphocytic Leukaemia by Promoting Constitutive BCR-Mediated Signalling

PKCβ通过促进组成型BCR介导的信号传导来促进慢性淋巴细胞白血病中的白血病发生

Hay, Jodie; Tarafdar, Anuradha; Holroyd, Ailsa K; Moka, Hothri A; Dunn, Karen M; Alshayeb, Alzahra; Lloyd, Bryony H; Cassels, Jennifer; Malik, Natasha; Khan, Ashfia F; Sou, IengFong; Lees, Jamie; Almuhanna, Hassan N B; Kalakonda, Nagesh; Slupsky, Joseph R; Michie, Alison M

Evidence that hematopoietic stem cell function is preserved during aging in long-lived S6K1 mutant mice

证据表明,在长寿的S6K1突变小鼠中,造血干细胞功能在衰老过程中得以保留。

Selman, Colin; Sinclair, Amy; Pedroni, Silvia M A; Irvine, Elaine E; Michie, Alison M; Withers, Dominic J

Generation of a poor prognostic chronic lymphocytic leukemia-like disease model: PKCα subversion induces up-regulation of PKCβII expression in B lymphocytes

构建预后不良的慢性淋巴细胞白血病样疾病模型:PKCα抑制诱导B淋巴细胞中PKCβII表达上调

Nakagawa, Rinako; Vukovic, Milica; Tarafdar, Anuradha; Cosimo, Emilio; Dunn, Karen; McCaig, Alison M; Holroyd, Ailsa; McClanahan, Fabienne; Ramsay, Alan G; Gribben, John G; Michie, Alison M