日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Bile acids engage the SIPR-STAT3 signaling axis to modulate regulatory T cell responses in fibrosing cholangiopathies

胆汁酸通过激活SIPR-STAT3信号通路来调节纤维化胆管病中的调节性T细胞反应。

Kudira, Ramesh; Yang, Zi F; Osuji, Immaculeta; Damen, Michelle S M A; Yang Vom Hofe, Annika; Singh, Manavi; Karns, Rebekah; Bariya, Priya; Pfuhler, Liva; Mullen, Mary; Taylor, Amy; Ji, Hong; Lages, Celine S; Shi, Tiffany; Pasula, Srikar; Wayman, Joseph A; Bernieh, Anas; Zhang, Wujuan; Chougnet, Claire A; Hildeman, David A; Tiao, Gregory M; Huppert, Stacey S; Subramanian, Sanjay; Salomonis, Nathan; Miraldi, Emily R; Miethke, Alexander G

Interleukin 8-CXCR2-mediated neutrophil extracellular trap formation in biliary atresia associated with neutrophil extracellular trap-induced stellate cell activation

胆道闭锁中白细胞介素 8-CXCR2 介导的中性粒细胞胞外陷阱形成与中性粒细胞胞外陷阱诱导的星状细胞活化相关

Luo, Yuhuan; Fraser, Lisa; Jezykowski, Julia; Gupta, Nitika A; Miethke, Alexander G; Taylor, Sarah A; Alonso, Estella M; Horslen, Simon; Kohli, Rohit; Molleston, Jean P; Kamath, Binita M; Guthery, Stephen L; Loomes, Kathleen M; Magee, John C; Rosenthal, Phillip; Valentino, Pamela; Sokol, Ronald J; Mack, Cara L

A new multisystem ERCC1-hepatorenal syndrome: insights from a clinical cohort, molecular pathogenesis, and management guidelines

一种新的多系统ERCC1肝肾综合征:来自临床队列、分子发病机制和治疗指南的见解

White, Susan M; Wondergem, Annelotte P; Breet, Isa; Dittmaier, Maren; Bell, Katrina; Richmond, Christopher M; Hardikar, Winita; Bhatia, Kanika; Quinlan, Catherine; Orchard, David; D'Souza, Areetha; Chazin, Walter J; Smith, Christopher; Sparkes, Rebecca; Lam, Simon; Carter, Alexandra; Hopkin, Robert J; Khendek, Leticia; Sullivan, Bonnie R; Becher, Naja; Simonsen, Anne Katrine W; Kvistgaard, Helene; Dempsey, Katherine; Miethke, Alexander G; Gregersen, Pernille Axél; Phillips, Eliza; Luijsterburg, Martijn S

Advantages in orthopaedic implant infection diagnostics by additional analysis of explants

通过对取出植入物进行额外分析,在骨科植入物感染诊断中具有优势

Suda, Arnold J; Miethke, Thomas; Landua, Nadine; Obertacke, Udo

Prospective Multicenter Longitudinal Measurement of Liver Stiffness in School-Age Children With Cholestatic Liver Disease

前瞻性多中心纵向研究测量学龄期胆汁淤积性肝病患儿的肝脏硬度

Shneider, Benjamin L; Goodrich, Nathan P; Ye, Wen; Molleston, Jean P; Leung, Daniel H; Sokol, Ronald J; Cavallo, Laurel; Wang, Kasper; Valentino, Pamela L; Teckman, Jeffery H; Squires, James E; Sundaram, Shikha S; Rosenthal, Philip; Romero, Rene; Miethke, Alexander G; Loomes, Kathleen M; Kohli, Rohit; Karpen, Saul J; Kamath, Binita M; Jensen, M Kyle; Bezerra, Jorge A; Bass, Lee M; Magee, John C

Macrophages drive a fibrogenic gene program of periductal fibroblasts in pediatric primary sclerosing cholangitis

巨噬细胞驱动儿童原发性硬化性胆管炎中胆管周围成纤维细胞的纤维化基因程序

Wang, Yunguan; Adeleke, David; Xie, Xiangfei; Yang, Zi; von Hofe, Annika Yang; Singh, Manavi; Malik, Astha; Kudira, Ramesh; Castro-Rojas, Cyd; Pfuhler, Liva; Alquraish, Mosab; Sylvestre, Pamela; Dillman, Jonathan R; Trout, Andrew T; Miraldi, Emily; Miethke, Alexander G

Deleterious variants in TNFAIP3 are associated with type II and seronegative pediatric autoimmune hepatitis

TNFAIP3基因的有害变异与II型和血清阴性儿童自身免疫性肝炎相关

Pandurangi, Sindhu; Malik, Astha; Owens, Joshua; Valencia, C Alexander; Miethke, Alexander G

Association Between MR Elastography Liver Stiffness and Histologic Liver Fibrosis in Children and Young Adults With Autoimmune Liver Disease

磁共振弹性成像肝脏硬度与自身免疫性肝病患儿及青少年肝组织学纤维化之间的关联

Dillman, Jonathan R; Trout, Andrew T; Taylor, Amy E; Khendek, Leticia; Kasten, Jennifer L; Sheridan, Rachel M; Sharma, Divya; Karns, Rebekah A; Castro-Rojas, Cyd; Zhang, Bin; Miethke, Alexander G

DNAJB1-PKAc Kinase Is Expressed in Young Patients with Pediatric Liver Cancers and Enhances Carcinogenic Pathways

DNAJB1-PKAc 激酶在儿童肝癌患者中表达并增强致癌途径

Yasmeen Fleifil, Ruhi Gulati, Katherine Jennings, Alexander Miethke, Alexander Bondoc, Gregory Tiao, James I Geller, Rebekah Karns, Lubov Timchenko, Nikolai Timchenko

Case Report: Childhood Erythrocytosis due to Hypermanganesemia Caused by Homozygous SLC30A10 Mutation

病例报告:由纯合SLC30A10突变引起的锰血症导致的儿童红细胞增多症

Coppola, Tiziana; Hughes, Hannah; Finch, Paul; Hess, Joshua; Wu, Steve; Prada, Carlos; Miethke, Alexander G; Zhang, Wenying; Kalfa, Theodosia A