日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

CFTR activity in nasal potential difference of adults with idiopathic bronchiectasis

特发性支气管扩张成人患者鼻腔电位差中CFTR活性

Tümmler, Burkhard; Schulz, Angela; Minso, Rebecca; Alfeis, Nadine; Tamm, Stephanie; Rademacher, Jessica; Ringshausen, Felix C

Genotype and transcript processing of the tumour necrosis factor receptor TNFRSF1A in epithelial cells: implications for survival in cystic fibrosis.

肿瘤坏死因子受体 TNFRSF1A 在上皮细胞中的基因型和转录加工:对囊性纤维化患者生存的影响

Uden Alexander, Dunsche Inga, Janciauskiene Sabina, Gräber Simon, Feng Longhua, Tamm Stephanie, Hedtfeld Silke, Stege Gesa, Jahn Kirsten, Kontsendorn Julia, Alfeis Nadine, Kühbandner Iris, Minso Rebecca, Dopfer Christian, Griese Matthias, Sommerburg Olaf, Ringshausen Felix C, Nährlich Lutz, Hansen Gesine, Welte Tobias, Braubach Peter, Mall Marcus A, Tümmler Burkhard, Dittrich Anna-Maria, Stanke Frauke

Differential effects of ELX/TEZ/IVA on organ-specific CFTR function in two patients with the rare CFTR splice mutations c.273+1G>A and c.165-2A>G

ELX/TEZ/IVA 对两名携带罕见 CFTR 剪接突变 c.273+1G>A 和 c.165-2A>G 的患者器官特异性 CFTR 功能的不同影响

Pallenberg, Sophia T; Held, Inka; Dopfer, Christian; Minso, Rebecca; Nietert, Manuel M; Hansen, Gesine; Tümmler, Burkhard; Dittrich, Anna-Maria

Spirometric and anthropometric improvements in response to elexacaftor/tezacaftor/ivacaftor depending on age and lung disease severity

根据年龄和肺部疾病严重程度,服用依来卡福托/替扎卡福托/伊伐卡福托后,肺功能和人体测量指标的改善情况可能有所不同。

Schütz, Katharina; Pallenberg, Sophia Theres; Kontsendorn, Julia; DeLuca, David; Sukdolak, Cinja; Minso, Rebecca; Büttner, Tina; Wetzke, Martin; Dopfer, Christian; Sauer-Heilborn, Annette; Ringshausen, Felix C; Junge, Sibylle; Tümmler, Burkhard; Hansen, Gesine; Dittrich, Anna-Maria

The Cystic Fibrosis Upper and Lower Airway Metagenome

囊性纤维化上呼吸道和下呼吸道宏基因组

Pienkowska, Katarzyna; Pust, Marie-Madlen; Gessner, Margaux; Gaedcke, Svenja; Thavarasa, Ajith; Rosenboom, Ilona; Morán Losada, Patricia; Minso, Rebecca; Arnold, Christin; Hedtfeld, Silke; Dorda, Marie; Wiehlmann, Lutz; Mainz, Jochen G; Klockgether, Jens; Tümmler, Burkhard

Multicentre feasibility of multiple-breath washout in preschool children with cystic fibrosis and other lung diseases

多中心研究多呼吸冲洗法在患有囊性纤维化和其他肺部疾病的学龄前儿童中的可行性

Stahl, Mirjam; Joachim, Cornelia; Kirsch, Ines; Uselmann, Tatjana; Yu, Yin; Alfeis, Nadine; Berger, Christiane; Minso, Rebecca; Rudolf, Isa; Stolpe, Cornelia; Bovermann, Xenia; Liboschik, Lena; Steinmetz, Alena; Tennhardt, Dunja; Dörfler, Friederike; Röhmel, Jobst; Unorji-Frank, Klaudia; Rückes-Nilges, Claudia; von Stoutz, Bianca; Naehrlich, Lutz; Kopp, Matthias V; Dittrich, Anna-Maria; Sommerburg, Olaf; Mall, Marcus A

Intestinal current measurement and nasal potential difference to make a diagnosis of cases with inconclusive CFTR genetics and sweat test

肠道电流测量和鼻腔电位差可用于诊断CFTR基因检测和汗液试验结果不明确的病例。

Minso, Rebecca; Schulz, Angela; Dopfer, Christian; Alfeis, Nadine; Barneveld, Andrea van; Makartian-Gyulumyan, Lena; Hansen, Gesine; Junge, Sibylle; Müller, Carsten; Ringshausen, Felix C C; Sauer-Heilborn, Annette; Stanke, Frauke; Stolpe, Cornelia; Tamm, Stephanie; Welte, Tobias; Dittrich, Anna-Maria; Tümmler, Burkhard