日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Taperin bundles F-actin at stereocilia pivot points enabling optimal lifelong mechanosensitivity.

Taperin 将 F-肌动蛋白束固定在立体纤毛的枢轴点,从而实现最佳的终生机械敏感性

Belyantseva Inna A, Liu Chang, Dragich Abigail K, Miyoshi Takushi, Inagaki Sayaka, Imtiaz Ayesha, Tona Risa, Zuluaga-Osorio Karen Sofia, Hadi Shadan, Wilson Elizabeth, Morozko Eva, Olszewski Rafal, Yousaf Rizwan, Sokolova Yuliya, Riordan Gavin P, Aston S Andrew, Rehman Atteeq U, Fenollar Ferrer Cristina, Wisniewski Jan, Gu Shoujun, Nayak Gowri, Goodyear Richard J, Li Jinan, Krey Jocelyn F, Wafa Talah, Faridi Rabia, Adadey Samuel Mawuli, Drummond Meghan, Perrin Benjamin, Winkler Dennis C, Starost Matthew F, Cheng Hui, Fitzgerald Tracy, Richardson Guy P, Dong Lijin, Barr-Gillespie Peter G, Hoa Michael, Frolenkov Gregory I, Friedman Thomas B, Zhao Bo

Pathophysiology of human hearing loss associated with variants in myosins

肌球蛋白变异相关的人类听力损失的病理生理学

Miyoshi, Takushi; Belyantseva, Inna A; Sajeevadathan, Mrudhula; Friedman, Thomas B

Human deafness-associated variants alter the dynamics of key molecules in hair cell stereocilia F-actin cores

人类耳聋相关变异会改变毛细胞立体纤毛F-肌动蛋白核心中关键分子的动力学

Miyoshi, Takushi; Belyantseva, Inna A; Kitajiri, Shin-Ichiro; Miyajima, Hiroki; Nishio, Shin-Ya; Usami, Shin-Ichi; Kim, Bong Jik; Choi, Byung Yoon; Omori, Koichi; Shroff, Hari; Friedman, Thomas B

Late-onset hearing loss case associated with a heterozygous truncating variant of DIAPH1

与DIAPH1基因杂合截断变异相关的迟发性听力损失病例

Kim, Bong Jik; Miyoshi, Takushi; Chaudhry, Taimur; Friedman, Thomas B; Choi, Byung Yoon; Ueyama, Takehiko

Quantitative Analysis of Aquaporin Expression Levels during the Development and Maturation of the Inner Ear

内耳发育成熟过程中水通道蛋白表达水平的定量分析

Miyoshi, Takushi; Yamaguchi, Taro; Ogita, Kiyokazu; Tanaka, Yasuko; Ishibashi, Ken-Ichi; Ito, Hiroaki; Kobayashi, Taisuke; Nakagawa, Takayuki; Ito, Juichi; Omori, Koichi; Yamamoto, Norio

Therapeutic potential of a gamma-secretase inhibitor for hearing restoration in a guinea pig model with noise-induced hearing loss

γ-分泌酶抑制剂在噪声性听力损失豚鼠模型中恢复听力的治疗潜力

Tona, Yosuke; Hamaguchi, Kiyomi; Ishikawa, Masaaki; Miyoshi, Takushi; Yamamoto, Norio; Yamahara, Kohei; Ito, Juichi; Nakagawa, Takayuki