日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Transcriptomic Analysis Reveals the Beneficial Effects of Spermidine in an ALS Mouse Model

转录组分析揭示亚精胺在ALS小鼠模型中的有益作用

Tang, Maoxue; Teng, Sasa; Peng, Yueqing; Kim, Ashley Y; Her, Yoon-Ra; Canoll, Peter; Bruce, Jeffrey N; Faust, Phyllis L; Adhikari, Kailash; De Vivo, Darryl C; Monani, Umrao R; Akman, Nur; Kömüroğlu, Ahmet Ufuk; Çibuk, Salih; Altındağ, Fikret; Yılmaz, Osman; Ateşşahin, Ahmet; Fiorucci, Cristian; Rossi, Marianna Nicoletta; Santo, Rachele Di; Salvatori, Illari; Scaricamazza, Silvia; Giuliani, Stefano; Carletta, Olga; Filomena, Ermes; Laurenti, Davide; Mattioli, Roberto; Mosca, Luciana; Valle, Cristiana; Ferri, Alberto; D’Erchia, Anna Maria; Cervelli, Manuela

Protein-stabilizing and neurotransmission-potentiating activities of a synaptic chaperone modify spinal muscular atrophy in model mice

突触伴侣蛋白的蛋白质稳定和神经递质增强活性可改善模型小鼠的脊髓性肌萎缩症。

Her, Yoon-Ra; Fuentes-Moliz, Andrea; Kothary, Rashmi; Tabares, Lucia; Monani, Umrao R

Transgenic expression of the human Glucose Transporter1 (GLUT1) gene locus reduces disease burden in Glut1 deficiency syndrome model mice

转基因表达人葡萄糖转运蛋白1 (GLUT1) 基因位点可减轻GLUT1缺乏症模型小鼠的疾病负担。

Tang, Maoxue; Teng, Sasa; Kim, Ashley Y; Peng, Yueqing; Monani, Umrao R

A variant of the Hspa8 synaptic chaperone modifies disease in a SOD1(G86R) mouse model of amyotrophic lateral sclerosis.

Hspa8 突触伴侣蛋白的一个变体可以改变 SOD1(G86R) 小鼠肌萎缩侧索硬化症模型中的疾病

Takeda Taishi, Her Yoon-Ra, Kim Jeong-Ki, Jha Narendra N, Monani Umrao R

NODG-01 EVALUATING THE CURRENT NEURO-ONCOLOGY CAPACITY IN SUB-SAHARAN AFRICA: A QUESTIONNAIRE-BASED SURVEY

NODG-01 评估撒哈拉以南非洲当前神经肿瘤学能力:一项基于问卷调查的研究

Tang, Maoxue; Teng, Sasa; Peng, Yueqing; Kim, Ashley Y; Canoll, Peter; Bruce, Jeffrey N; Faust, Phyllis L; Adhikari, Kailash; De Vivo, Darryl C; Monani, Umrao R; Kim, Yeshin; Jang, Hyemin; Jang, Jae‐Won; Moon, So Young; Kim, Eun‐Joo; Karim, Helmet T; Son, Sang Joon; Zerd, Francis; Odukoya, Lateef A; Cheserem, Beverly; Darko, Kwado; Ghomsi, Nathalie; Llewellyn, Henry; Eckel-Passow, Jeanette; Jenkins, Robert; Kamson, David; Fonkem, Ekokobe; Schroeder, Kristin

A transgene harboring the human Glucose Transporter1 (GLUT1) gene locus ameliorates disease in GLUT1 deficiency syndrome model mice

携带人葡萄糖转运蛋白1 (GLUT1) 基因位点的转基因小鼠可改善GLUT1缺乏症模型小鼠的疾病症状。

Tang, Maoxue; Teng, Sasa; Kim, Ashley Y; Peng, Yueqing; Monani, Umrao R

Muscle: an independent contributor to the neuromuscular spinal muscular atrophy disease phenotype

肌肉:脊髓性肌萎缩症神经肌肉疾病表型的一个独立贡献因素

Jha, Narendra N; Kim, Jeong-Ki; Her, Yoon-Ra; Monani, Umrao R

Emerging concepts underlying selective neuromuscular dysfunction in infantile-onset spinal muscular atrophy

婴儿期发病脊髓性肌萎缩症选择性神经肌肉功能障碍的新兴概念

Gollapalli, Kishore; Kim, Jeong-Ki; Monani, Umrao R

An early endothelial cell-specific requirement for Glut1 is revealed in Glut1 deficiency syndrome model mice

在 Glut1 缺乏综合征模型小鼠中揭示了内皮细胞对 Glut1 的早期特异性需求。

Tang, Maoxue; Park, Sarah H; Petri, Sabrina; Yu, Hang; Rueda, Carlos B; Abel, E Dale; Kim, Carla Y; Hillman, Elizabeth Mc; Li, Fanghua; Lee, Yeojin; Ding, Lei; Jagadish, Smitha; Frankel, Wayne N; De Vivo, Darryl C; Monani, Umrao R

Diminished muscle oxygen uptake and fatigue in spinal muscular atrophy

脊髓性肌萎缩症患者的肌肉氧气摄取减少和疲劳

Montes, Jacqueline; Goodwin, Ashley M; McDermott, Michael P; Uher, David; Hernandez, Feliz Marie; Coutts, Kayla; Cocchi, Julia; Hauschildt, Margarethe; Cornett, Kayla M; Rao, Ashwini K; Monani, Umrao R; Ewing Garber, Carol; De Vivo, Darryl C