Deleterious effect of Pseudomonas aeruginosa on F508del-CFTR rescued by elexacaftor/tezacaftor/ivacaftor is clinical strain-dependent in patient-derived nasal cells
铜绿假单胞菌对F508del-CFTR的有害影响(可通过elexacaftor/tezacaftor/ivacaftor挽救)在患者鼻细胞中具有临床菌株依赖性。
期刊:Erj Open Research
影响因子:4
doi:10.1183/23120541.00970-2024
Allegretta, Caterina; Montemitro, Enza; Sgobba, Maria Noemi; Capurro, Valeria; Pesce, Emanuela; Ciciriello, Fabiana; La Bella, Gianfranco; Rossito, Martina; Tuccio, Vanessa; Arena, Fabio; Gunawardena, Tarini N A; Guerra, Lorenzo; Pedemonte, Nicoletta; Capitanio, Nazzareno; Piccoli, Claudia; Laselva, Onofrio