日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Long-term efficacy and safety of cardiac genome editing for catecholaminergic polymorphic ventricular tachycardia

心脏基因组编辑治疗儿茶酚胺敏感性多形性室性心动过速的长期疗效和安全性

Moore, Oliver M; Aguilar-Sanchez, Yuriana; Lahiri, Satadru K; Hulsurkar, Mohit M; Alberto Navarro-Garcia, J; Word, Tarah A; Keefe, Joshua A; Barazi, Dean; Munivez, Elda M; Moore, Charles T; Parthasarathy, Vaidya; Davidson, Jaysón; Lagor, William R; Park, So Hyun; Bao, Gang; Miyake, Christina Y; Wehrens, Xander H T

Targeting calpain-2-mediated junctophilin-2 cleavage delays heart failure progression following myocardial infarction

靶向钙蛋白酶-2介导的连接蛋白-2裂解可延缓心肌梗死后心力衰竭的进展

Lahiri, Satadru K; Lu, Jiao; Aguilar-Sanchez, Yuriana; Li, Hui; Moreira, Lucia M; Hulsurkar, Mohit M; Mendoza, Arielys; Turkieltaub Paredes, Mara R; Navarro-Garcia, Jose Alberto; Munivez, Elda; Horist, Brooke; Moore, Oliver M; Weninger, Gunnar; Brandenburg, Sören; Lenz, Christof; Lehnart, Stephan E; Sayeed, Rana; Krasopoulos, George; Srivastava, Vivek; Zhang, Lilei; Karch, Jason M; Reilly, Svetlana; Wehrens, Xander H T

Correlations Between Bone Mechanical Properties and Bone Composition Parameters in Mouse Models of Dominant and Recessive Osteogenesis Imperfecta and the Response to Anti-TGF-β Treatment

显性和隐性成骨不全小鼠模型中骨力学特性与骨成分参数的相关性及对抗TGF-β治疗的反应

Bi, Xiaohong; Grafe, Ingo; Ding, Hao; Flores, Rene; Munivez, Elda; Jiang, Ming Ming; Dawson, Brian; Lee, Brendan; Ambrose, Catherine G

Restoration of the serum level of SERPINF1 does not correct the bone phenotype in Serpinf1 null mice

恢复血清中SERPINF1的水平并不能纠正Serpinf1基因敲除小鼠的骨骼表型。

Rajagopal, Abbhirami; Homan, Erica P; Joeng, Kyu Sang; Suzuki, Masataka; Bertin, Terry; Cela, Racel; Munivez, Elda; Dawson, Brian; Jiang, Ming-Ming; Gannon, Frank; Crawford, Susan; Lee, Brendan H

A transgenic mouse model of OI type V supports a neomorphic mechanism of the IFITM5 mutation

V型成骨不全症转基因小鼠模型支持IFITM5突变的新功能机制

Lietman, Caressa D; Marom, Ronit; Munivez, Elda; Bertin, Terry K; Jiang, Ming-Ming; Chen, Yuqing; Dawson, Brian; Weis, Mary Ann; Eyre, David; Lee, Brendan

Losartan increases bone mass and accelerates chondrocyte hypertrophy in developing skeleton.

氯沙坦可增加骨量并加速发育中骨骼的软骨细胞肥大

Chen Shan, Grover Monica, Sibai Tarek, Black Jennifer, Rianon Nahid, Rajagopal Abbhirami, Munivez Elda, Bertin Terry, Dawson Brian, Chen Yuqing, Jiang Ming-Ming, Lee Brendan, Yang Tao, Bae Yangjin

miRNA-34c regulates Notch signaling during bone development

miRNA-34c在骨骼发育过程中调控Notch信号通路

Bae, Yangjin; Yang, Tao; Zeng, Huan-Chang; Campeau, Philippe M; Chen, Yuqing; Bertin, Terry; Dawson, Brian C; Munivez, Elda; Tao, Jianning; Lee, Brendan H

Interaction of TGFβ and BMP signaling pathways during chondrogenesis.

软骨形成过程中TGFβ和BMP信号通路的相互作用

Keller Bettina, Yang Tao, Chen Yuqing, Munivez Elda, Bertin Terry, Zabel Bernhard, Lee Brendan

Brachy-syndactyly caused by loss of Sfrp2 function

由 Sfrp2 功能丧失引起的短指并指

Morello, Roy; Bertin, Terry K; Schlaubitz, Silke; Shaw, Chad A; Kakuru, Sujatha; Munivez, Elda; Hermanns, Pia; Chen, Yuqing; Zabel, Bernhard; Lee, Brendan

Uncoupling of chondrocyte differentiation and perichondrial mineralization underlies the skeletal dysplasia in tricho-rhino-phalangeal syndrome

软骨细胞分化与软骨膜矿化脱钩是毛发-鼻-指骨综合征骨骼发育不良的根本原因。

Napierala, Dobrawa; Sam, Kathy; Morello, Roy; Zheng, Qiping; Munivez, Elda; Shivdasani, Ramesh A; Lee, Brendan