日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Condition-Specific Growth Charts for Children With Alagille Syndrome

阿拉吉尔综合征患儿的特定生长曲线图

Huysentruyt, Koen; Vandriel, Shannon M; Roelants, Mathieu; Piccoli, David A; Loomes, Kathleen M; Rand, Elizabeth B; Ebel, Noelle H; Feinstein, Jeffrey A; Jankowska, Irena; Czubkowski, Piotr; Gliwicz-Miedzinska, Dorota; Gonzales, Emmanuel M; Jacquemin, Emmanuel; Bouligand, Jérôme; Karpen, Saul J; Romero, Rene; Lin, Henry C; Fischler, Björn; Arnell, Henrik; Li, Li-Ting; Wang, Jian-She; Fawaz, Rima; Nastasio, Silvia; Kim, Kyung Mo; Oh, Seak Hee; D'Antiga, Lorenzo; Nicastro, Emanuele; Fischer, Ryan T; Siew, Susan M; Stormon, Michael; Lertudomphonwanit, Chatmanee; Hardikar, Winita; Shankar, Sahana; Squires, James E; Sundaram, Shikha S; Larson-Nath, Catherine; Kelly, Deirdre A; Hartley, Jane; Bulut, Pinar; Jensen, M Kyle; Jaramillo, Catalina; Roberts, Amin J; Evans, Helen M; Sokal, Étienne M; Demaret, Tanguy; Verkade, Henkjan J; Thompson, Richard J; Hansen, Bettina E; Cole, Tim J; Kamath, Binita M; Debray, Dominique; Lacaille, Florence; Brecelj, Jernej; El-Koofy, Nehal M; Elmonem, Mohamed A; Lee, Way Seah; Sanchez, Maria Camila; Cavalieri, Maria Lorena; Hajinicolaou, Christina; Schwarz, Kathleen B; Carvalho, Elisa; Rock, Nathalie; Karnsakul, Wikrom; Quiros-Tejeira, Ruben E; Alam, Seema; Nebbia, Gabriella; Mozer-Glassberg, Yael; Valentino, Pamela L; Santos-Silva, Ermelinda; Önal, Zerrin; Dezsofi-Gottl, Antal; Melere, Melina; Legarda Tamara, María; Eshun, John; Zellos, Aglaia; Indolfi, Giuseppe; Rogalidou, Maria; Blondet, Niviann; Luigi Calvo, Pier; Beretta, Marisa; Zizzo, Andréanne N; Arikan, Cigdem; Kasahara, Mureo; Kerkar, Nanda; Aqul, Amal A; Wolters, Victorien M; Borges Pinto, Raquel; Quintero Bernabeu, Jesus; Garcia, Jennifer; Wiecek, Sabina; Tzivinikos, Christos; Mujawar, Quais; Jimenez-Rivera, Carolina; Molera Busoms, Cristina; Gonçalves, Cristina; Bujanda, Luis

Neonatal acute liver failure cases with echovirus 11 infections, Japan, August to November 2024

日本2024年8月至11月新生儿急性肝衰竭病例(伴有埃可病毒11型感染)

Ikuse, Tatsuki; Matsui, Toshihiro; Shoji, Kensuke; Kono, Naoko; Yamada, Masaki; Ogimi, Chikara; Takahashi, Chika; Funaki, Takanori; Ide, Kentaro; Matsumoto, Shotaro; Ito, Reiko; Shimabukuro, Rinshu; Gocho, Yoshihiro; Hayakawa, Itaru; Ishikawa, Takashi; Sakamoto, Seisuke; Kasahara, Mureo; Igarashi, Takashi

Phenotypic Divergence of JAG1- and NOTCH2-Associated Alagille Syndrome & Disease-Specific NOTCH2 Variant Classification Guidelines

JAG1 和 NOTCH2 相关阿拉吉尔综合征的表型差异及疾病特异性 NOTCH2 变异分类指南

Vandriel, Shannon M; Li, Li-Ting; She, Huiyu; Wang, Jian-She; Loomes, Kathleen M; Piccoli, David A; Jankowska, Irena; Czubkowski, Piotr; Gliwicz-Miedzińska, Dorota; D'Antiga, Lorenzo; Nicastro, Emanuele; Lacaille, Florence; Debray, Dominique; Sokal, Étienne M; Demaret, Tanguy; Fawaz, Rima L; Nastasio, Silvia; Kim, Kyung Mo; Oh, Seak Hee; Fischler, Björn; Arnell, Henrik; Larson-Nath, Catherine; Hardikar, Winita; Shankar, Sahana; Sundaram, Shikha S; Chaidez, Alexander; Bulut, Pinar; Calvo, Pier Luigi; Kasahara, Mureo; Blondet, Niviann; Lurz, Eberhard; Kavallar, Anna-Maria; Gonzales, Emmanuel M; Jacquemin, Emmanuel; Bouligand, Jérôme; Ebel, Noelle H; Feinstein, Jeffrey A; Siew, Susan M; Stormon, Michael O; Karpen, Saul J; Romero, Rene; Jensen, M Kyle; Jaramillo, Catalina; Squires, James E; Bedoyan, Sarah M; Kelly, Deirdre A; Hartley, Jane; Verkade, Henkjan J; Lee, Way Seah; Lertudomphonwanit, Chatmanee; Fischer, Ryan T; Lin, Henry C; Rock, Nathalie; Mozer-Glassberg, Yael; Roberts, Amin J; Evans, Helen M; Karnsakul, Wikrom; Nebbia, Gabriella; Wolters, Victorien M; Valentino, Pamela L; Bernabeu, Jesus Quintero; Aqul, Amal A; Arikan, Cigdem; Tamara, María Legarda; Busoms, Cristina Molera; Sandahl, Thomas Damgaard; Indolfi, Giuseppe; Zizzo, Andréanne N; Zellos, Aglaia; Quiros-Tejeira, Ruben E; Santos-Silva, Ermelinda; Schwarz, Kathleen B; Brecelj, Jernej; Sanchez, Maria Camila; Cavalieri, Maria Lorena; Tzivinikos, Christos; Wiecek, Sabina; Eshun, John; Kerkar, Nanda; Mujawar, Quais; Önal, Zerrin; Gonçalves, Cristina; Garcia, Jennifer; Alam, Seema; Jimenez-Rivera, Carolina; Bujanda, Luis; Thompson, Richard J; Hansen, Bettina E; Spinner, Nancy B; Gilbert, Melissa A; Kamath, Binita M

Elevated Serum Bile Acids Predict Poor Liver Outcomes in Children With Alagille Syndrome: Results From the GALA Study Group

血清胆汁酸水平升高预示阿拉吉勒综合征患儿肝脏预后不良:GALA研究组的结果

Perez, Carla Fiorella Murillo; Vandriel, Shannon M; Gonzales, Emmanuel M; Wang, Jian-She; Li, Li-Ting; She, Huiyu; Jankowska, Irena; Czubkowski, Piotr; Gliwicz-Miedzińska, Dorota; Jacquemin, Emmanuel; Bouligand, Jérôme; D'Antiga, Lorenzo; Nicastro, Emanuele; Fischler, Björn; Arnell, Henrik; Siew, Susan M; Stormon, Michael; Loomes, Kathleen M; Piccoli, David A; Rand, Elizabeth B; Squires, James E; Karpen, Saul J; Romero, Rene; Kasahara, Mureo; Önal, Zerrin; Sokal, Étienne; Demaret, Tanguy; Wiecek, Sabina; Lacaille, Florence; Debray, Dominique; Hardikar, Winita; Shankar, Sahana; Valentino, Pamela L; Sundaram, Shikha S; Ebel, Noelle H; Feinstein, Jeffrey A; Waisbourd-Zinman, Orith; Lin, Henry C; Rock, Nathalie; Verkade, Henkjan J; Jensen, M Kyle; Jaramillo, Catalina; Kim, Kyung Mo; Oh, Seak Hee; Brecemiclj, Jernej; Alam, Seema; Indolfi, Giuseppe; Blondet, Niviann; Fawaz, Rima; Nastasio, Silvia; Calvo, Pier Luigi; Nebbia, Gabriella; Arikan, Cigdem; Larson-Nath, Catherine; Zizzo, Andréanne N; Sandahl, Thomas Damgaard; Tzivinikos, Christos; El-Koofy, Nehal M; Elmonem, Mohamed A; Aqul, Amal A; Karnsakul, Wikrom; Bulut, Pinar; Kerkar, Nanda; Wolters, Victorien M; Roberts, Amin J; Evans, Helen M; Sanchez, Maria Camila; Cavalieri, Maria Lorena; Kelly, Deirdre A; Hartley, Jane; Lee, Way Seah; Hajinicolaou, Christina; Lertudomphonwanit, Chatmanee; Fischer, Ryan T; Bernabeu, Jesus Quintero; Quiros-Tejeira, Ruben E; Ferreira, Cristina Targa; Carvalho, Elisa; Eshun, John; Zellos, Aglaia; Dezsőfi, Antal; Pinto, Raquel Borges; Schwarz, Kathleen; Rogalidou, Maria; Garcia, Jennifer; Tamara, María Legarda; Beretta, Marisa; Mujawar, Quais; Santos-Silva, Ermelinda; Busoms, Cristina Molera; Lurz, Eberhard; Gonçalves, Cristina; Jimenez-Rivera, Carolina; Banales, Jesus M; Thompson, Richard J; Hansen, Bettina E; Kamath, Binita M

Intrauterine high-dose intravenous immunoglobulin therapy during pregnancy for women with a history of pregnancy ending in documented neonatal haemochromatosis (NH001): study protocol

对既往有新生儿血色素沉着症妊娠史的女性进行妊娠期宫内高剂量静脉注射免疫球蛋白治疗(NH001):研究方案

Sasaki, Aiko; Yachie, Akihiro; Mizuta, Koichi; Takahashi, Hironori; Okada, Noriki; Toma, Tomoko; Motomura, Kenichiro; Matsumoto, Kenji; Wada, Yuka Sano; Ito, Yushi; Ito, Reiko; Kasahara, Mureo; Fukuda, Akinari; Inoue, Eisuke; Yamaguchi, Koshi; Nakamura, Hidefumi; Wada, Seiji; Sako, Mayumi

Portal Vein Obstruction in Pediatric Liver Transplant Patients: An Evaluation of Self-Reported Management Practices

儿童肝移植患者门静脉阻塞:自我报告管理实践的评估

Sieben, Lydia; Alfares, Bader A; de Kleine, Ruben H; Wildhaber, Barbara E; Casswall, Thomas; Nowak, Greg; Delle, Martin; Aldrian, Denise; Berchtold, Valeria; Vogel, Georg F; Kaliciński, Piotr; Markiewicz-Kijewska, Malgorzata; Kolesnik, Adam; Quintero, Jesús; Hally, María Mercadal; King, Mauricio Larrarte; Marra, Paolo; Bravi, Michela; Pinelli, Domenico; Kasahara, Mureo; Sakamoto, Seisuke; Uchida, Hajime; Mali, Vidyadhar; Aw, Marion; Franchi-Abella, Stéphanie; Gonzales, Emmanuel; Guérin, Florent; Cervio, Guillermo; Minetto, Julia; Sierre, Sergio; de Santibañes, Martín; Ardiles, Victoria; Uño, Jimmy Walker; Evans, Helen; Duncan, David; McCall, John; Hartleif, Steffen; Sturm, Ekkehard; Patel, Jai V; Mtegha, Marumbo; Prasad, Raj; Ferreira, Cristina T; Nader, Luiza S; Farina, Marco; Jaramillo, Catalina; Rodriguez-Davalos, Manuel I; Feola, Peter; Shah, Amit A; Wood, Phoebe M; Acord, Michael R; Fischer, Ryan T; Mullapudi, Bhargava; Hendrickson, Richard J; Khanna, Rajeev; Pamecha, Viniyendra; Mukund, Amar; Sharif, Khalid; Gupte, Girish; McGuirk, Simon; Porta, Gilda; Hardikar, Winita; Spada, Marco; Alterio, Tommaso; Maggiore, Giuseppe; Beretta, Marisa; Dierckx, Rudi A J; Bokkers, Reinoud P H; van der Doef, Hubert P J

Assessing Native Liver Post-Kasai Portoenterostomy for Biliary Atresia Through Stool Proteome Analysis

通过粪便蛋白质组分析评估胆道闭锁行葛西氏肝门空肠吻合术后自体肝脏功能

Watanabe, Eiichiro; Saito, Takeshi; Yoshihara, Masahito; Konno, Ryo; Fujishiro, Jun; Takazawa, Shinya; Ichinose, Akinori; Miyake, Kazue; Kakihara, Tomo; Ishimaru, Tetsuya; Nishi, Akira; Fukuda, Akinari; Kasahara, Mureo; Ohara, Osamu; Kawashima, Yusuke

Japanese living donor liver transplantation criteria for hepatocellular carcinoma: nationwide cohort study

日本活体肝移植治疗肝细胞癌的标准:全国队列研究

Ohira, Masahiro; Aoki, Gaku; Orihashi, Yasushi; Yoshimura, Kenichi; Toshima, Takeo; Hatano, Etsuro; Eguchi, Susumu; Hibi, Taizo; Hasegawa, Kiyoshi; Umeda, Yuzo; Hashimoto, Takuya; Hasegawa, Yasushi; Nobori, Shuji; Ogura, Yasuhiro; Nitta, Hiroyuki; Egawa, Hiroto; Eguchi, Hidetoshi; Takada, Yasutsugu; Ueda, Yoshihide; Kasahara, Mureo; Kawachi, Shigeyuki; Soejima, Yuji; Tokushige, Katsutoshi; Nagano, Hiroaki; Haga, Hironori; Fukumoto, Takumi; Mochida, Satoshi; Umeshita, Koji; Ohdan, Hideki

Clinical symptoms, biochemistry, and liver histology during the native liver period of progressive familial intrahepatic cholestasis type 2

进行性家族性肝内胆汁淤积症2型患者在原位肝期的临床症状、生化指标和肝脏组织学变化

Kondou, Hiroki; Nakano, Satoshi; Mizuno, Tadahaya; Bessho, Kazuhiko; Hasegawa, Yasuhiro; Nakazawa, Atsuko; Tanikawa, Ken; Azuma, Yoshihiro; Okamoto, Tatsuya; Inui, Ayano; Imagawa, Kazuo; Kasahara, Mureo; Zen, Yoh; Suzuki, Mitsuyoshi; Hayashi, Hisamitsu

Impact of gallbladder hypoplasia on hilar hepatic ducts in biliary atresia

胆囊发育不全对胆道闭锁时肝门部肝管的影响

Nanae Miyazaki #, Shohei Takami #, Mami Uemura, Hironobu Oiki, Masataka Takahashi, Hiroshi Kawashima, Yutaka Kanamori, Takako Yoshioka, Mureo Kasahara, Atsuko Nakazawa, Mayumi Higashi, Ayaka Yanagida, Ryuji Hiramatsu, Masami Kanai-Azuma, Jun Fujishiro, Yoshiakira Kanai0