日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

CaMKII inhibition due to TRIC-B loss-of-function dysregulates SMAD signaling in osteogenesis imperfecta

由于 TRIC-B 功能丧失而导致的 CaMKII 抑制导致成骨不全症中的 SMAD 信号失调

Roberta Besio, Barbara M Contento, Nadia Garibaldi, Marta Filibian, Stephan Sonntag, Doron Shmerling, Francesca Tonelli, Marco Biggiogera, Marisa Brini, Andrea Salmaso, Milena Jovanovic, Joan C Marini, Antonio Rossi, Antonella Forlino

Targeting cellular stress in vitro improves osteoblast homeostasis, matrix collagen content and mineralization in two murine models of osteogenesis imperfecta

体外针对细胞应激可改善两种成骨不全症小鼠模型中的成骨细胞稳态、基质胶原含量和矿化

Nadia Garibaldi, Barbara M Contento, Gabriele Babini, Jacopo Morini, Stella Siciliani, Marco Biggiogera, Mario Raspanti, Joan C Marini, Antonio Rossi, Antonella Forlino, Roberta Besio1

Intracellular and Extracellular Markers of Lethality in Osteogenesis Imperfecta: A Quantitative Proteomic Approach

成骨不全症致死的细胞内和细胞外标志物:定量蛋白质组学方法

Luca Bini, Domitille Schvartz, Chiara Carnemolla, Roberta Besio, Nadia Garibaldi, Jean-Charles Sanchez, Antonella Forlino, Laura Bianchi

Osteoblasts mineralization and collagen matrix are conserved upon specific Col1a2 silencing

特定的 Col1a2 沉默可保留成骨细胞矿化和胶原基质

Silvia Maruelli, Roberta Besio, Julie Rousseau, Nadia Garibaldi, Jérôme Amiaud, Bénédicte Brulin, Pierre Layrolle, Virginie Escriou, Antonio Rossi, Valerie Trichet, Antonella Forlino

Cellular stress due to impairment of collagen prolyl hydroxylation complex is rescued by the chaperone 4-phenylbutyrate

胶原脯氨酰羟基化复合物受损导致的细胞应激可通过分子伴侣 4-苯基丁酸得到挽救

Roberta Besio, Nadia Garibaldi, Laura Leoni, Lina Cipolla, Simone Sabbioneda, Marco Biggiogera, Monica Mottes, Mona Aglan, Ghada A Otaify, Samia A Temtamy, Antonio Rossi, Antonella Forlino

4-PBA ameliorates cellular homeostasis in fibroblasts from osteogenesis imperfecta patients by enhancing autophagy and stimulating protein secretion

4-PBA 通过增强自噬和刺激蛋白质分泌来改善成骨不全症患者成纤维细胞的细胞稳态

Roberta Besio, Giusy Iula, Nadia Garibaldi, Lina Cipolla, Simone Sabbioneda, Marco Biggiogera, Joan C Marini, Antonio Rossi, Antonella Forlino