日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Somatic deficiency of the human E3 ubiquitin ligase CBL in leukocytes impairs B cell but not T cell development and function.

白细胞中人类 E3 泛素连接酶 CBL 的体细胞缺陷会损害 B 细胞的发育和功能,但不会影响 T 细胞的发育和功能。

Vatovec Taja, Neehus Anna-Lena, Jackson Katherine J L, Avery Danielle T, Bagarić Ivan, Erazo Lucia, Arango-Franco Carlos A, Ogishi Masato, Ahmed Syed F, Cederholm Axel, Russell Amanda J, Della Mina Erika, Al-Rifai Dena, Bull Rowena, Buetow Lori, Sobrino Steicy, Zhang Allison, Wahlster Lara, Michelet Marine, Parvaneh Nima, Peel Jessica, Barzaghi Federica, Leardini Davide, Philippot Quentin, Saettini Francesco, Dutrieux Jacques, de Muylder Benedicte, Vendemini Francesca, Baccelli Francesco, Catala Albert, Gambineri Eleonora, Veltroni Marinella, Pandiarajan Vignesh, Aguilar Yurena, Haerynck Filomeen, Elliott Michael, Turville Stuart, Brillot Fabienne, Khan Taushif, Consonni Filippo, Berteloot Laureline, Sewell William A, Rao Geetha, Largeaud Laetitia, Conti Francesca, Roullion Cecile, Masson Cécile, Pegoraro Francesco, Ye Tianyi, Joubran Samantha, Villalpando Emily, Bessot Boris, Seeleuthner Yoann, Le Voyer Tom, Rosain Jérémie, Li Hailun, Janda Zarah, Muratore Edoardo, Soudée Camille, Delabesse Eric, Goulvestre Claire, Shahrooei Mohammad, Puel Anne, André Isabelle, Bole-Feysot Christine, Abel Laurent, Erlacher Miriam, Béziat Vivien, Lagresle-Peyrou Chantal, Cheynier Remi, Six Emmanuelle, Marr Nico, Pasquet Marlène, Alsina Laia, Goodnow Christopher C, Landegren Nils, Aiuti Alessandro, Zhang Peng, Masetti Riccardo, Huang Danny T, Ma Cindy S, Casanova Jean-Laurent, Sankaran Vijay G, Bustamante Jacinta, Tangye Stuart G, Bohlen Jonathan

Human iPSC-derived alveolar macrophages reveal macrophage subtype functions of itaconate in M. tuberculosis defense.

人类 iPSC 衍生的肺泡巨噬细胞揭示了衣康酸在结核分枝杆菌防御中的巨噬细胞亚型功能。

Krebs Adam S, Lazarov Tomi, Reynolds Anthony T, Dill-McFarland Kimberly A, Xie Abigail, Bean James M, Du Muxue, Levy Olivier, Buglino John A, Zhong Aaron, Neehus Anna-Lena, Boisson-Dupuis Stéphanie, Casanova Jean-Laurent, Kroon Elouise E, Möller Marlo, Hawn Thomas R, Zhou Ting, Finley Lydia Ws, Jean Juste Marc Antoine, Fitzgerald Dan W, Geissmann Frederic, Glickman Michael S

Immune activation and response dynamics of human iPSC-derived macrophages in tuberculosis infection models.

结核病感染模型中人iPSC衍生巨噬细胞的免疫激活和反应动态。

Paasch Daniela, Schevel Hannah, Riehle Andrea, Costa Bibiana, Toufaili Hassan, Gehnen Tabea, Dahlmann Julia, Pavlou Andreas, Neehus Anna-Lena, Nguyen Ariane Hai Ha, Schiering Erika, Buchegger Theresa, Bustamante Jacinta, Hansen Gesine, Kalinke Ulrich, Gulbins Erich, Grassmé Heike, Lachmann Nico

Cerebral amebiasis due to Acanthamoeba sp. in a patient with complete gp91 (phox) deficiency

一名患有完全性gp91(phox)缺陷的患者罹患由棘阿米巴属(Acanthamoeba sp.)引起的脑阿米巴病。

Roelens, Marie; Neehus, Anna-Lena; Rosain, Jérémie; Collobert, Gislène; Boddaert, Nathalie; Carausu, Liana; Bustamante, Jacinta

Human genetic influences on early B cell development

人类遗传因素对早期B细胞发育的影响

Neehus, Anna-Lena; Romberg, Neil; Sankaran, Vijay G

Inherited resilience to clonal hematopoiesis by modifying stem cell RNA regulation.

通过改变干细胞 RNA 调控来获得对克隆造血的遗传抵抗力

Agarwal Gaurav, Antoszewski Mateusz, Xie Xueqin, Pershad Yash, Arora Uma P, Poon Chi-Lam, Lyu Peng, Lee Andrew J, Guo Chun-Jie, Ye Tianyi, Norford Laila Barakat, Neehus Anna-Lena, Volpe Lucrezia Della, Wahlster Lara, Ranasinghe Diyanath, Ho Tzu-Chieh, Barlowe Trevor S, Chow Arthur, Schurer Alexandra, Taggart James, Durham Benjamin H, Abdel-Wahab Omar, McGraw Kathy L, Allan James M, Soldatov Ruslan, Bick Alexander G, Kharas Michael G, Sankaran Vijay G

Human iPSC derived alveolar macrophages reveal macrophage subtype specific functions of itaconate in M. tuberculosis host defense.

人类 iPSC 衍生的肺泡巨噬细胞揭示了衣康酸在结核分枝杆菌宿主防御中的巨噬细胞亚型特异性功能

Krebs Adam, Lazarov Tomi, Reynolds Anthony, Dill-McFarland Kimberly A, Xie Abigail, Bean James, Du Muxue, Levy Olivier, Buglino John, Zhong Aaron, Neehus Anna-Lena, Boisson-Dupuis Stephanie, Casanova Jean-Laurent, Kroon Elouise E, Möller Marlo, Hawn Thomas R, Zhou Ting, Finley Lydia W S, Juste Marc Antoine Jean, Fitzgerald Dan, Geissmann Frederic, Glickman Michael S

Autoinflammation in patients with leukocytic CBL loss of heterozygosity is caused by constitutive ERK-mediated monocyte activation

白细胞性CBL杂合性缺失患者的自身炎症是由组成型ERK介导的单核细胞活化引起的。

Bohlen, Jonathan; Bagarić, Ivan; Vatovec, Taja; Ogishi, Masato; Ahmed, Syed F; Cederholm, Axel; Buetow, Lori; Sobrino, Steicy; Le Floc'h, Corentin; Arango-Franco, Carlos A; Seabra, Luis; Michelet, Marine; Barzaghi, Federica; Leardini, Davide; Saettini, Francesco; Vendemini, Francesca; Baccelli, Francesco; Catala, Albert; Gambineri, Eleonora; Veltroni, Marinella; Aguilar de la Red, Yurena; Rice, Gillian I; Consonni, Filippo; Berteloot, Laureline; Largeaud, Laetitia; Conti, Francesca; Roullion, Cécile; Masson, Cécile; Bessot, Boris; Seeleuthner, Yoann; Le Voyer, Tom; Rinchai, Darawan; Rosain, Jérémie; Neehus, Anna-Lena; Erazo-Borrás, Lucia; Li, Hailun; Janda, Zarah; Cho, En-Jui; Muratore, Edoardo; Soudée, Camille; Lainé, Candice; Delabesse, Eric; Goulvestre, Claire; Ma, Cindy S; Puel, Anne; Tangye, Stuart G; André, Isabelle; Bole-Feysot, Christine; Abel, Laurent; Erlacher, Miriam; Zhang, Shen-Ying; Béziat, Vivien; Lagresle-Peyrou, Chantal; Six, Emmanuelle; Pasquet, Marlène; Alsina, Laia; Aiuti, Alessandro; Zhang, Peng; Crow, Yanick J; Landegren, Nils; Masetti, Riccardo; Huang, Danny T; Casanova, Jean-Laurent; Bustamante, Jacinta

Human IL-23 is essential for IFN-γ-dependent immunity to mycobacteria

人类IL-23对于IFN-γ依赖性抗分枝杆菌免疫至关重要

Philippot, Quentin; Ogishi, Masato; Bohlen, Jonathan; Puchan, Julia; Arias, Andrés Augusto; Nguyen, Tina; Martin-Fernandez, Marta; Conil, Clement; Rinchai, Darawan; Momenilandi, Mana; Mahdaviani, Seyed Alireza; Keramatipour, Mohammad; Rosain, Jérémie; Yang, Rui; Khan, Taushif; Neehus, Anna-Lena; Materna, Marie; Han, Ji Eun; Peel, Jessica; Mele, Federico; Weisshaar, Marc; Jovic, Sandra; Bastard, Paul; Lévy, Romain; Le Voyer, Tom; Zhang, Peng; Maglorius Renkilaraj, Majistor Raj Luxman; Arango-Franco, Carlos A; Pelham, Simon; Seeleuthner, Yoann; Pochon, Mathieu; Ata, Manar Mahmoud Ahmad; Al Ali, Fatima; Migaud, Mélanie; Soudée, Camille; Kochetkov, Tatiana; Molitor, Anne; Carapito, Raphael; Bahram, Seiamak; Boisson, Bertrand; Fieschi, Claire; Mansouri, Davood; Marr, Nico; Okada, Satoshi; Shahrooei, Mohammad; Parvaneh, Nima; Chavoshzadeh, Zahra; Cobat, Aurélie; Bogunovic, Dusan; Abel, Laurent; Tangye, Stuart G; Ma, Cindy S; Béziat, Vivien; Sallusto, Federica; Boisson-Dupuis, Stéphanie; Bustamante, Jacinta; Casanova, Jean-Laurent; Puel, Anne

Fulminant Viral Hepatitis in Two Siblings with Inherited IL-10RB Deficiency

两名患有遗传性IL-10RB缺陷的兄弟姐妹罹患暴发性病毒性肝炎

Korol, Cecilia B; Belkaya, Serkan; Alsohime, Fahad; Lorenzo, Lazaro; Boisson-Dupuis, Stéphanie; Brancale, Joseph; Neehus, Anna-Lena; Vilarinho, Silvia; Zobaida, Alsum; Halwani, Rabih; Al-Muhsen, Saleh; Casanova, Jean-Laurent; Jouanguy, Emmanuelle