日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Gynecologic and obstetric complications in women with congenital fibrinogen disorders: insights from the Prospective Rare Bleeding Disorders Database

先天性纤维蛋白原疾病女性的妇科和产科并发症:来自前瞻性罕见出血性疾病数据库的启示

Mohsenian, Samin; Palla, Roberta; Menegatti, Marzia; Cairo, Andrea; Siboni, Simona Maria; Neerman-Arbez, Marguerite; Karimi, Mehran; Pargantou, Helen; Asselta, Rosanna; Mikovic, Danijela; Saracevic, Marko; Laros-van Gorkom, Britta; Jacobs, Laura; Shapiro, Amy; Williamson, Adrianna; Makris, Michael; Casini, Alessandro; Peyvandi, Flora

Congenital fibrinogen disorders: a retrospective clinical and genetic analysis of the Prospective Rare Bleeding Disorders Database

先天性纤维蛋白原疾病:前瞻性罕见出血性疾病数据库的回顾性临床和遗传分析

Mohsenian, Samin; Palla, Roberta; Menegatti, Marzia; Cairo, Andrea; Lecchi, Anna; Casini, Alessandro; Neerman-Arbez, Marguerite; Asselta, Rosanna; Scardo, Sara; Siboni, Simona Maria; Blatny, Jan; Zapletal, Ondrej; Schved, Jean-Francois; Giansily-Blaizot, Muriel; Halimeh, Susan; Daoud, Mohamad Ayman; Platokouki, Helen; Pergantou, Helen; Schutgens, Roger E G; Van Haaften-Spoor, Monique; Brons, Paul; Laros-van Gorkom, Britta; Van Pinxten, Elise; Borhany, Munira; Fatima, Naveena; Mikovic, Danijela; Saracevic, Marko; Özdemir, Gül Nihal; Ay, Yılmaz; Makris, Michael; Lockley, Caryl; Mumford, Andrew; Harvey, Andrew; Austin, Steve; Shapiro, Amy; Williamson, Adrianna; McGuinn, Catherine; Goldberg, Ilene; De Moerloose, Philippe; Peyvandi, Flora

Composition of thrombi in zebrafish: similarities and distinctions with mammals

斑马鱼血栓的组成:与哺乳动物的异同

Griffin, Megan S; Dahlgren, Anna R; Nagaswami, Chandrasekaran; Litvinov, Rustem I; Keeler, Kevin; Madenjian, Charles; Fuentes, Ricardo; Fish, Richard J; Neerman-Arbez, Marguerite; Holinstat, Michael; Adili, Reheman; Weisel, John W; Shavit, Jordan A

Highly thrombogenic phenotype and impaired wound healing in a patient with congenital dysfibrinogenemia: case report

先天性异常纤维蛋白原血症患者表现出高度血栓形成表型和伤口愈合障碍:病例报告

El Beayni, Nancy; Szanto, Timea; Neerman-Arbez, Marguerite; Casini, Alessandro; Lassila, Riitta

Regulation of fibrinogen synthesis

纤维蛋白原合成的调节

Dobson, Dre'Von A; Fish, Richard J; de Vries, Paul S; Morrison, Alanna C; Neerman-Arbez, Marguerite; Wolberg, Alisa S

Diagnostic value of clot formation parameters determined by rotational thromboelastometry in 63 patients with congenital dysfibrinogenemia

旋转血栓弹力图测定的凝块形成参数在63例先天性纤维蛋白原异常血症患者中的诊断价值

Simurda, Tomas; Marchi, Rita; Casini, Alessandro; Neerman-Arbez, Marguerite; Drotarova, Miroslava; Skornova, Ingrid; Zolkova, Jana; Kolkova, Zuzana; Loderer, Dusan; Brunclikova, Monika; Belakova, Kristina Maria; Stasko, Jan

Coexpression of factor VIII and factor von Willebrand variants in a woman with heavy menstrual bleeding

一名月经过多女性体内因子VIII和血管性血友病因子变体的共表达

Casini, Alessandro; Yaron, Michal; Couzens, Alexander; Fontana, Pierre; Neerman-Arbez, Marguerite

A homozygous duplication of the <I>FGG</i> exon 8-intron 8 junction causes congenital afibrinogenemia. Lessons learned from the study of a large consanguineous Turkish family

<I>FGG</i> 外显子 8-内含子 8 连接处的纯合重复会导致先天性无纤维蛋白原血症。从对一个土耳其近亲家族的研究中汲取的经验教训

Guipponi, Michel; Masclaux, Frédéric; Sloan-Béna, Frédérique; Di Sanza, Corinne; Özbek, Namik; Peyvandi, Flora; Menegatti, Marzia; Casini, Alessandro; Malbora, Baris; Neerman-Arbez, Marguerite

Chemical Modulators of Fibrinogen Production and Their Impact on Venous Thrombosis

纤维蛋白原生成的化学调节剂及其对静脉血栓形成的影响

Rui Vilar, Samuel W Lukowski, Marco Garieri, Corinne Di Sanza, Marguerite Neerman-Arbez, Richard J Fish

Venous Thrombosis and Thrombocyte Activity in Zebrafish Models of Quantitative and Qualitative Fibrinogen Disorders

斑马鱼定量和定性纤维蛋白原紊乱模型中的静脉血栓形成和血小板活性

Fish, Richard J; Freire, Cristina; Di Sanza, Corinne; Neerman-Arbez, Marguerite