日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

AAV9-mediated KCNH2 suppression-replacement gene therapy in a transgenic rabbit model of type 1 short QT syndrome

在1型短QT综合征转基因兔模型中,AAV9介导的KCNH2抑制替代基因疗法

Nimani, Saranda; Bains, Sahej; Alerni, Nicolò; Ördög, Balázs; Horváth, András; Matas, Lluis; Louradour, Julien; Giammarino, Lucilla; Tester, David J; Beslac, Olgica; Lopez, Ruben; Meier, Stefan; Egle, Manuel; Christoforou, Nicolas; Barbieri, Miriam; Vashanthakumar, Varjany; Perez-Feliz, Stefanie; Parodi, Chiara; Garcia Casalta, Luisana G; Kim, C S John; Zhou, Wei; Ye, Dan; Jurgensen, Jacqulyn; Barry, Michael A; Bego, Mariana; Keyes, Lisa; Owens, Jane; Pinkstaff, Jason; Christoph, Jan; Zehender, Manfred; Brunner, Michael; Heijman, Jordi; Casoni, Daniela; Praz, Fabien; Haeberlin, Andreas; Brooks, Gabriel; Ackerman, Michael J; Odening, Katja E

Mechano-electrical feedback in transgenic rabbit models of long QT syndrome Type 2 and short QT syndrome Type 1

转基因兔长QT综合征2型和短QT综合征1型模型中的机械电反馈

Alerni, Nicolò; Buonocunto, Melania; Nimani, Saranda; Louradour, Julien; Barbieri, Miriam; Giammarino, Lucilla; Matas, Lluis; Lumens, Joost; Delhaas, Tammo; Koren, Gideon; Lopez, Ruben; Zehender, Manfred; Brunner, Michael; Ördög, Balázs; Heijman, Jordi; Odening, Katja E

Differential effects of non-selective and cardio-selective beta-blocker therapy on ECG parameters in long QT syndrome type 1

非选择性β受体阻滞剂和心脏选择性β受体阻滞剂治疗对1型长QT间期综合征患者心电图参数的不同影响

Rieder, Marina; Christe, Vanessa; Nimani, Saranda; Deissler, Peter M; Ter Bekke, Rachel M A; Odening, Katja E

Sex and sex hormonal regulation of the atrial inward rectifier potassium current (IK1): insights into potential pro-arrhythmic mechanisms.

性与性激素对心房内向整流钾电流 (IK1) 的调节:对潜在致心律失常机制的深入了解

Giammarino Lucilla, Matas Lluis, Alerni Nicolò, Horváth András, Vashanthakumar Varjany, Nimani Saranda, Barbieri Miriam, Bains Sahej, Lopez Ruben, Louradour Julien, Ördög Balazs, Hof Thomas, Maguy Ange, Conte Giulio, Auricchio Angelo, Schotten Ulrich, Odening Katja E

Current and future precision therapy approaches in the long QT syndrome

长QT综合征的当前和未来精准治疗方法

Nimani, Saranda; Barbieri, Miriam; Rieder, Marina; Odening, Katja E

Beneficial action potential duration-shortening effects, but deleterious negative inotropism of IKs-activator docosahexaenoyl glycine in long QT syndrome type 2

二十二碳六烯酸甘氨酸(DHA)是一种IKs激活剂,在长QT综合征2型中具有缩短动作电位时程的有益作用,但同时也具有有害的负性肌力作用。

Louradour, Julien; Hornyik, Tibor; De la Cruz, Alicia; Hiniesto-Iñigo, Irene; Alerni, Nicolò; Barbieri, Miriam; Lopez, Ruben; Perez-Feliz, Stefanie; Matas, Lluís; Nimani, Saranda; Giammarino, Lucilla; Koren, Gideon; Zehender, Manfred; Brunner, Michael; Liin, Sara I; Larsson, H Peter; Odening, Katja E

KCNQ1 suppression-replacement gene therapy in transgenic rabbits with type 1 long QT syndrome

在患有1型长QT综合征的转基因兔中进行KCNQ1抑制替代基因治疗

Bains, Sahej; Giammarino, Lucilla; Nimani, Saranda; Alerni, Nicolo; Tester, David J; Kim, C S John; Christoforou, Nicolas; Louradour, Julien; Horváth, András; Beslac, Olgica; Barbieri, Miriam; Matas, Lluis; Hof, Thomas S; Lopez, Ruben; Perez-Feliz, Stefanie; Parodi, Chiara; Garcia Casalta, Luisana G; Jurgensen, Jacqulyn; Barry, Michael A; Bego, Mariana; Keyes, Lisa; Owens, Jane; Pinkstaff, Jason; Koren, Gideon; Zehender, Manfred; Brunner, Michael; Casoni, Daniela; Praz, Fabien; Haeberlin, Andreas; Brooks, Gabriel; Ackerman, Michael J; Odening, Katja E

Beneficial normalization of cardiac repolarization by carnitine in transgenic short QT syndrome type 1 rabbit models

肉碱在转基因短QT综合征1型兔模型中对心脏复极化具有有益的正常化作用

Bodi, Ilona; Mettke, Lea; Michaelides, Konstantin; Hornyik, Tibor; Meier, Stefan; Nimani, Saranda; Perez-Feliz, Stefanie; El-Battrawy, Ibrahim; Bugger, Heiko; Zehender, Manfred; Brunner, Michael; Heijman, Jordi; Odening, Katja E

Gene- and variant-specific efficacy of serum/glucocorticoid-regulated kinase 1 inhibition in long QT syndrome types 1 and 2

血清/糖皮质激素调节激酶1抑制剂对长QT综合征1型和2型的基因和变异特异性疗效

Giannetti, Federica; Barbieri, Miriam; Shiti, Assad; Casini, Simona; Sager, Philip T; Das, Saumya; Pradhananga, Sabindra; Srinivasan, Dinesh; Nimani, Saranda; Alerni, Nicolò; Louradour, Julien; Mura, Manuela; Gnecchi, Massimiliano; Brink, Paul; Zehender, Manfred; Koren, Gideon; Zaza, Antonio; Crotti, Lia; Wilde, Arthur A M; Schwartz, Peter J; Remme, Carol Ann; Gepstein, Lior; Sala, Luca; Odening, Katja E